相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。Induction of Type I Interferon Signaling by Pseudomonas aeruginosa Is Diminished in Cystic Fibrosis Epithelial Cells
Dane Parker et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2012)
Lack of an exaggerated inflammatory response on virus infection in cystic fibrosis
E. Kieninger et al.
EUROPEAN RESPIRATORY JOURNAL (2012)
Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation
J. P. Clancy et al.
THORAX (2012)
Mucous solids and liquid secretion by airways: studies with normal pig, cystic fibrosis human, and non-cystic fibrosis human bronchi
Chelsea J. Martens et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2011)
MAPK signaling pathways regulate IL-8 mRNA stability and IL-8 protein expression in cystic fibrosis lung epithelial cell lines
Sharmistha Bhattacharyya et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2011)
Infection, Inflammation, and Lung Function Decline in Infants with Cystic Fibrosis
Naveen Pillarisetti et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
Denufosol Tetrasodium in Patients with Cystic Fibrosis and Normal to Mildly Impaired Lung Function
Frank J. Accurso et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
Pseudomonas aeruginosa Population Diversity and Turnover in Cystic Fibrosis Chronic Infections
Eilidh Mowat et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
The Th17 Pathway in Cystic Fibrosis Lung Disease
Hui-Leng Tan et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
IL-17 in Cystic Fibrosis: More Than Just Th17 Cells
Patricia J. Dubin et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
Nebulized Hypertonic Saline Decreases IL-8 in Sputum of Patients with Cystic Fibrosis
Emer P. Reeves et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2011)
Lack of Cystic Fibrosis Transmembrane Conductance Regulator in CD3+ Lymphocytes Leads to Aberrant Cytokine Secretion and Hyperinflammatory Adaptive Immune Responses
Christian Mueller et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2011)
Innate Immunity in the Respiratory Epithelium
Dane Parker et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2011)
Innate Inflammatory Responses of Pediatric Cystic Fibrosis Airway Epithelial Cells Effects of Nonviral and Viral Stimulation
Erika N. Sutanto et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2011)
Staphylococcus aureus Biofilm and Planktonic cultures differentially impact gene expression, mapk phosphorylation, and cytokine production in human keratinocytes
Patrick R. Secor et al.
BMC MICROBIOLOGY (2011)
Inflammatory Responses to Individual Microorganisms in the Lungs of Children With Cystic Fibrosis
Catherine Gangell et al.
CLINICAL INFECTIOUS DISEASES (2011)
Early production of IL-17 protects against acute pulmonary Pseudomonas aeruginosa infection in mice
Jialin Liu et al.
FEMS IMMUNOLOGY AND MEDICAL MICROBIOLOGY (2011)
Infection of Polarized Airway Epithelial Cells by Normal and Small-Colony Variant Strains of Staphylococcus aureus Is Increased in Cells with Abnormal Cystic Fibrosis Transmembrane Conductance Regulator Function and Is Influenced by NF-κB
Gabriel Mitchell et al.
INFECTION AND IMMUNITY (2011)
Anaerobiosis-Induced Loss of Cytotoxicity Is Due to Inactivation of Quorum Sensing in Pseudomonas aeruginosa
Kang-Mu Lee et al.
INFECTION AND IMMUNITY (2011)
Pulmonary Proteases in the Cystic Fibrosis Lung Induce Interleukin 8 Expression from Bronchial Epithelial Cells via a Heme/Meprin/Epidermal Growth Factor Receptor/Toll-like Receptor Pathway
Sonya Cosgrove et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2011)
Strategies of professional phagocytes in vivo: unlike macrophages, neutrophils engulf only surface-associated microbes
Emma Colucci-Guyon et al.
JOURNAL OF CELL SCIENCE (2011)
Azithromycin blocks autophagy and may predispose cystic fibrosis patients to mycobacterial infection
Maurizio Renna et al.
JOURNAL OF CLINICAL INVESTIGATION (2011)
Inhaled mannitol in patients with cystic fibrosis: A randomised open-label dose response trial
Alejandro Teper et al.
