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D Bergemalm et al.
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H Kikuchi et al.
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Lessons from models of SOD1-linked familial ALS
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Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria
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Amyotrophic lateral sclerosis-associated SOD1 mutant proteins bind and aggregate with Bcl-2 in spinal cord mitochondria
P Pasinelli et al.
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VK Mootha et al.
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LS Field et al.
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CMJ Higgins et al.
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High molecular weight complexes of mutant superoxide dismutase 1: Age-dependent and tissue-specific accumulation
J Wang et al.
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