4.6 Article

Acid Sphingomyelinase Inhibitors Normalize Pulmonary Ceramide and Inflammation in Cystic Fibrosis

相关参考文献

注意:仅列出部分参考文献,下载原文获取全部文献信息。
Article Biochemistry & Molecular Biology

Cystic Fibrosis Fatty Acid Imbalance Is Linked to Ceramide Deficiency and Corrected by Fenretinide

Claudine Guilbault et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2009)

Article Cell Biology

Therapeutic Efficacy and Safety of Amitriptyline in Patients with Cystic Fibrosis

Joachim Riethmueller et al.

CELLULAR PHYSIOLOGY AND BIOCHEMISTRY (2009)

Article Biochemistry & Molecular Biology

Defective CFTR increases synthesis and mass of sphingolipids that modulate membrane composition and lipid signaling

Hiroko Hamai et al.

JOURNAL OF LIPID RESEARCH (2009)

Article Physiology

cAMP-mediated regulation of cholesterol accumulation in cystic fibrosis and Niemann-Pick type C cells

Mary E. Manson et al.

AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2008)

Article Biochemistry & Molecular Biology

Fenretinide corrects newly found ceramide deficiency in cystic fibrosis

Claudine Guilbault et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2008)

Article Hematology

Lysosomal Targeting and Trafficking of Acid Sphingomyelinase to Lipid Raft Platforms in Coronary Endothelial Cells

Si Jin et al.

ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY (2008)

Article Chemistry, Medicinal

Identification of new functional inhibitors of acid sphingomyelinase using a structure-property-activity relation model

Johannes Kornhuber et al.

JOURNAL OF MEDICINAL CHEMISTRY (2008)

Article Biochemistry & Molecular Biology

Ceramide accumulation mediates inflammation, cell death and infection susceptibility in cystic fibrosis

Volker Teichgraeber et al.

NATURE MEDICINE (2008)

Article Pediatrics

Impact of nutrition on phenotype in CFTR-deficient mice

Charles-Henry Cottart et al.

PEDIATRIC RESEARCH (2007)

Article Biochemistry & Molecular Biology

Host defense against Pseudomonas aeruginosa requires ceramide-rich membrane rafts

H Grassmé et al.

NATURE MEDICINE (2003)

Article Biochemistry & Molecular Biology

Inflammation and infection in naive human cystic fibrosis airway grafts

R Tirouvanziam et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2000)

Article Biochemistry & Molecular Biology

Exaggerated activation of nuclear factor-kappa B and altered I kappa B-beta processing in cystic fibrosis bronchial epithelial cells

A Venkatakrishnan et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2000)