JOURNAL OF CYSTIC FIBROSIS (2011)
Abnormal Trafficking and Degradation of TLR4 Underlie the Elevated Inflammatory Response in Cystic Fibrosis
Emanuela M. Bruscia et al.
JOURNAL OF IMMUNOLOGY (2011)
IL-17A and TNF-α Exert Synergistic Effects on Expressi on of CXCL5 by Alveolar Type II Cells In Vivo and In Vitro
Yuhong Liu et al.
JOURNAL OF IMMUNOLOGY (2011)
Mechanisms controlling Th17 cytokine expression and host defense
Jeremy P. McAleer et al.
JOURNAL OF LEUKOCYTE BIOLOGY (2011)
A CFTR Potentiator in Patients with Cystic Fibrosis and the G551D Mutation
Bonnie W. Ramsey et al.
NEW ENGLAND JOURNAL OF MEDICINE (2011)
The ΔF508 Mutation Causes CFTR Misprocessing and Cystic Fibrosis-Like Disease in Pigs
Lynda S. Ostedgaard et al.
SCIENCE TRANSLATIONAL MEDICINE (2011)
Streptococcus pneumoniae DNA Initiates Type I Interferon Signaling in the Respiratory Tract
Dane Parker et al.
MBIO (2011)
Acute inhalation of hypertonic saline does not improve mucociliary clearance in all children with cystic fibrosis
Beth L. Laube et al.
BMC PULMONARY MEDICINE (2011)
A Pseudomonas aeruginosa Toxin that Hijacks the Host Ubiquitin Proteolytic System
Jennifer M. Bomberger et al.
PLOS PATHOGENS (2011)
AAV Exploits Subcellular Stress Associated with Inflammation, Endoplasmic Reticulum Expansion, and Misfolded Proteins in Models of Cystic Fibrosis
Jarrod S. Johnson et al.
PLOS PATHOGENS (2011)
TLR-4-Mediated Innate Immunity Is Reduced in Cystic Fibrosis Airway Cells
Gerrit John et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2010)
Impaired Interleukin-8 Chemokine Secretion by Staphylococcus aureus-Activated Epithelium and T-Cell Chemotaxis in Cystic Fibrosis
Denise Al Alam et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2010)
Loss of Anion Transport without Increased Sodium Absorption Characterizes Newborn Porcine Cystic Fibrosis Airway Epithelia
Jeng-Haur Chen et al.
CELL (2010)
The Changing Microbial Epidemiology in Cystic Fibrosis
John J. LiPuma
CLINICAL MICROBIOLOGY REVIEWS (2010)
Biofilm-forming Pseudomonas aeruginosa bacteria undergo lipopolysaccharide structural modifications and induce enhanced inflammatory cytokine response in human monocytes
Cristina D. Ciornei et al.
INNATE IMMUNITY (2010)
Effect of Azithromycin on Pulmonary Function in Patients With Cystic Fibrosis Uninfected With Pseudomonas aeruginosa A Randomized Controlled Trial
Lisa Saiman et al.
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION (2010)
Association Between Respiratory Tract Methicillin-Resistant Staphylococcus aureus and Survival in Cystic Fibrosis
Elliott C. Dasenbrook et al.
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION (2010)
Airway Surface Liquid Volume Regulation Determines Different Airway Phenotypes in Liddle Compared with βENaC-overexpressing Mice
Marcus A. Mall et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2010)
Loss of Cystic Fibrosis Transmembrane Conductance Regulator Function Enhances Activation of p38 and ERK MAPKs, Increasing Interleukin-6 Synthesis in Airway Epithelial Cells Exposed to Pseudomonas aeruginosa
Julie Berube et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2010)
Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis
Xingshen Sun et al.
JOURNAL OF CLINICAL INVESTIGATION (2010)
Vitamin D3 attenuates Th2 responses to Aspergillus fumigatus mounted by CD4+ T cells from cystic fibrosis patients with allergic bronchopulmonary aspergillosis
James L. Kreindler et al.
