期刊
CURRENT OPINION IN PULMONARY MEDICINE
卷 15, 期 5, 页码 463-469出版社
LIPPINCOTT WILLIAMS & WILKINS
DOI: 10.1097/MCP.0b013e32832ea4b3
关键词
acute exacerbation; clinical review; idiopathic interstitial pneumonia; idiopathic pulmonary fibrosis; interstitial lung disease; IPF Network; pulmonary hypertension; usual interstitial pneumonia
Purpose of review This review aims to highlight and place in context recent advances in and insights into the natural history, diagnosis, and management of idiopathic pulmonary fibrosis (IPF). Recent findings Although the diagnosis of IPF remains challenging, an evolution in systems of practice and advancing technologies are steadily improving diagnostic accuracy. The identification of concomitant pulmonary hypertension as well as acute exacerbations of the underlying disease have taken on increasing importance in the natural history of IPF Similarly, the management of IPF remains challenging, and although a number of recent trials of novel investigational agents for the treatment of IPF yielded negative results, at least one of these trials showed significant benefit suggesting progress in the treatment of this disease. Summary Although IPF remains a diagnostic and therapeutic challenge to even the most experienced of clinicians, our knowledge of the natural history of the disease, diagnostic accuracy, and therapeutic approach continue to advance.
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