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注意:仅列出部分参考文献,下载原文获取全部文献信息。Quality of Life since Pre-Ataxic Phases of Spinocerebellar Ataxia Type 3/Machado-Joseph Disease
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Unique degeneration signatures in the cerebellar cortex for spinocerebellar ataxias 2, 3, and 7
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BRAIN (2015)
Structural and functional MRI abnormalities of cerebellar cortex and nuclei in SCA3, SCA6 and Friedreich's ataxia
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In vivo analysis of Purkinje cell firing properties during postnatal mouse development
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Aberrant Purkinje cell activity is the cause of dystonia in a shRNA-based mouse model of Rapid Onset Dystonia-Parkinsonism
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Lithium Chloride Therapy Fails to Improve Motor Function in a Transgenic Mouse Model of Machado-Joseph Disease
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Brain pathology of spinocerebellar ataxias
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Cellular protein quality control and the evolution of aggregates in spinocerebellar ataxia type 3 (SCA3)
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JOURNAL OF PHYSIOLOGY-LONDON (2008)
The parallel rod floor test: a measure of ataxia in mice
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Scale for the assessment and rating of ataxia -: Development of a new clinical scale
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Decreases in the precision of Purkinje cell pacemaking cause cerebellar dysfunction and ataxia
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Neurogranin expression identifies a novel array of Purkinje cell parasagittal stripes during mouse cerebellar development
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Characterization of the parallel rod floor apparatus to test motor incoordination in mice
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Potassium channel blockers inhibit the triggers of attacks in the calcium channel mouse mutant tottering
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