JOURNAL OF CLINICAL INVESTIGATION (2010)
The Streptococcus milleri Population of a Cystic Fibrosis Clinic Reveals Patient Specificity and Intraspecies Diversity
Christopher D. Sibley et al.
JOURNAL OF CLINICAL MICROBIOLOGY (2010)
IFN Regulatory Factor 3 Contributes to the Host Response during Pseudomonas aeruginosa Lung Infection in Mice
Svetlana O. Carrigan et al.
JOURNAL OF IMMUNOLOGY (2010)
Extracellular DNA: A Major Proinflammatory Component of Pseudomonas aeruginosa Biofilms
Juan I. Fuxman Bass et al.
JOURNAL OF IMMUNOLOGY (2010)
In Cystic Fibrosis Homozygotes and Heterozygotes, Neutrophil Apoptosis Is Delayed and Modulated by Diamide or Roscovitine: Evidence for an Innate Neutrophil Disturbance
Sandra Moriceau et al.
JOURNAL OF INNATE IMMUNITY (2010)
Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition
Alessandro Luciani et al.
NATURE CELL BIOLOGY (2010)
Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation
Frank J. Accurso et al.
NEW ENGLAND JOURNAL OF MEDICINE (2010)
Cystic Fibrosis Pigs Develop Lung Disease and Exhibit Defective Bacterial Eradication at Birth
David A. Stoltz et al.
SCIENCE TRANSLATIONAL MEDICINE (2010)
Parallel Evolution in Pseudomonas aeruginosa over 39,000 Generations In Vivo
Holly K. Huse et al.
MBIO (2010)
Elevated expression of both mRNA and protein levels of IL-17A in sputum of stable Cystic Fibrosis patients
Ann Decraene et al.
RESPIRATORY RESEARCH (2010)
Airway surface liquid depth measured in ex vivo fragments of pig and human trachea: dependence on Na+ and Cl- channel function
Yuanlin Song et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2009)
Novel human bronchial epithelial cell lines for cystic fibrosis research
M. L. Fulcher et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2009)
Pseudomonas aeruginosa Microevolution during Cystic Fibrosis Lung Infection Establishes Clones with Adapted Virulence
Alessandra Bragonzi et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2009)
Macrophages Directly Contribute to the Exaggerated Inflammatory Response in Cystic Fibrosis Transmembrane Conductance Regulator-/- Mice
Emanuela M. Bruscia et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2009)
Oxidative Stress Causes IL8 Promoter Hyperacetylation in Cystic Fibrosis Airway Cell Models
Toni R. Bartling et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2009)
Coronin-1 Is Associated with Neutrophil Survival and Is Cleaved during Apoptosis: Potential Implication in Neutrophils from Cystic Fibrosis Patients
Sandra Moriceau et al.
JOURNAL OF IMMUNOLOGY (2009)
Decreased Levels of Secretory Leucoprotease Inhibitor in the Pseudomonas-Infected Cystic Fibrosis Lung Are Due to Neutrophil Elastase Degradation
Sinead Weldon et al.
JOURNAL OF IMMUNOLOGY (2009)
Dynamics of Adaptive Microevolution of Hypermutable Pseudomonas aeruginosa during Chronic Pulmonary Infection in Patients with Cystic Fibrosis
Christina Hoboth et al.
JOURNAL OF INFECTIOUS DISEASES (2009)
Respiratory Syncytial Virus Infection Facilitates Acute Colonization of Pseudomonas aeruginosa in Mice
Angelica M. M. de Vrankrijker et al.
JOURNAL OF MEDICAL VIROLOGY (2009)
CFTR Is a Negative Regulator of NFκB Mediated Innate Immune Response
Neeraj Vij et al.
PLOS ONE (2009)
Pseudomonas aeruginosa Biofilms in the Respiratory Tract of Cystic Fibrosis Patients
Thomas Bjarnsholt et al.
