Extradural haematoma: a rare, but fatal complication of pyknodysostosis

We report a 4-year-old girl with pyknodysostosis who suffered a skull fracture and epidural haematoma following a minor fall. Craniotomy was needed to evacuate the haematoma and prevent mortality. Extradural haematoma in this group of patients is rare, ours being the second case reported in literature.