4.6 Article

Triheptanoin Protects Motor Neurons and Delays the Onset of Motor Symptoms in a Mouse Model of Amyotrophic Lateral Sclerosis

相关参考文献

注意:仅列出部分参考文献,下载原文获取全部文献信息。
Article Clinical Neurology

Triheptanoin improves brain energy metabolism in patients with Huntington disease

Isaac Mawusi Adanyeguh et al.

NEUROLOGY (2015)

Article Endocrinology & Metabolism

Alterations of hippocampal glucose metabolism by even versus uneven medium chain triglycerides

Tanya S. McDonald et al.

JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM (2014)

Article Endocrinology & Metabolism

Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease

Jeremy S. Francis et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2014)

Article Biochemistry & Molecular Biology

Triheptanoin partially restores level of tricarboxylic acid cycle intermediates in the mouse pilocarpine model of epilepsy

Mussie G. Hadera et al.

JOURNAL OF NEUROCHEMISTRY (2014)

Review Medicine, General & Internal

Advances in motor neurone disease

Dirk Baeumer et al.

JOURNAL OF THE ROYAL SOCIETY OF MEDICINE (2014)

Article Clinical Neurology

Functional pattern of brain FDG-PET in amyotrophic lateral sclerosis

Marco Pagani et al.

NEUROLOGY (2014)

Article Endocrinology & Metabolism

Heptanoate as a neural fuel: energetic and neurotransmitter precursors in normal and glucose transporter I-deficient (G1D) brain

Isaac Marin-Valencia et al.

JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM (2013)

Review Neurosciences

Genetics of amyotrophic lateral sclerosis: an update

Sheng Chen et al.

MOLECULAR NEURODEGENERATION (2013)

Article Clinical Neurology

Gene expression profile of SOD1-G93A mouse spinal cord, blood and muscle

Christiaan G. J. Saris et al.

AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION (2013)

Review Clinical Neurology

ALS Untangled No. 20: The Deanna Protocol

Christina Fournier et al.

AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION (2013)

Article Clinical Neurology

Triheptanoin in acute mouse seizure models

Nicola K. Thomas et al.

EPILEPSY RESEARCH (2012)

Article Radiology, Nuclear Medicine & Medical Imaging

Brain hypermetabolism in amyotrophic lateral sclerosis: a FDG PET study in ALS of spinal and bulbar onset

Angelina Cistaro et al.

EUROPEAN JOURNAL OF NUCLEAR MEDICINE AND MOLECULAR IMAGING (2012)

Article Endocrinology & Metabolism

Early and progressive impairment of spinal blood flow-glucose metabolism coupling in motor neuron degeneration of ALS model mice

Kazunori Miyazaki et al.

JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM (2012)

Article Geriatrics & Gerontology

Lactate dyscrasia: a novel explanation for amyotrophic lateral sclerosis

Sivan Vadakkadath Meethal et al.

NEUROBIOLOGY OF AGING (2012)

Review Neurosciences

Mitochondrial dysfunction in ALS

Mauro Cozzolino et al.

PROGRESS IN NEUROBIOLOGY (2012)

Article Medicine, General & Internal

Amyotrophic lateral sclerosis

Matthew C. Kiernan et al.

LANCET (2011)

Review Clinical Neurology

Energy metabolism in amyotrophic lateral sclerosis

Luc Dupuis et al.

LANCET NEUROLOGY (2011)

Review Clinical Neurology

Molecular pathways of motor neuron injury in amyotrophic lateral sclerosis

Laura Ferraiuolo et al.

NATURE REVIEWS NEUROLOGY (2011)

Review Neurosciences

SOD1 Transcriptional and Posttranscriptional Regulation and Its Potential Implications in ALS

Pamela Milani et al.

NEUROLOGY RESEARCH INTERNATIONAL (2011)

Article Endocrinology & Metabolism

Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats. II. Effects on lipolysis, glucose production, and liver acyl-CoA profile

Lei Gu et al.

AMERICAN JOURNAL OF PHYSIOLOGY-ENDOCRINOLOGY AND METABOLISM (2010)

Article Clinical Neurology

Guidelines for preclinical animal research in ALS/MND: A consensus meeting

Albert C. Ludolph et al.

AMYOTROPHIC LATERAL SCLEROSIS (2010)

Article Biochemistry & Molecular Biology

Dietary anaplerotic therapy improves peripheral tissue energy metabolism in patients with Huntington's disease

Fanny Mochel et al.

EUROPEAN JOURNAL OF HUMAN GENETICS (2010)

Review Biochemistry & Molecular Biology

Oxidative stress in ALS: Key role in motor neuron injury and therapeutic target

Sian C. Barber et al.

FREE RADICAL BIOLOGY AND MEDICINE (2010)

Article Neurosciences

Anticonvulsant effects of a triheptanoin diet in two mouse chronic seizure models

Sarah Willis et al.

NEUROBIOLOGY OF DISEASE (2010)

Review Medicine, Research & Experimental

Pathophysiology of Neurodegeneration in Familial Amyotrophic Lateral Sclerosis

Steve Vucic et al.

CURRENT MOLECULAR MEDICINE (2009)

Article Multidisciplinary Sciences

Mutations in the FUS/TLS Gene on Chromosome 16 Cause Familial Amyotrophic Lateral Sclerosis

T. J. Kwiatkowski et al.

SCIENCE (2009)

Article Genetics & Heredity

TARDBP mutations in individuals with sporadic and familial amyotrophic lateral sclerosis

Edor Kabashi et al.

NATURE GENETICS (2008)

Review Neurosciences

Transgenics, toxicity and therapeutics in rodent models of mutant SOD1-mediated familial ALS

Bradley J. Turner et al.

PROGRESS IN NEUROBIOLOGY (2008)

Review Clinical Neurology

Anticonvulsant mechanisms of the ketogenic diet

Kristopher J. Bough et al.

EPILEPSIA (2007)

Article Clinical Neurology

Differential expression of genes in amyotrophic lateral sclerosis revealed by profiling the post mortem cortex

Xin-Sheng Wang et al.

AMYOTROPHIC LATERAL SCLEROSIS (2006)

Review Biochemistry & Molecular Biology

Oxidative stress in ALS: A mechanism of neurodegeneration and a therapeutic target

Sian C. Barber et al.

BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE (2006)

Article Endocrinology & Metabolism

Anaplerotic diet therapy in inherited metabolic disease: Therapeutic potential

Charles R. Roe et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2006)

Article Endocrinology & Metabolism

Anaplerotic molecules: Current and future

Henri Brunengraber et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2006)

Article Multidisciplinary Sciences

Evidence for defective energy homeostasis in amyotrophic lateral sclerosis:: benefit of a high-energy diet in a transgenic mouse

L Dupuis et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2004)

Review Clinical Neurology

Inflammatory processes in amyotrophic lateral sclerosis

PL McGeer et al.

MUSCLE & NERVE (2002)

Article Biochemistry & Molecular Biology

Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice

M Mattiazzi et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2002)

Review Neurosciences

From Charcot to Lou Gehrig: Deciphering selective motor neuron death in ALS

DW Cleveland et al.

NATURE REVIEWS NEUROSCIENCE (2001)

Article Clinical Neurology

Cytoskeletal abnormalities in amyotrophic lateral sclerosis: beneficial or detrimental effects?

JP Julien et al.

JOURNAL OF THE NEUROLOGICAL SCIENCES (2000)