PEDIATRIC PULMONOLOGY (2009)
The antioxidant role of thiocyanate in the pathogenesis of cystic fibrosis and other inflammation-related diseases
Yanping Xu et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
Fredrick Van Goor et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)
Cystic fibrosis transmembrane conductance regulator controls lung proteasomal degradation and nuclear factor-κB activity in conditions of oxidative stress
Emilie Boncoeur et al.
AMERICAN JOURNAL OF PATHOLOGY (2008)
Pharmacoscintigraphic and pharmacokinetic evaluation of tobramycin DPI formulations in cystic fibrosis patients
Gabrielle Pilcer et al.
EUROPEAN JOURNAL OF PHARMACEUTICS AND BIOPHARMACEUTICS (2008)
Oxidative stress caused by pyocyanin impairs CFFR Cl- transport in human bronchial epithelial cells
Christian Schwarzer et al.
FREE RADICAL BIOLOGY AND MEDICINE (2008)
Production of CFTR-null and CFTR-ΔF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer
Christopher S. Rogers et al.
JOURNAL OF CLINICAL INVESTIGATION (2008)
Anti-inflammatory effect of miglustat in bronchial epithelial cells
Maria Cristina Dechecchi et al.
JOURNAL OF CYSTIC FIBROSIS (2008)
High mobility group protein-1 inhibits phagocytosis of apoptotic neutrophils through binding to phosphatidylserine
Gang Liu et al.
JOURNAL OF IMMUNOLOGY (2008)
The Pseudomonas toxin pyocyanin inhibits the dual oxidase-based antimicrobial system as it imposes oxidative stress on airway epithelial cells
Balazs Rada et al.
JOURNAL OF IMMUNOLOGY (2008)
The role of chloride anion and CFTR in killing of Pseudomonas aeruginosa by normal and CF neutrophils
Richard G. Painter et al.
JOURNAL OF LEUKOCYTE BIOLOGY (2008)
Relationship between Inhaled Corticosteroid Therapy and Rate of Lung Function Decline in Children with Cystic Fibrosis
Clement L. Ren et al.
JOURNAL OF PEDIATRICS (2008)
TRAM couples endocytosis of Toll-like receptor 4 to the induction of interferon-beta
Jonathan C. Kagan et al.
NATURE IMMUNOLOGY (2008)
Bronchial Provocation Testing With Dry Powder Mannitol in Children With Cystic Fibrosis
Caro Minasian et al.
PEDIATRIC PULMONOLOGY (2008)
Prevalence and Impact of Respiratory Viral Infections in Young Children With Cystic Fibrosis: Prospective Cohort Study
Bart E. van Ewijk et al.
PEDIATRICS (2008)
Prolonged survival of neutrophils from patients with ΔF508 CFTR mutations
D. J. McKeon et al.
THORAX (2008)
Cleavage of CXCR1 on neutrophils disables bacterial killing in cystic fibrosis lung disease
Dominik Hartl et al.
NATURE MEDICINE (2007)
Cystic fibrosis transmembrane conductance regulator-independent phagosomal acidification in macrophages
Peter M. Haggie et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Unique lipid A modifications in Pseudomonas aeruginosa isolated from the airways of patients with cystic fibrosis
Robert K. Ernst et al.
JOURNAL OF INFECTIOUS DISEASES (2007)
Phase 2 randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis
Robin R. Deterding et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2007)
Early inflammation in the airways of a cystic fibrosis foetus
Catherine Verhaeghe et al.
JOURNAL OF CYSTIC FIBROSIS (2007)
Role of IKK and ERK pathways in intrinsic inflammation of cystic fibrosis airways
Catherine Verhaeghe et al.
BIOCHEMICAL PHARMACOLOGY (2007)
Molecular epidemiology and dynamics of Pseudomonas aeruginosa populations in lungs of cystic fibrosis patients
Lars Jelsbak et al.
INFECTION AND IMMUNITY (2007)
MPB-07 reduces the inflammatory response to Pseudomonas aeruginosa in cystic fibrosis bronchial cells
Maria Cristina Dechecchi et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2007)
A role of Toll-IL-1 receptor domain-containing adaptor-inducing IFN-β in the host response to Pseudomonas aeruginosa lung infection in mice
Melanie R. Power et al.
