4.7 Article

Casein Glycomacropeptide: An Alternative Protein Substitute in Tyrosinemia Type I

相关参考文献

注意:仅列出部分参考文献,下载原文获取全部文献信息。
Article Nutrition & Dietetics

Growth and Body Composition in PKU Children-A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes

Anne Daly et al.

Summary: Protein quality and quantity are crucial for determining muscle mass. In PKU, protein substitutes play a key role in providing nitrogen and amino acids. Results of a 3-year study comparing the impact of AA and CGMP-AA on body composition and growth did not show significant differences.

NUTRIENTS (2021)

Article Genetics & Heredity

Type 1 tyrosinemia in Finland: a nationwide study

Linnea Aarela et al.

ORPHANET JOURNAL OF RARE DISEASES (2020)

Article Nutrition & Dietetics

Blood and Brain Biochemistry and Behaviour in NTBC and Dietary Treated Tyrosinemia Type 1 Mice

Willem G. van Ginkel et al.

NUTRIENTS (2019)

Article Agriculture, Multidisciplinary

Glycomacropeptide Sustains Microbiota Diversity and Promotes Specific Taxa in an Artificial Colon Model of Elderly Gut Microbiota

Alexandra Ntemiri et al.

JOURNAL OF AGRICULTURAL AND FOOD CHEMISTRY (2017)

Article Nutrition & Dietetics

Glycomacropeptide in children with phenylketonuria: does its phenylalanine content affect blood phenylalanine control?

A. Daly et al.

JOURNAL OF HUMAN NUTRITION AND DIETETICS (2017)

Article Genetics & Heredity

Neurocognitive outcome in tyrosinemia type 1 patients compared to healthy controls

Willem G. van Ginkel et al.

ORPHANET JOURNAL OF RARE DISEASES (2016)

Article Gastroenterology & Hepatology

Glycomacropeptide is a prebiotic that reduces Desulfovibrio bacteria, increases cecal short-chain fatty acids, and is anti-inflammatory in mice

Emily A. Sawin et al.

AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY (2015)

Review Biochemistry & Molecular Biology

Nutritional and medicinal aspects of D-amino acids

Mendel Friedman et al.

AMINO ACIDS (2012)

Article Endocrinology & Metabolism

Adherence Issues in Inherited Metabolic Disorders Treated by Low Natural Protein Diets

A. MacDonald et al.

ANNALS OF NUTRITION AND METABOLISM (2012)

Article Endocrinology & Metabolism

Increase of CSF tyrosine and impaired serotonin turnover in tyrosinemia type I

Eva Thimm et al.

MOLECULAR GENETICS AND METABOLISM (2011)

Article Endocrinology & Metabolism

Nutritional management of PKU with glycomacropeptide from cheese whey

D. M. Ney et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2009)

Article Endocrinology & Metabolism

NTBC treatment in tyrosinaemia type I: Long-term outcome in French patients

A. Masurel-Paulet et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2008)

Article Endocrinology & Metabolism

Acceptable low-phenylalanine foods and beverages can be made with glycomacropeptide from cheese whey for individuals with PKU

Kyungwha Lim et al.

MOLECULAR GENETICS AND METABOLISM (2007)

Article Nutrition & Dietetics

Bioactive properties of milk proteins with particular focus on anticariogenesis

WR Aimutis

JOURNAL OF NUTRITION (2004)

Article Nutrition & Dietetics

Nutrient intakes and physical growth of children with phenylketonuria undergoing nutrition therapy

PB Acosta et al.

JOURNAL OF THE AMERICAN DIETETIC ASSOCIATION (2003)

Review Nutrition & Dietetics

The role and potential of sialic acid in human nutrition

B Wang et al.

EUROPEAN JOURNAL OF CLINICAL NUTRITION (2003)

Article Endocrinology & Metabolism

Phenylalanine supplementation improves the phenylalanine profile in tyrosinaemia

CJ Wilson et al.

JOURNAL OF INHERITED METABOLIC DISEASE (2000)