相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。Modifying ADAMTS13 to modulate binding of pathogenic autoantibodies of patients with acquired thrombotic thrombocytopenic purpura
Nuno A. G. Graca et al.
HAEMATOLOGICA (2020)
Exploring the minimal structure of a functional ADAMTS13 by mutagenesis and small-angle X-ray scattering
Jian Zhu et al.
BLOOD (2019)
Characterization and treatment of congenital thrombotic thrombocytopenic purpura
Ferras Alwan et al.
BLOOD (2019)
Crystal structure and substrate-induced activation of ADAMTS13
Anastasis Petri et al.
NATURE COMMUNICATIONS (2019)
Treatment of Congenital Thrombotic Thrombocytopenia Purpura
Louis M. Aledort et al.
JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY (2017)
The role of the ADAMTS13 cysteine-rich domain in VWF binding and proteolysis
Rens de Groot et al.
BLOOD (2015)
ADAMTS13 and von Willebrand factor interactions
Catherine B. Zander et al.
CURRENT OPINION IN HEMATOLOGY (2015)
von Willebrand factor, Jedi knight of the bloodstream
Timothy A. Springer
BLOOD (2014)
Allosteric activation of ADAMTS13 by von Willebrand factor
Joshua Muia et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2014)
Conformational activation of ADAMTS13
Kieron South et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2014)
AAV-mediated expression of an ADAMTS13 variant prevents shigatoxin-induced thrombotic thrombocytopenic purpura
Sheng-Yu Jin et al.
BLOOD (2013)
Gain-of-function ADAMTS13 variants that are resistant to autoantibodies against ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura
Cui Jian et al.
BLOOD (2012)
Pregnancy-induced thrombocytopenia and TTP, and the risk of fetal death, in Upshaw-Schulman syndrome: a series of 15 pregnancies in 9 genotyped patients
Yoshihiro Fujimura et al.
BRITISH JOURNAL OF HAEMATOLOGY (2009)
Crystal structures of the noncatalytic domains of ADAMTS13 reveal multiple discontinuous exosites for von Willebrand factor
Masashi Akiyama et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)
In-vitro and in-vivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTSI3 in thrombotic thrombocytopenic purpura
Roberta Donadelli et al.
THROMBOSIS AND HAEMOSTASIS (2006)
Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura
T Uchida et al.
BLOOD (2004)
Cleavage of von Willebrand factor requires the spacer domain of the metalloprotease ADAMTS13
XL Zheng et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
ADAMTS-13 cysteine-rich/spacer domains are functionally essential for von Willebrand factor cleavage
K Soejima et al.
BLOOD (2003)
Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura
GG Levy et al.
NATURE (2001)