JOURNAL OF IMMUNOLOGY (2007)
A morphometric study of mucins and small airway plugging in cystic fibrosis
Pierre-Regis Burgel et al.
THORAX (2007)
IL-23 mediates inflammatory responses to mucoid Pseudomonas aeruginosa lung infection in mice
Patricia J. Dubin et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2007)
A novel host defense system of airways is defective in cystic fibrosis
Patryk Moskwa et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2007)
Prevalence and clinical significance of Staphylococcus aureus small-colony variants in cystic fibrosis lung disease
Silke Besier et al.
JOURNAL OF CLINICAL MICROBIOLOGY (2007)
Cathepsin-G interferes with clearance of Pseudomonas aeruginosa from mouse lungs
Julia Sedor et al.
PEDIATRIC RESEARCH (2007)
CFTR regulates phagosome acidification in macrophages and alters bactericidal activity
Anke Di et al.
NATURE CELL BIOLOGY (2006)
Anti-inflammatory cytokines in cystic fibrosis lung disease
V. Starosta et al.
EUROPEAN RESPIRATORY JOURNAL (2006)
Innate immune response in CF airway epithelia: hyperinflammatory?
Terry E. Machen
AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY (2006)
Genetic adaptation by Pseudomonas aeruginosa to the airways of cystic fibrosis patients
Eric E. Smith et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)
Oxidant stress suppresses CFTR expression
AM Cantin et al.
AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY (2006)
Pulmonary T(H)2 response in Pseudomonas aeruginos-infected patients with cystic fibrosis
D Hartl et al.
JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY (2006)
Genetic modifiers of lung disease in cystic fibrosis
ML Drumm et al.
NEW ENGLAND JOURNAL OF MEDICINE (2005)
Pyocyanin and its precursor phenazine-1-carboxylic acid increase IL-8 and intercellular adhesion molecule-1 expression in human airway epithelial cells by oxidant-dependent mechanisms
DC Look et al.
JOURNAL OF IMMUNOLOGY (2005)
Cystic fibrosis and lipoxins
CL Karp et al.
PROSTAGLANDINS LEUKOTRIENES AND ESSENTIAL FATTY ACIDS (2005)
The effect of cyclosporin A on airway cell proinflammatory signaling and pneumonia
V Waters et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2005)
Regulation of Pseudomonas quinolone signal synthesis in Pseudomonas aeruginosa
DS Wade et al.
JOURNAL OF BACTERIOLOGY (2005)
Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-a and granulocyte colony-stimulating factor in bronchial epithelium: Implications for airway inflammation in cystic fibrosis
F McAllister et al.
JOURNAL OF IMMUNOLOGY (2005)
Thymidine-dependent Staphylococcus aureus small-colony variants are associated with extensive alterations in regulator and virulence gene expression profiles
BC Kahl et al.
INFECTION AND IMMUNITY (2005)
Genotype-phenotype correlation for pulmonary function in cystic fibrosis
J de Gracia et al.
THORAX (2005)
Chronic airway Infection/Inflammation induces a Ca2+i-dependent hyperinflammatory response in human cystic fibrosis airway epithelia
CMP Ribeiro et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
TLR-induced inflammation in cystic fibrosis and non-cystic fibrosis airway epithelial cells
CM Greene et al.
JOURNAL OF IMMUNOLOGY (2005)
Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway
CL Karp et al.
NATURE IMMUNOLOGY (2004)
Increased frequency of genomic alterations in Staphylococcus aureus during chronic infection is in part due to phage mobilization
C Goerke et al.
JOURNAL OF INFECTIOUS DISEASES (2004)
Analysis of quorum sensing-deficient clinical isolates of Pseudomonas aeruginosa
JA Schaber et al.
