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Dystroglycan is not required for localization of dystrophin, syntrophin, and neuronal nitric-oxide synthase at the sarcolemma but regulates integrin α7B expression and caveolin-3 distribution
PD Côté et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Dystrophin isoform Dp71 is present in lamellipodia and focal complexes in human astrocytoma cells U-373 MG
CG Garcia-Tovar et al.
ACTA HISTOCHEMICA (2002)
Mutations in the fukutin-related protein gene (FKRP) cause a form of congenital muscular dystrophy with secondary laminin α2 deficiency and abnormal glycosylation of α-dystroglycan
M Brockington et al.
AMERICAN JOURNAL OF HUMAN GENETICS (2001)
Transforming growth factor-β repression of matrix metalloproteinase-1 in dermal fibroblasts involves Smad3
WH Yuan et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Dystrophin-deficient cardiomyocytes are abnormally vulnerable to mechanical stress-induced contractile failure and injury
G Danialou et al.
FASEB JOURNAL (2001)
Dilated cardiomyopathy of Becker-type muscular dystrophy with exon 4 deletion - A case report
M Saotome et al.
ANGIOLOGY (2001)
The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin
IN Rybakova et al.
JOURNAL OF CELL BIOLOGY (2000)
Congenital muscular dystrophy with secondary merosin deficiency and normal brain MRI: A novel entity?
E Mercuri et al.
NEUROPEDIATRICS (2000)
GRB2 links signaling to actin assembly by enhancing interaction of neural Wiskott-Aldrich syndrome protein (N-WASp) with actin-related protein (ARP2/3) complex
MF Carlier et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2000)
Disruption of heart sarcoglycan complex and severe cardiomyopathy caused by β sarcoglycan mutations
R Barresi et al.
JOURNAL OF MEDICAL GENETICS (2000)
Mutations in the human delta-sarcoglycan gene in familial and sporadic dilated cardiomyopathy
S Tsubata et al.
JOURNAL OF CLINICAL INVESTIGATION (2000)