Portal Embolisation as Treatment of Severe Portal Hypertension Due to Idiopathic Intrahepatic Arterioportal Fistula: A Case Report

Intrahepatic arterioportal fistula (IAPF) is a rare cause of portal hypertension. Treatment is usually aimed at restoring the normal portal hemodynamics by obliterating the shunt. This report describes a case of idiopathic IAPF with severe portal hypertension complicated by portal enteropathy with vomiting, gastrointestinal hemor-rhage and sepsis. The patient was successfully treated with portal embolization. ( J CLIN EXP HEPA-TOL 2024;14:101295)

Automated summary

Intrahepatic arterioportal fistula (IAPF) is a rare cause of portal hypertension. The aim of treatment is to restore normal portal hemodynamics by closing the shunt. This report describes a case of idiopathic IAPF with severe portal hypertension complicated by portal enteropathy, vomiting, gastrointestinal hemorrhage, and sepsis. The patient was successfully treated with portal embolization.