4.3 Article

Prion-Like Characteristics of Polyglutamine-Containing Proteins

相关参考文献

注意:仅列出部分参考文献,下载原文获取全部文献信息。
Article Medicine, Research & Experimental

Huntington's Disease: Mechanisms of Pathogenesis and Therapeutic Strategies

Maria Jimenez-Sanchez et al.

COLD SPRING HARBOR PERSPECTIVES IN MEDICINE (2017)

Article Biochemistry & Molecular Biology

Relating sequence encoded information to form and function of intrinsically disordered proteins

Rahul K. Das et al.

CURRENT OPINION IN STRUCTURAL BIOLOGY (2015)

Article Biochemistry & Molecular Biology

DnaJ-1 and karyopherin α3 suppress degeneration in a new Drosophila model of Spinocerebellar Ataxia Type 6

Wei-Ling Tsou et al.

HUMAN MOLECULAR GENETICS (2015)

Review Cell Biology

Intrinsically disordered proteins in cellular signalling and regulation

Peter E. Wright et al.

NATURE REVIEWS MOLECULAR CELL BIOLOGY (2015)

Article Chemistry, Physical

On the lag phase in amyloid fibril formation

Paolo Arosio et al.

PHYSICAL CHEMISTRY CHEMICAL PHYSICS (2015)

Review Cell Biology

Molecular chaperones and neuronal proteostasis

Heather L. Smith et al.

SEMINARS IN CELL & DEVELOPMENTAL BIOLOGY (2015)

Article Multidisciplinary Sciences

Prion-like transmission of neuronal huntingtin aggregates to phagocytic glia in the Drosophila brain

Margaret M. P. Pearce et al.

NATURE COMMUNICATIONS (2015)

Article Clinical Neurology

Mutant Huntingtin is Present in Neuronal Grafts in Huntington Disease Patients

Francesca Cicchetti et al.

ANNALS OF NEUROLOGY (2014)

Review Biochemistry & Molecular Biology

Defining the limits: Protein aggregation and toxicity in vivo

William M. Holmes et al.

CRITICAL REVIEWS IN BIOCHEMISTRY AND MOLECULAR BIOLOGY (2014)

Article Biochemistry & Molecular Biology

Autophagy induction enhances TDP43 turnover and survival in neuronal ALS models

Sami J. Barmada et al.

NATURE CHEMICAL BIOLOGY (2014)

Article Multidisciplinary Sciences

Overexpression of Q-rich prion-like proteins suppresses polyQ cytotoxicity and alters the polyQ interactome

Leslie Ripaud et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2014)

Article Multidisciplinary Sciences

Prion-like proteins sequester and suppress the toxicity of huntingtin exon 1

Can Kayatekin et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2014)

Review Cell Biology

Proteostasis impairment in protein-misfolding and -aggregation diseases

Mark S. Hipp et al.

TRENDS IN CELL BIOLOGY (2014)

Review Pharmacology & Pharmacy

Drugging unconventional targets: insights from Huntington's disease

Shenliang Yu et al.

TRENDS IN PHARMACOLOGICAL SCIENCES (2014)

Article Clinical Neurology

Stages of pTDP-43 Pathology in Amyotrophic Lateral Sclerosis

Johannes Brettschneider et al.

ANNALS OF NEUROLOGY (2013)

Review Biochemistry & Molecular Biology

Molecular Chaperone Functions in Protein Folding and Proteostasis

Yujin E. Kim et al.

ANNUAL REVIEW OF BIOCHEMISTRY, VOL 82 (2013)

Review Genetics & Heredity

Biology and Genetics of Prions Causing Neurodegeneration

Stanley B. Prusiner

ANNUAL REVIEW OF GENETICS, VOL 47 (2013)

Article Cell Biology

Transfer of polyglutamine aggregates in neuronal cells occurs in tunneling nanotubes

Maddalena Costanzo et al.

JOURNAL OF CELL SCIENCE (2013)

Review Physics, Condensed Matter

Modelling amyloid fibril formation kinetics: mechanisms of nucleation and growth

J. E. Gillam et al.

JOURNAL OF PHYSICS-CONDENSED MATTER (2013)

Article Biochemistry & Molecular Biology

Proteostasis of polyglutamine varies among neurons and predicts neurodegeneration

Andrey S. Tsvetkov et al.

NATURE CHEMICAL BIOLOGY (2013)

Article Multidisciplinary Sciences

Brain homogenates from human tauopathies induce tau inclusions in mouse brain

Florence Clavaguera et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2013)

Article Multidisciplinary Sciences

Heparan sulfate proteoglycans mediate internalization and propagation of specific proteopathic seeds

Brandon B. Holmes et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2013)

Review Biochemistry & Molecular Biology

Folding the proteome

Esther Braselmann et al.

TRENDS IN BIOCHEMICAL SCIENCES (2013)

Review Biochemistry & Molecular Biology

Huntington's disease: underlying molecular mechanisms and emerging concepts

John Labbadia et al.

