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Julio A. Alfieri et al.
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Ammar Al-Chalabi et al.
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Pierre Paoletti et al.
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Ramesh K. Narayanan et al.
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Harry J. Han et al.
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Gina Turrigiano
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Vivek Swarup et al.
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Steve Vucic et al.
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Youhna M. Ayala et al.
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Lionel M. Igaz et al.
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Liqun Liu-Yesucevitz et al.
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A Urbani et al.
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