Leadless intracardiac transcatheter pacing system: 20 months follow up in adult Duchenne muscular dystrophy

Duchenne muscular dystrophy (DMD) is an X-linked muscular dystrophy in relation with dystrophin deficient. Heart and respiratory function are classically involved and affect long-term prognosis. Significant atrio-ventricular block may occur in some patients. Implantation of traditional pacemaker may be challenging in patients with tracheotomy and on permanent home mechanical ventilation. We report the first case of a successful leadless intra-cardiac trans-catheter pacing system implantation in an adult DMD on wheelchair and on permanent home mechanical ventilation. (c) 2021 Elsevier B.V. All rights reserved.

Automated summary

Duchenne muscular dystrophy (DMD) is an X-linked genetic disease related to dystrophin deficiency, which can affect heart and respiratory function, with the possibility of severe atrio-ventricular block in some cases. The implantation of a leadless intra-cardiac trans-catheter pacing system was successfully performed in an adult DMD patient using a wheelchair and permanent home mechanical ventilation.