相关参考文献
注意：仅列出部分参考文献，下载原文获取全部文献信息。Real-Life Safety and Effectiveness of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis
Pierre-Regis Burgel et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2020)
Lumacaftor/ivacaf tor reduces exacerbations in adults homozygous for Phe508del mutation with severe lung disease
Koliarne Tong et al.
JOURNAL OF CYSTIC FIBROSIS (2020)
Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease
Siddhartha G. Kapnadak et al.
JOURNAL OF CYSTIC FIBROSIS (2020)
Italian and North American dietary intake after ivacaftor treatment for Cystic Fibrosis Gating Mutations
Nina N. Sainath et al.
JOURNAL OF CYSTIC FIBROSIS (2019)
Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines
Kathleen J. Ramos et al.
JOURNAL OF CYSTIC FIBROSIS (2019)
Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial
Harry G. M. Heijerman et al.
LANCET (2019)
Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele
P. G. Middleton et al.
NEW ENGLAND JOURNAL OF MEDICINE (2019)
Predictive factors for lumacaftor/ivacaftor clinical response
Alexandra Masson et al.
JOURNAL OF CYSTIC FIBROSIS (2019)
Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR
Jennifer L. Taylor-Cousar et al.
JOURNAL OF CYSTIC FIBROSIS (2018)
Energy Balance and Mechanisms of Weight Gain with Ivacaftor Treatment of Cystic Fibrosis Gating Mutations
Virginia A. Stallings et al.
JOURNAL OF PEDIATRICS (2018)
Association between body composition and pulmonary function in children and young people with cystic fibrosis
Patrizia Calella et al.
NUTRITION (2018)
Orkambi in patients with severe disease - Bumps in the road to CFTR modulation
Alex Horsley
JOURNAL OF CYSTIC FIBROSIS (2017)
Real-life initiation of lumacaftor/ivacaftor combination in adults with cystic fibrosis homozygous for the Phe508del CFTR mutation and severe lung disease
Dominique Hubert et al.
JOURNAL OF CYSTIC FIBROSIS (2017)
Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study
Michael W. Konstan et al.
LANCET RESPIRATORY MEDICINE (2017)
Effects of new and emerging therapies on gastrointestinal outcomes in cystic fibrosis
Roderick H. J. Houwen et al.
CURRENT OPINION IN PULMONARY MEDICINE (2017)
Body composition and lung function in cystic fibrosis and their association with adiposity and normal-weight obesity
Jessica A. Alvarez et al.
NUTRITION (2016)
Efficacy and safety of lumacaftor/ivacaftor combination therapy in patients with cystic fibrosis homozygous for Phe508del CFTR by pulmonary function subgroup: a pooled analysis
J. Stuart Elborn et al.
LANCET RESPIRATORY MEDICINE (2016)
Diagnostic criteria for malnutrition - An ESPEN Consensus Statement
T. Cederholm et al.
CLINICAL NUTRITION (2015)
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
Abdul Rehman et al.
NEW ENGLAND JOURNAL OF MEDICINE (2015)
Loss of fat-free mass over four years in adult cystic fibrosis is associated with high serum interleukin-6 levels but not tumour necrosis factor-alpha
Susannah J. King et al.
CLINICAL NUTRITION (2014)
212 Impact of enteral tube feeding on body fat and lean body mass
H. White et al.
Journal of Cystic Fibrosis (2014)
Recurrent pulmonary exacerbations are associated with low fat free mass and low bone mineral density in young adults with cystic fibrosis
Gianfranco Alicandro et al.
JOURNAL OF CYSTIC FIBROSIS (2014)
Body composition and pulmonary function in cystic fibrosis
Saba Sheikh et al.
FRONTIERS IN PEDIATRICS (2014)
What makes a BIA equation unique? Validity of eight-electrode multifrequency BIA to estimate body composition in a healthy adult population
A. Bosy-Westphal et al.
EUROPEAN JOURNAL OF CLINICAL NUTRITION (2013)
Fat-free mass depletion in cystic fibrosis: Associated with lung disease severity but poorly detected by body mass index
Susannah J. King et al.
NUTRITION (2010)
Hidden depletion of fat-free mass and bone mineral density in adults with cystic fibrosis
AA Ionescu et al.
CHEST (2003)
Altered tissue distribution in adults with cystic fibrosis
CE Bolton et al.
THORAX (2003)
Insulin-like growth factor I correlates with lean body mass in cystic fibrosis patients
I Sermet-Gaudelus et al.
ARCHIVES OF DISEASE IN CHILDHOOD (2003)
Relationship between nutritional status and lung function in cystic fibrosis: cross sectional and longitudinal analyses from the German CF quality assurance (CFQA) project
G Steinkamp et al.
THORAX (2002)
Pulmonary function, body composition, and protein catabolism in adults with cystic fibrosis
AA Ionescu et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2002)
分享论文
