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Zhijian J. Chen et al.
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Karoly Varga et al.
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Kim Newton et al.
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Om V. Singh et al.
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A Swiatecka-Urban et al.
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AL Berger et al.
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M Sharma et al.
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A Gnann et al.
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JM Younger et al.
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Y Kawaguchi et al.
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Y Yoshida et al.
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J Fu et al.
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GC Meacham et al.
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