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A conserved role for cytoplasmic poly(A)-binding protein 1 (PABPC1) in nonsense-mediated mRNA decay
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Mutations in EDAR account for one-quarter of non-ED1-related hypohidrotic ectodermal dysplasia
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hUPF2 silencing identifies physiologic substrates of mammalian nonsense-mediated mRNA decay
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The exon junction core complex is locked onto RNA by inhibition of eIF4AIII ATPase activity
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eIF4AIII binds spliced mRNA in the exon junction complex and is essential for nonsense-mediated decay
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A faux 3′-UTR promotes aberrant termination and triggers nonsense-mediated mRNA decay
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The mRNA surveillance protein hSMG-1 functions in genotoxic stress response pathways in mammalian cells
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The ever-increasing complexities of the exon junction complex
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CURRENT OPINION IN CELL BIOLOGY (2004)
Inhibition of nonsense-mediated mRNA decay rescues the phenotype in Ullrich's disease
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Nonsense surveillance regulates expression of diverse classes of mammalian transcripts and mutes genomic noise
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Y14 and hUpf3b form an NMD-activating complex
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SMG-5, required for C-elegans nonsense-mediated mRNA decay, associates with SMG-2 and protein phosphatase 2A
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mRNAs encoding telomerase components and regulators are controlled by UPF genes in Saccharomyces cerevisiae
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Evidence for the widespread coupling of alternative splicing and nonsense-mediated mRNA decay in humans
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Phosphorylation of hUPF1 induces formation of mRNA surveillance complexes containing hSMG-5 and hSMG-7
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Poly(A)-binding proteins: multifunctional scaffolds for the post-transcriptional control of gene expression
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Mammalian heat shock p70 and histone H4 transcripts, which derive from naturally intronless genes, are immune to nonsense-mediated decay
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RNA (2001)
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Premature termination mutations in exon 3 of the SMN1 gene are associated with exon skipping and a relatively mild SMA phenotype
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Rent1, a trans-effector of nonsense-mediated mRNA decay, is essential for mammalian embryonic viability
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