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HDAC6 controls autophagosome maturation essential for ubiquitin-selective quality-control autophagy
Joo-Yong Lee et al.
EMBO JOURNAL (2010)
ALS-associated fused in sarcoma (FUS) mutations disrupt Transportin-mediated nuclear import
Dorothee Dormann et al.
EMBO JOURNAL (2010)
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FEBS LETTERS (2010)
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Keith A. Hanson et al.
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Andrew C. Elden et al.
NATURE (2010)
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NATURE (2010)
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T. Van Langenhove et al.
NEUROLOGY (2010)
Sortilin-Mediated Endocytosis Determines Levels of the Frontotemporal Dementia Protein, Progranulin
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NEURON (2010)
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TDP-43-Mediated Neuron Loss In Vivo Requires RNA-Binding Activity
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PLOS ONE (2010)
Tar DNA Binding Protein-43 (TDP-43) Associates with Stress Granules: Analysis of Cultured Cells and Pathological Brain Tissue
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PLOS ONE (2010)
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ACTA NEUROPATHOLOGICA (2009)
TARDBP Mutations in Motoneuron Disease with Frontotemporal Lobar Degeneration
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ANNALS OF NEUROLOGY (2009)
A new subtype of frontotemporal lobar degeneration with FUS pathology
Manuela Neumann et al.
BRAIN (2009)
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Katie Moisse et al.
BRAIN RESEARCH (2009)
Rethinking ALS: The FUS about TDP-43
Clotilde Lagier-Tourenne et al.
CELL (2009)
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CELL (2009)
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CELL (2009)
LRRK2 regulates autophagic activity and localizes to specific membrane microdomains in a novel human genomic reporter cellular model
Javier Alegre-Abarrategui et al.
HUMAN MOLECULAR GENETICS (2009)
Mutation within TARDBP Leads to Frontotemporal Dementia without Motor Neuron Disease
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HUMAN MUTATION (2009)
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VCP Mutations Causing Frontotemporal Lobar Degeneration Disrupt Localization of TDP-43 and Induce Cell Death
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JOURNAL OF BIOLOGICAL CHEMISTRY (2009)
TDP-43 Is Intrinsically Aggregation-prone, and Amyotrophic Lateral Sclerosis-linked Mutations Accelerate Aggregation and Increase Toxicity
Brian S. Johnson et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2009)
Valosin-containing protein (VCP) is required for autophagy and is disrupted in VCP disease
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TDP-43 is recruited to stress granules in conditions of oxidative insult
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JOURNAL OF NEUROCHEMISTRY (2009)
TARDBP Variation Associated with Frontotemporal Dementia, Supranuclear Gaze Palsy, and Chorea
Gabor G. Kovacs et al.
MOVEMENT DISORDERS (2009)
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Andrea D'Ambrogio et al.
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TDP-43 mutant transgenic mice develop features of ALS and frontotemporal lobar degeneration
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Mutations in FUS, an RNA Processing Protein, Cause Familial Amyotrophic Lateral Sclerosis Type 6
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SCIENCE (2009)
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SCIENCE (2009)
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Ian R. A. Mackenzie et al.
CURRENT OPINION IN NEUROLOGY (2008)
Histone deacetylase 6 interacts with the microtubule-associated protein tau
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JOURNAL OF NEUROCHEMISTRY (2008)
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LANCET NEUROLOGY (2008)
TARDBP mutations in individuals with sporadic and familial amyotrophic lateral sclerosis
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SCIENCE (2008)
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CELL DEATH AND DIFFERENTIATION (2008)
Homeostatic levels of p62 control cytoplasmic inclusion body formation in autophagy-deficient mice
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CELL (2007)
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BRAIN RESEARCH (2007)
Angiogenin loss-of-function mutations in amyotrophic lateral sclerosis
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ANNALS OF NEUROLOGY (2007)
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ACTA NEUROPATHOLOGICA (2007)
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ACTA NEUROPATHOLOGICA (2007)
Inhibition of the ubiquitin-proteasome system induces stress granule formation
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MOLECULAR BIOLOGY OF THE CELL (2007)
HDAC6 rescues neurodegeneration and provides an essential link between autophagy and the UPS
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FEBS LETTERS (2004)
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