JOURNAL OF MEDICAL MICROBIOLOGY (2004)
Impaired nitric oxide synthase-2 signaling pathway in cystic fibrosis airway epithelium
S Zheng et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2004)
Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice
AM van Heeckeren et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2004)
Toll-like receptors in normal and cystic fibrosis airway epithelial cells
A Muir et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2004)
Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice
M Mall et al.
NATURE MEDICINE (2004)
Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium
RD Coakley et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)
Azithromycin in, patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa -: A randomized controlled trial
L Saiman et al.
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION (2003)
Nuclear factor-κB p50 limits inflammation and prevents lung injury during Escherichia coli pneumonia
JP Mizgerd et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2003)
Bacterial diversity in cases of lung infection in cystic fibrosis patients: 16S ribosomal DNA (rDNA) length heterogeneity PCR and 16S rDNA terminal restriction fragment length polymorphism profiling
GB Rogers et al.
JOURNAL OF CLINICAL MICROBIOLOGY (2003)
Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study
EF McKone et al.
LANCET (2003)
Impaired innate host defense causes susceptibility to respiratory virus infections in cystic fibrosis
S Zheng et al.
IMMUNITY (2003)
CFTR directly mediates nucleotide-regulated glutathione flux
I Kogan et al.
EMBO JOURNAL (2003)
Endothelium-derived toll-like receptor-4 is the key molecule in LPS-induced neutrophil sequestration into lungs
G Andonegui et al.
JOURNAL OF CLINICAL INVESTIGATION (2003)
Transcriptional adaptation to cystic fibrosis transmembrane conductance regulator deficiency
Y Xu et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Plasma membrane CFTR regulates RANTES expression via its C-terminal PDZ-interacting motif
K Estell et al.
MOLECULAR AND CELLULAR BIOLOGY (2003)
Induced sputum inflammatory measures correlate with lung function in children with cystic fibrosis
SD Sagel et al.
JOURNAL OF PEDIATRICS (2002)
A simple alfalfa seedling infection model for Pseudomonas aeruginosa strains associated with cystic fibrosis shows AlgT (sigma-22) and RhIR contribute to pathogenesis
L Silo-Suh et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)
Bacterial stimulation of epithelial G-CSF and GM-CSF expression promotes PMN survival in CF airways
S Saba et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2002)
Interleukin-17 stimulates the expression of interleukin-8, growth-related oncogene-α, and granulocyte-colony-stimulating factor by human airway epithelial cells
CE Jones et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2002)
Endotoxin activity and inflammatory markers in the airways of young patients with cystic fibrosis
MS Muhlebach et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2002)
Human Toll-like receptor 4 recognizes host-specific LPS modifications
AM Hajjar et al.
NATURE IMMUNOLOGY (2002)
Elastase-mediated phosphatidylserine receptor cleavage impairs apoptotic cell clearance in cystic fibrosis and bronchiectasis
RW Vandivier et al.
JOURNAL OF CLINICAL INVESTIGATION (2002)
Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis
M Rosenfeld et al.
PEDIATRIC PULMONOLOGY (2001)
Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na+] and pH but elevated viscosity
S Jayaraman et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2001)
Rethinking cystic fibrosis pathology: The critical role of abnormal reduced glutathione (GSH) transport caused by CFTR mutation
VM Hudson
FREE RADICAL BIOLOGY AND MEDICINE (2001)
Quorum-sensing signals indicate that cystic fibrosis lungs are infected with bacterial biofilms
PK Singh et al.
NATURE (2000)
Inflammation and infection in naive human cystic fibrosis airway grafts
R Tirouvanziam et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2000)
In vivo alterations of IFN regulatory factor-1 and PIAS1 protein levels in cystic fibrosis epithelium
TJ Kelley et al.
JOURNAL OF CLINICAL INVESTIGATION (2000)
Oxidative stress and regulation of glutathione in lung inflammation
I Rahman et al.
EUROPEAN RESPIRATORY JOURNAL (2000)
Exaggerated activation of nuclear factor-kappa B and altered I kappa B-beta processing in cystic fibrosis bronchial epithelial cells
A Venkatakrishnan et al.
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2000)