Clinical effect of progressive pulmonary fibrosis on patients with connective tissue disease-associated interstitial lung disease: a single center retrospective cohort study

Letter Critical Care Medicine

Patient Characteristics and Survival for Progressive Pulmonary Fibrosis Using Different Definitions

Yet H. Khor et al.

AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2023)

Article Critical Care Medicine

Validation of Proposed Criteria for Progressive Pulmonary Fibrosis

Janelle Vu Pugashetti et al.

Summary: This study found that a decline in FVC of >= 10% and six additional criteria can predict transplant-free survival in patients with non-IPF ILD.

AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2023)

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Article Critical Care Medicine

Rituximab versus intravenous cyclophosphamide in patients with connective tissue disease-associated interstitial lung disease in the UK (RECITAL): a double-blind, double-dummy, randomised, controlled, phase 2b trial

Toby M. Maher et al.

Summary: In a randomized, double-blind clinical trial, it was found that rituximab is not superior to cyclophosphamide in treating connective tissue disease-associated interstitial lung disease (ILD). However, both treatment methods improved lung function and quality of life in patients within 24 weeks.

LANCET RESPIRATORY MEDICINE (2023)

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Article Rheumatology

Prediction of progressive pulmonary fibrosis in patients with anti-synthetase syndrome-associated interstitial lung disease

Hongyan Fu et al.

Summary: Positive non-Jo-1 antibodies, NLR, and serum KL-6 are independent risk factors for progressive pulmonary fibrosis (PPF) in patients with ASS-ILD.

CLINICAL RHEUMATOLOGY (2023)

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Review Respiratory System

Prevalence, imaging patterns and risk factors of interstitial lung disease in connective tissue disease: a systematic review and meta-analysis

Greta M. Joy et al.

Summary: This systematic review summarizes the prevalence, risk factors, and ILD patterns in connective tissue disease (CTD) cases. The study found substantial variability in ILD across different CTD subtypes, indicating that CTD-ILD should not be considered as a single entity.

EUROPEAN RESPIRATORY REVIEW (2023)

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Article Medicine, General & Internal

Prognostication of progressive pulmonary fibrosis in connective tissue disease-associated interstitial lung diseases: A cohort study

Yu-Hsiang Chiu et al.

Summary: This study examines the prognostic relevance of different definitions of progressive pulmonary fibrosis (PPF) in patients with CTD-ILD. The results show that higher age, smoking, increased extent of fibrosis, and low baseline DLCO are associated with poor prognosis, while regular pulmonary function evaluation is associated with better survival. The INBUILD, ATS/ERS/JRS/ALAT 2022, and simplified PF criteria have similar prognostic implications in two cohorts.

FRONTIERS IN MEDICINE (2023)

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Article Respiratory System

Clinical outcomes and risk factors of progressive pulmonary fibrosis in primary Sjogren's syndrome-associated interstitial lung disease

Yu-Hsuan Chen et al.

Summary: The study investigated the clinical outcomes and risk factors associated with progressive fibrosing interstitial lung disease (PF-ILD) in patients with primary Sjogren's syndrome-associated interstitial lung disease (pSjS-ILD). It was found that persistent lower albumin levels may be a risk factor for PF-ILD and the PF-ILD group had poorer 3-year survival outcomes. Early lung function tests could be helpful for the early detection of PF-ILD.

BMC PULMONARY MEDICINE (2023)

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Article Respiratory System

Expert consensus on the management of systemic sclerosis-associated interstitial lung disease

Franck F. Rahaghi et al.

Summary: This study aimed to develop consensus recommendations on the management of patients with SSc-ILD based on expert physician insights. A modified Delphi process was completed by pulmonologists and rheumatologists, resulting in the generation of a management algorithm that addresses the current gaps in management approaches.

RESPIRATORY RESEARCH (2023)

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Article Critical Care Medicine

Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline

Ganesh Raghu et al.

Summary: This article provides updates on the guidelines for idiopathic pulmonary fibrosis (IPF) and addresses the progression of pulmonary fibrosis in patients with interstitial lung diseases (ILDs) other than IPF. The recommendations are based on consensus and systematic reviews, aiming to provide evidence-based guidance for clinicians.

AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2022)

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Article Respiratory System

Prevalence and characteristics of progressive fibrosing interstitial lung disease in a prospective registry

Nathan Hambly et al.

Summary: The study found that PF-ILD is common in patients with fibrotic ILD, with varying progression patterns among different subtypes. Background treatments differ significantly among subtypes, and several factors are independently associated with disease progression.

EUROPEAN RESPIRATORY JOURNAL (2022)

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Article Critical Care Medicine

Consensus Guidelines for Evaluation and Management of Pulmonary Disease in Sjogren's

Augustine S. Lee et al.

Summary: This study developed clinical practice guidelines for pulmonary manifestations in Sjogren's syndrome to improve early identification, evaluation, and uniformity of care. A total of 52 recommendations were generated and finalized, covering the assessment, management, and treatment of pulmonary symptoms in Sjogren's patients, highlighting the critical importance of diagnosis.

CHEST (2021)

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Article Respiratory System

Diagnosis and management of connective tissue disease-associated interstitial lung disease in Australia and New Zealand: A position statement from the Thoracic Society of Australia and New Zealand*

Adelle S. Jee et al.

Summary: Pulmonary complications in CTD commonly involve various parts of the lungs and ILD can vary in severity, making accurate diagnosis and careful treatment decisions important. Management of CTD-ILD can be challenging due to limited data and the need for individualized approaches.

RESPIROLOGY (2021)

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Letter Respiratory System

The burden of Progressive Fibrotic Interstitial lung disease across the UK

Thomas Simpson et al.

EUROPEAN RESPIRATORY JOURNAL (2021)

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Article Respiratory System

2020 guide for the diagnosis and treatment of interstitial lung disease associated with connective tissue disease

Yasuhiro Kondoh et al.

Summary: The prognosis of patients with connective tissue disease (CTD) has improved, but interstitial lung disease (ILD) associated with CTD remains a refractory condition and a leading cause of mortality. The guide focusing on CTD-ILD, published through collaboration between Japanese Respiratory Society and Japan College of Rheumatology, aims to help standardize medical care for CTD-ILD and promote future research by addressing unresolved issues.

RESPIRATORY INVESTIGATION (2021)

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Article Respiratory System