TRENDS IN BIOCHEMICAL SCIENCES (2013)

Article Cell Biology

Prion-like Properties of Pathological TDP-43 Aggregates from Diseased Brains

Takashi Nonaka et al.

CELL REPORTS (2013)

Article Cell Biology

SUMO-2 and PIAS1 Modulate Insoluble Mutant Huntingtin Protein Accumulation

Jacqueline Gire O'Rourke et al.

CELL REPORTS (2013)

Article Biophysics

Fibrillar α-Synuclein and Huntingtin Exon 1 Assemblies Are Toxic to the Cells

Laura Pieri et al.

BIOPHYSICAL JOURNAL (2012)

Article Biochemistry & Molecular Biology

Spt4 Is Selectively Required for Transcription of Extended Trinucleotide Repeats

Chia-Rung Liu et al.

Article Biochemistry & Molecular Biology

Critical Role of Amyloid-like Oligomers of Drosophila Orb2 in the Persistence of Memory

Amitabha Majumdar et al.

Review Biochemistry & Molecular Biology

The Amyloid State of Proteins in Human Diseases

David Eisenberg et al.

Article Biochemistry & Molecular Biology

Fibrillar Structure and Charge Determine the Interaction of Polyglutamine Protein Aggregates with the Cell Surface

R. Sean Trevino et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2012)

Review Neurosciences

Mouse Models of Polyglutamine Diseases: Review and Data Table. Part I

Maciej Figiel et al.

MOLECULAR NEUROBIOLOGY (2012)

Article Multidisciplinary Sciences

Prions are a common mechanism for phenotypic inheritance in wild yeasts

Randal Halfmann et al.

NATURE (2012)

Article Neurosciences

Propagation of Tau Pathology in a Model of Early Alzheimer's Disease

Alix de Calignon et al.

NEURON (2012)

Article Biochemistry & Molecular Biology

Evolution and function of CAG/polyglutamine repeats in protein-protein interaction networks

Martin H. Schaefer et al.

NUCLEIC ACIDS RESEARCH (2012)

Article Multidisciplinary Sciences

Trans-Synaptic Spread of Tau Pathology In Vivo

Li Liu et al.

PLOS ONE (2012)

Article Multidisciplinary Sciences

Alzheimer brain-derived tau oligomers propagate pathology from endogenous tau

Cristian A. Lasagna-Reeves et al.

SCIENTIFIC REPORTS (2012)

Article Medicine, Research & Experimental

α-Synuclein propagates from mouse brain to grafted dopaminergic neurons and seeds aggregation in cultured human cells

Christian Hansen et al.

JOURNAL OF CLINICAL INVESTIGATION (2011)

Article Multidisciplinary Sciences

Neuronal circuitry regulates the response of Caenorhabditis elegans to misfolded proteins

Veena Prahlad et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)

Article Multidisciplinary Sciences

Prion-like propagation of mutant superoxide dismutase-1 misfolding in neuronal cells

Christian Muench et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)

Article Multidisciplinary Sciences

In vivo demonstration that α-synuclein oligomers are toxic

Beate Winner et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)

Review Genetics & Heredity

CAG-Repeat Length and the Age of Onset in Huntington Disease (HD): A Review and Validation Study of Statistical Approaches

Douglas R. Langbehn et al.

AMERICAN JOURNAL OF MEDICAL GENETICS PART B-NEUROPSYCHIATRIC GENETICS (2010)

Article Biochemistry & Molecular Biology

Essential Role of Coiled Coils for Aggregation and Activity of Q/N-Rich Prions and PolyQ Proteins

Ferdinando Fiumara et al.

Review Biochemistry & Molecular Biology

Biological and Chemical Approaches to Diseases of Proteostasis Deficiency

Evan T. Powers et al.

ANNUAL REVIEW OF BIOCHEMISTRY (2009)

Article Biochemistry & Molecular Biology

Propagation of Tau Misfolding from the Outside to the Inside of a Cell

Bess Frost et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2009)

Article Cell Biology

Transmission and spreading of tauopathy in transgenic mouse brain

Florence Clavaguera et al.

NATURE CELL BIOLOGY (2009)

Review Biochemistry & Molecular Biology

Amyloid formation by globular proteins under native conditions

Fabrizio Chiti et al.

NATURE CHEMICAL BIOLOGY (2009)

Article Biochemistry & Molecular Biology

Polyglutamine disruption of the huntingtin exon 1 N terminus triggers a complex aggregation mechanism

Ashwani K. Thakur et al.

NATURE STRUCTURAL & MOLECULAR BIOLOGY (2009)

Article Multidisciplinary Sciences

RNAi Screening in Drosophila Cells Identifies New Modifiers of Mutant Huntingtin Aggregation

Joanna Doumanis et al.

