相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。Lack of Cystic Fibrosis Transmembrane Conductance Regulator in CD3+ Lymphocytes Leads to Aberrant Cytokine Secretion and Hyperinflammatory Adaptive Immune Responses
Christian Mueller et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2011)
Cardiomyocytes with disrupted CFTR function require CaMKII and Ca2+-activated Cl- channel activity to maintain contraction rate
Zachary M. Sellers et al.
JOURNAL OF PHYSIOLOGY-LONDON (2010)
Macrophages Directly Contribute to the Exaggerated Inflammatory Response in Cystic Fibrosis Transmembrane Conductance Regulator-/- Mice
Emanuela M. Bruscia et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2009)
Cystic fibrosis and innate immunity: how chloride channel mutations provoke lung disease
Gerd Doering et al.
CELLULAR MICROBIOLOGY (2009)
Alveolar macrophages and CC chemokines are increased in children with cystic fibrosis
S. Brennan et al.
EUROPEAN RESPIRATORY JOURNAL (2009)
Chloride channels as drug targets
Alan S. Verkman et al.
NATURE REVIEWS DRUG DISCOVERY (2009)
Calcium homeostasis is abnormal in cystic fibrosis airway epithelial cells but is normalized after rescue of F508del-CFTR
Fabrice Antigny et al.
CELL CALCIUM (2008)
Innate immune activation and cystic fibrosis
Siobhain Brennan
PAEDIATRIC RESPIRATORY REVIEWS (2008)
Rectal potential difference and the functional expression of CFTR in the gastrointestinal epithelia in cystic fibrosis mouse models
Scott A. Weiner et al.
PEDIATRIC RESEARCH (2008)
Abnormal spatial diffusion of Ca2+ in F508del-CFTR airway epithelial cells
Fabrice Antigny et al.
RESPIRATORY RESEARCH (2008)
Characteristics of rat downregulated in adenoma (rDRA) expressed in HEK 293 cells
Christian Barmeyer et al.
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY (2007)
ΔF508 mutation results in impaired gastric acid secretion
Shafik M. Sidani et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Engraftment of donor-derived epithelial cells in multiple organs following bone marrow transplantation into newborn mice
Emanuela M. Bruscia et al.
STEM CELLS (2006)
CFTR regulates phagosome acidification in macrophages and alters bactericidal activity
Anke Di et al.
NATURE CELL BIOLOGY (2006)
Cystic fibrosis since 1938
PB Davis
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2006)
Mouse as a model of growth retardation in cystic fibrosis
LA Rosenberg et al.
PEDIATRIC RESEARCH (2006)
Chronic airway Infection/Inflammation induces a Ca2+i-dependent hyperinflammatory response in human cystic fibrosis airway epithelia
CMP Ribeiro et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Fluorescent imaging of Cl- in Amphiuma red blood cells:: How the nuclear exclusion of Cl- affects the plasma membrane potential
JF Hoffman et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2005)
Extracellular calcium sensing and signalling
AM Hofer et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2003)
Calcium-pump inhibitors induce functional surface expression of ΔF508-CFTR protein in cystic fibrosis epithelial cells
ME Egan et al.
NATURE MEDICINE (2002)
Distinct pattern of immune cell population in the lung of human fetuses with cystic fibrosis
C Hubeau et al.
JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY (2001)
Regulation of CFTR Cl- channel gating by ATP binding and hydrolysis
M Ikuma et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2000)
G551D cystic fibrosis mice exhibit abnormal regulation of inflammation in lungs and macrophages
GR Thomas et al.
JOURNAL OF IMMUNOLOGY (2000)