Congenital pulmonary airway malformation manifesting with severe respiratory distress and pneumothorax in a neonate

Congenital pulmonary airway malformation (CPAM) is congenital pulmonary anomaly characterized by multicystic areas, over-distension, and proliferation of terminal bronchioles with lack of normal alveoli. Clinical presentation may vary from mild respiratory symptoms to severe respiratory distress and frequent pneumothoraxes. We report a rare case of neonatal CPAM type I manifested with neonatal respiratory distress and pneumothorax, which was managed successfully with left lower lobectomy.

Automated summary

Congenital pulmonary airway malformation (CPAM) is a congenital lung anomaly characterized by multicystic areas and over-distension of bronchioles. This case report describes a rare case of neonatal CPAM type I, presenting with respiratory distress and pneumothorax, which was successfully managed with left lower lobectomy.