PLOS ONE (2009)

Article Multidisciplinary Sciences

Inclusion formation and neuronal cell death through neuron-to-neuron transmission of α-synuclein

Paula Desplats et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)

Article Multidisciplinary Sciences

Rhes, a Striatal Specific Protein, Mediates Mutant-Huntingtin Cytotoxicity

Srinivasa Subramaniam et al.

SCIENCE (2009)

Article Biochemistry & Molecular Biology

Structural Polymorphism of 441-Residue Tau at Single Residue Resolution

Marco D. Mukrasch et al.

PLOS BIOLOGY (2009)

Article Clinical Neurology

Aggregates Assembled From Overexpression of Wild-Type α-Synuclein are not Toxic to Human Neuronal Cells

Li-wen Ko et al.

JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY (2008)

Article Biochemistry & Molecular Biology

Lewy body-like pathology in long-term embryonic nigral transplants in Parkinson's disease

Jeffrey H. Kordower et al.

NATURE MEDICINE (2008)

Article Multidisciplinary Sciences

The structural basis of yeast prion strain variants

Brandon H. Toyama et al.

NATURE (2007)

Article Multidisciplinary Sciences

Global changes to the ubiquitin system in Huntington's disease

Eric J. Bennett et al.

NATURE (2007)

Article Biotechnology & Applied Microbiology

CAG-encoded polyglutamine length polymorphism in the human genome

Stefanie L. Butland et al.

BMC GENOMICS (2007)

Article Biochemistry & Molecular Biology

Cooperative hydrogen bonding in amyloid formation

Kiril Tsemekhman et al.

PROTEIN SCIENCE (2007)

Article Multidisciplinary Sciences

Onset and progression in inherited ALS determined by motor neurons and microglia

Severine Boillee et al.

SCIENCE (2006)

Article Biochemistry & Molecular Biology

Oligoproline effects on polyglutamine conformation and aggregation

A Bhattacharyya et al.

JOURNAL OF MOLECULAR BIOLOGY (2006)

Article Multidisciplinary Sciences

Structural insights into a yeast prion illuminate nucleation and strain diversity

R Krishnan et al.

NATURE (2005)

Article Multidisciplinary Sciences

Structure of the cross-β spine of amyloid-like fibrils

R Nelson et al.

NATURE (2005)

Review Genetics & Heredity

Prions as adaptive conduits of memory and inheritance

J Shorter et al.

NATURE REVIEWS GENETICS (2005)

Article Multidisciplinary Sciences

Molecular basis for amyloid fibril formation and stability

OS Makin et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2005)

Article Multidisciplinary Sciences

SUMO modification of Huntingtin and Huntington's disease pathology

JS Steffan et al.

SCIENCE (2004)

Article Biochemistry & Molecular Biology

Scrambled prion domains form prions and amyloid

ED Ross et al.

MOLECULAR AND CELLULAR BIOLOGY (2004)

Review Clinical Neurology

Trinucleotide repeats and neurodegenerative disease

CM Everett et al.

Review Biochemistry & Molecular Biology

Differential loss of striatal projection systems in Huntington's disease: a quantitative immunohistochemical study

YP Deng et al.

JOURNAL OF CHEMICAL NEUROANATOMY (2004)

Review Cell Biology

Stages in the development of Parkinson's disease-related pathology

H Braak et al.

CELL AND TISSUE RESEARCH (2004)

Article Biochemistry & Molecular Biology

Aggregated polyglutamine peptides delivered to nuclei are toxic to mammalian cells

W Yang et al.

HUMAN MOLECULAR GENETICS (2002)

Article Biochemistry & Molecular Biology

The behaviour of polyamino acids reveals an inverse side chain effect in amyloid structure formation

M Fändrich et al.

EMBO JOURNAL (2002)

Article Multidisciplinary Sciences

A linear lattice model for polyglutamine in CAG-expansion diseases

MJ Bennett et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)

Article Multidisciplinary Sciences

Huntington's disease age-of-onset linked to polyglutamine aggregation nucleation

SM Chen et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)

Article Multidisciplinary Sciences

The threshold for polyglutamine-expansion protein aggregation and cellular toxicity is dynamic and influenced by aging in Caenorhabditis elegans

JF Morley et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)

Article Biochemistry & Molecular Biology

Amyloid-like features of polyglutamine aggregates and their assembly kinetics

SM Chen et al.

BIOCHEMISTRY (2002)

Article Biochemistry & Molecular Biology

Polyglutamine aggregation behavior in vitro supports a recruitment mechanism of cytotoxicity

S Chen et al.

JOURNAL OF MOLECULAR BIOLOGY (2001)

Article Multidisciplinary Sciences

Aggregation of huntingtin in yeast varies with the length of the polyglutamine expansion and the expression of chaperone proteins

S Krobitsch et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2000)

Article Biochemistry & Molecular Biology

Expanded polyglutamine peptides alone are intrinsically cytotoxic and cause neurodegeneration in Drosophila

JL Marsh et al.

HUMAN MOLECULAR GENETICS (2000)