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Function and redox state of mitochondrial localized cysteine-rich proteins important in the assembly of cytochrome c oxidase
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BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH (2008)
Dissecting membrane insertion of mitochondrial β-barrel proteins
Stephan Kutik et al.
CELL (2008)
A mitochondrial protein compendium elucidates complex I disease biology
David J. Pagliarini et al.
CELL (2008)
Pet191 is a cytochrome c oxidase assembly factor in Saccharomyces cerevisiae
Oleh Khalimonchuk et al.
EUKARYOTIC CELL (2008)
The Tim8-Tim13 Complex Has Multiple Substrate Binding Sites and Binds Cooperatively to Tim23
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JOURNAL OF MOLECULAR BIOLOGY (2008)
The Variability of the Harlequin Mouse Phenotype Resembles that of Human Mitochondrial-Complex I-Deficiency Syndromes
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PLOS ONE (2008)
Mitochondrial copper(I) transfer from Cox17 to Sco1 is coupled to electron transfer
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PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)
A structural-dynamical characterization of human Cox17
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JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Tom20 and Tom22 share the common signal recognition pathway in mitochondrial protein import
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JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
A role for cytochrome c and cytochrome c peroxidase in electron shuttling from Erv1
Deepa V. Dabir et al.
EMBO JOURNAL (2007)
Glucose restriction extends Caenorhabditis elegans life span by inducing mitochondrial respiration and increasing oxidative stress
Tim J. Schulz et al.
CELL METABOLISM (2007)
Oxidative folding of small Tims is mediated by site-specific docking onto Mia40 in the mitochondrial intermembrane space
Dionisia P. Sideris et al.
MOLECULAR MICROBIOLOGY (2007)
Biogenesis of the essential Tim9-Tim10 chaperone complex of mitochondria - Site-specific recognition of cysteine residues by the intermembrane space receptor Mia40
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JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
AMP-activated protein kinase (AMPK) action in skeletal muscle via direct phosphorylation of PGC-1α
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PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2007)
Mitochondrial respiratory chain and thioredoxin reductase regulate intermembrane Cu, Zn-superoxide dismutase activity:: implications for mitochondrial energy metabolism and apoptosis
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BIOCHEMICAL JOURNAL (2007)
The Qo site of the mitochondrial complex III is required for the transduction of hypoxic signaling via reactive oxygen species production
Eric L. Bell et al.
JOURNAL OF CELL BIOLOGY (2007)
Evidence for a pro-oxidant intermediate in the assembly of cytochrome oxidase
Oleh Khalimonchuk et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Characterization of the cytochrome c oxidase assembly factor Cox19 of Saccharomyces cerevisiae
Kevin Rigby et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
The sulfhydryl oxidase Erv1 is a substrate of the Mia40-dependent protein translocation pathway
Nadia Terziyska et al.
FEBS LETTERS (2007)
Superoxide production is inversely related to complex I activity in inherited complex I deficiency
Sjoerd Verkaart et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE (2007)
Novel mitochondrial intermembrane space proteins as substrates of the MIA import pathway
Kipros Gabriel et al.
JOURNAL OF MOLECULAR BIOLOGY (2007)
The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis
Scot C. Leary et al.
CELL METABOLISM (2007)
A novel protein, Romo1, induces ROS production in the mitochondria
Young Min Chung et al.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS (2006)
The complete yeast mitochondrial proteome: Multidimensional separation techniques for mitochondrial proteomics
Joerg Reinders et al.
JOURNAL OF PROTEOME RESEARCH (2006)
Copper trafficking to the mitochondrion and assembly of copper metalloenzymes
Paul A. Cobine et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH (2006)
Mitochondrial metabolic states regulate nitric oxide and hydrogen peroxide diffusion to the cytosol
Alberto Boveris et al.
BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS (2006)
Crystal structure of the mitochondrial chaperone TIM9•10 reveals a six-bladed α-propeller
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MOLECULAR CELL (2006)
Erv1 mediates the Mia40-dependent protein import pathway and provides a functional link to the respiratory chain by shuttling electrons to cytochrome c
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JOURNAL OF MOLECULAR BIOLOGY (2005)
Functional and mutational characterization of human MIA40 acting during import into the mitochondrial intermembrane space
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JOURNAL OF MOLECULAR BIOLOGY (2005)
A disulfide relay system in the intermembrane space of mitochondria that mediates protein import
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CELL (2005)
Mitochondrial complex III is required for hypoxia-induced ROS production and cellular oxygen sensing
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CELL METABOLISM (2005)
Redox activation of mitochondrial intermembrane space Cu,Zn-superoxide dismutase
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BIOCHEMICAL JOURNAL (2005)
Mitochondrial nitric oxide synthase
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TRENDS IN PHARMACOLOGICAL SCIENCES (2005)
Mia40, a novel factor for protein import into the intermembrane space of mitochondria is able to bind metal ions
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FEBS LETTERS (2005)
Functional TIM10 chaperone assembly is redox-regulated in vivo
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Cox17 is functional when tethered to the mitochondrial inner membrane
AB Maxfield et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Essential role of Mia40 in import and assembly of mitochondrial intermembrane space proteins
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EMBO JOURNAL (2004)
Human SCO1 and SCO2 have independent, cooperative functions in copper delivery to cytochrome c oxidase
SC Leary et al.
HUMAN MOLECULAR GENETICS (2004)
Specific copper transfer from the Cox17 metallochaperone to both Sco1 and Cox11 in the assembly of yeast cytochrome c oxidase
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Metal-binding mechanism of Cox17, a copper chaperone for cytochrome c oxidase
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BIOCHEMICAL JOURNAL (2004)
Solution structure of Cox11, a novel type of β-immunoglobulin-like fold involved in CuB site formation of cytochrome C oxidase
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
COX23, a homologue of COX17, is required for cytochrome oxidase assembly
MH Barros et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
AIF deficiency compromises oxidative phosphorylation
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EMBO JOURNAL (2004)
Complex III releases superoxide to both sides of the inner mitochondrial membrane
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Identification of Tim40 that mediates protein sorting to the mitochondrial intermembrane space
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
The role of Hot13p and redox chemistry in the mitochondrial TIM22 import pathway
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JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
The small tim proteins and the twin CX3C motif
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TRENDS IN BIOCHEMICAL SCIENCES (2004)
Evolutionary conservation of biogenesis of β-barrel membrane proteins
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NATURE (2003)
Oma1, a novel membrane-bound metallopeptidase in mitochondria with activities overlapping with the m-AAA protease
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JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
The proteome of Saccharomyces cerevisiae mitochondria
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PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)
Voltage-dependent anion channels control the release of the superoxide anion from mitochondria to cytosol
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JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Characterization of COX19, a widely distributed gene required for expression of mitochondrial cytochrome oxidase
MP Nobrega et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Yeast Cox11, a protein essential for cytochrome c oxidase assembly, is a Cu(I)-binding protein
HS Carr et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Yeast Sco1, a protein essential for cytochrome c oxidase function is a Cu(I)-binding protein
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JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
An essential function of the mitochondrial sulfhydryl oxidase Erv1p/ALR in the maturation of cytosolic Fe/S proteins
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EMBO REPORTS (2001)
Kinetic characterization of the rotenone-insensitive internal NADH:: Ubiquinone oxidoreductase of mitochondria from Saccharomyces cerevisiae
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ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS (2001)
The mitochondrial copper metallochaperone Cox17 exists as an oligomeric, polycopper complex
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BIOCHEMISTRY (2001)
Mutational analysis of the mitochondrial copper metallochaperone Cox17
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JOURNAL OF BIOLOGICAL CHEMISTRY (2000)
Structure at 2.3 Å resolution of the cytochrome bc1 complex from the yeast Saccharomyces cerevisiae co-crystallized with an antibody Fv fragment
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STRUCTURE (2000)
Mutations in SCO2 are associated with a distinct form of hypertrophic cardiomyopathy and cytochrome c oxidase deficiency
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HUMAN MOLECULAR GENETICS (2000)
Membrane protein degradation by AAA proteases in mitochondria: Extraction of substrates from either membrane surface
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MOLECULAR CELL (2000)
Cox11p is required for stable formation of the CuB and magnesium centers of cytochrome c oxidase
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JOURNAL OF BIOLOGICAL CHEMISTRY (2000)
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