相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。RNF5, DAB2 and Friends: Novel Drug Targets for Cystic Fibrosis
Elvira Sondo et al.
CURRENT PHARMACEUTICAL DESIGN (2017)
Molecular Structure of the Human CFTR Ion Channel
Fangyu Liu et al.
CELL (2017)
Correctors Rescue CFTR Mutations in Nucleotide-Binding Domain 1 (NBD1) by Modulating Proteostasis
Miqueias Lopes-Pacheco et al.
CHEMBIOCHEM (2016)
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
Abdul Rehman et al.
NEW ENGLAND JOURNAL OF MEDICINE (2015)
Genetic Inhibition Of The Ubiquitin Ligase Rnf5 Attenuates Phenotypes Associated To F508del Cystic Fibrosis Mutation
Valeria Tomati et al.
SCIENTIFIC REPORTS (2015)
Epithelial Sodium Channel Silencing as a Strategy to Correct the Airway Surface Fluid Deficit in Cystic Fibrosis
Ambra Gianotti et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2013)
CHD4 in the DNA-damage response and cell cycle progression: not so NuRDy now
Aoife O'Shaughnessy et al.
BIOCHEMICAL SOCIETY TRANSACTIONS (2013)
High-Content siRNA Screen Reveals Global ENaC Regulators and Potential Cystic Fibrosis Therapy Targets
Joana Almaca et al.
CELL (2013)
Small heat shock proteins target mutant cystic fibrosis transmembrane conductance regulator for degradation via a small ubiquitin-like modifier-dependent pathway
Annette Ahner et al.
MOLECULAR BIOLOGY OF THE CELL (2013)
Mechanism-based corrector combination restores ΔF508-CFTR folding and function
Tsukasa Okiyoneda et al.
NATURE CHEMICAL BIOLOGY (2013)
Pharmacological Characterization of a Novel ENaCα siRNA (GSK2225745) With Potential for the Treatment of Cystic Fibrosis
Kenneth L. Clark et al.
MOLECULAR THERAPY-NUCLEIC ACIDS (2013)
Association of TMEM16A chloride channel overexpression with airway goblet cell metaplasia
Paolo Scudieri et al.
JOURNAL OF PHYSIOLOGY-LONDON (2012)
Rescue of the mutant CFTR chloride channel by pharmacological correctors and low temperature analyzed by gene expression profiling
Elvira Sondo et al.
AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY (2011)
Rescue of ΔF508-CFTR Trafficking via a GRASP-Dependent Unconventional Secretion Pathway
Heon Yung Gee et al.
CELL (2011)
Af17 Deficiency Increases Sodium Excretion and Decreases Blood Pressure
Lihe Chen et al.
JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY (2011)
Influence of cell background on pharmacological rescue of mutant CFTR
Nicoletta Pedemonte et al.
AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY (2010)
Epithelial Sodium Channel Inhibition in Primary Human Bronchial Epithelia by Transfected siRNA
Emanuela Caci et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2009)
UBXD1 is a VCP-interacting protein that is involved in ER-associated degradation
Masami Nagahama et al.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS (2009)
Regulation of p53 TRIM24 enters the RING
Abhinav K. Jain et al.
CELL CYCLE (2009)
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
Fredrick Van Goor et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)
Chemical and biological approaches synergize to ameliorate protein-folding diseases
Ting-Wei Mu et al.
CELL (2008)
Adapting proteostasis for disease intervention
William E. Balch et al.
SCIENCE (2008)
Evidence for airway surface dehydration as the initiating event in CF airway disease
R. C. Boucher
JOURNAL OF INTERNAL MEDICINE (2007)
Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion
TH Ma et al.
JOURNAL OF CLINICAL INVESTIGATION (2002)