期刊
JOURNAL OF CLINICAL MEDICINE
卷 11, 期 24, 页码 -出版社
MDPI
DOI: 10.3390/jcm11247429
关键词
eosinophilic granulomatosis with polyangiitis; ANCA; cutaneous manifestation; vasculitis; rituximab
This article reports the clinical features and cutaneous manifestations of an ANCA-positive EGPA patient, emphasizing the importance of dermatologic signs in diagnosis and treatment.
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare immune-mediated vasculitis associated with anti-neutrophil cytoplasmic antibodies (ANCAs). Having systemic and possibly severe involvement, a prompt recognition of its clinical features is crucial to achieve favorable patient outcomes. Although cutaneous manifestations represent key elements, these still remain poorly characterized. We report a case of ANCA-positive EGPA presenting with palpable purpura, livedo reticularis, and pemphigoid-like lesions that was successfully treated with glucocorticoid therapy and rituximab. This report portrays the evolution of cutaneous lesions in ANCA-positive EGPA and demonstrates how dermatologic signs may represent indicators of active disease, allowing for timely diagnosis and for the monitoring of disease activity during treatment.
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