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Mechanisms of disease: Mitochondrial respiratory-chain diseases
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Human mitochondrial transcription factor B1 methylates ribosomal RNA at a conserved stem-loop
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EUROPEAN JOURNAL OF BIOCHEMISTRY (2002)
Isolation and characterization of the putative nuclear modifier gene MTO1 involved in the pathogenesis of deafness-associated mitochondrial 12 S rRNA A1555G mutation
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Cosegregation of the mitochondrial DNA A1555G and G4309A mutations results in deafness and mitochondrial myopathy
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Crystal structure of the ribosome at 5.5 Å resolution
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Search for characteristic structural features of mammalian mitochondrial tRNAs
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