期刊
JOURNAL OF THE ACADEMY OF NUTRITION AND DIETETICS
卷 112, 期 8, 页码 1201-1210出版社
ELSEVIER SCIENCE INC
DOI: 10.1016/j.jand.2012.05.004
关键词
Inborn errors of metabolism; Whey proteins; Phenylalanine metabolism; Glycomacropeptide
资金
- Department of Health and Human Services from the Clinical and Translational Science Award program of the National Center for Research Resources [R03-DK-071534, P30-HD-03352, R01-FD-003711, IUL1RR025011]
- Michaux Family Foundation
- College of Agricultural and Life Sciences, University of Wisconsin-Madison
Phenylketonuria (PKU), an inborn error in phenylalanine metabolism, requires lifelong nutrition management with a low-phenylalanine diet, which includes a phenylalanine-free amino acid-based medical formula to provide the majority of an individual's protein needs. Compliance with this diet is often difficult for older children, adolescents, and adults with PKU. The whey protein glycomacropeptide (GMP) is ideally suited for the PKU diet because it is naturally low in phenylalanine. Nutritionally complete, acceptable medical foods and beverages can be made with GMP to increase the variety of protein sources for the PKU diet. As an intact protein, GMP improves protein use and increases satiety compared with amino acids. Thus, GMP provides a new, more physiologic source of low-phenylalanine dietary protein for people with PKU. J Acad Nutr Diet. 2012;112:1201-1210.
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