相关参考文献
注意：仅列出部分参考文献，下载原文获取全部文献信息。Abrogation of neutral cholesterol ester hydrolytic activity causes adrenal enlargement
Keisuke Ohta et al.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS (2011)
Identification of StARD3 as a Lutein-Binding Protein in the Macula of the Primate Retina
Binxing Li et al.
BIOCHEMISTRY (2011)
Subcellular localization and regulation of StarD4 protein in macrophages and fibroblasts
Daniel Rodriguez-Agudo et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2011)
Cholesterol-Dependent Degradation of Squalene Monooxygenase, a Control Point in Cholesterol Synthesis beyond HMG-CoA Reductase
Saloni Gill et al.
CELL METABOLISM (2011)
The Molecular Biology, Biochemistry, and Physiology of Human Steroidogenesis and Its Disorders
Walter L. Miller et al.
ENDOCRINE REVIEWS (2011)
High allele frequency of the p.Q258X mutation and identification of a novel mis-splicing mutation in the STAR gene in Korean patients with congenital lipoid adrenal hyperplasia
Jae-Min Kim et al.
EUROPEAN JOURNAL OF ENDOCRINOLOGY (2011)
Structural Basis for Three-step Sequential Catalysis by the Cholesterol Side Chain Cleavage Enzyme CYP11A1
Natalia Mast et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2011)
Novel Androstenetriol Interacts with the Mitochondrial Translocator Protein and Controls Steroidogenesis
Andrew Midzak et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2011)
Identification of Luminal Loop 1 of Scap Protein as the Sterol Sensor That Maintains Cholesterol Homeostasis
Massoud Motamed et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2011)
Partial Defect in the Cholesterol Side-Chain Cleavage Enzyme P450scc (CYP11A1) Resembling Nonclassic Congenital Lipoid Adrenal Hyperplasia
Taninee Sahakitrungruang et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2011)
Malformation syndromes caused by disorders of cholesterol synthesis
Forbes D. Porter et al.
JOURNAL OF LIPID RESEARCH (2011)
A sensitive and specific LC-MS/MS method for rapid diagnosis of Niemann-Pick C1 disease from human plasma
Xuntian Jiang et al.
JOURNAL OF LIPID RESEARCH (2011)
StarD7 Gene Expression in Trophoblast Cells: Contribution of SF-1 and Wnt-β-Catenin Signaling
Viviana Rena et al.
MOLECULAR ENDOCRINOLOGY (2011)
Genetic Variant of the Scavenger Receptor BI in Humans
Menno Vergeer et al.
NEW ENGLAND JOURNAL OF MEDICINE (2011)
Mitochondrial heat shock protein participates in placental steroidogenesis
S. Olvera-Sanchez et al.
PLACENTA (2011)
Comparative Structural Analysis of Lipid Binding START Domains
Ann-Gerd Thorsell et al.
PLOS ONE (2011)
Histone deacetylase inhibitor treatment dramatically reduces cholesterol accumulation in Niemann-Pick type C1 mutant human fibroblasts
Nina H. Pipalia et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)
Structural basis for pregnenolone biosynthesis by the mitochondrial monooxygenase system
Natallia Strushkevich et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)
Greasing Their Way: Lipid Modifications Determine Protein Association with Membrane Rafts
Ilya Levental et al.
BIOCHEMISTRY (2010)
Lipid Trafficking sans Vesicles: Where, Why, How?
William A. Prinz
CELL (2010)
Identification of Surface Residues on Niemann-Pick C2 Essential for Hydrophobic Handoff of Cholesterol to NPC1 in Lysosomes
Michael L. Wang et al.
CELL METABOLISM (2010)
StarD7 Mediates the Intracellular Trafficking of Phosphatidylcholine to Mitochondria
Yasuhiro Horibata et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2010)
Targeted disruption of steroidogenic acute regulatory protein D4 leads to modest weight reduction and minor alterations in lipid metabolism
Joshua J. Riegelhaupt et al.
JOURNAL OF LIPID RESEARCH (2010)
MLN64 mediates egress of cholesterol from endosomes to mitochondria in the absence of functional Niemann-Pick Type C1 protein
Mark Charman et al.
JOURNAL OF LIPID RESEARCH (2010)
Revitalizing membrane rafts: new tools and insights
Kai Simons et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2010)
Non-vesicular lipid transport by lipid-transfer proteins and beyond
Sima Lev
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2010)
Weekly Cyclodextrin Administration Normalizes Cholesterol Metabolism in Nearly Every Organ of the Niemann-Pick Type C1 Mouse and Markedly Prolongs Life
Charina M. Ramirez et al.
PEDIATRIC RESEARCH (2010)
Humans possess two mitochondrial ferredoxins, Fdx1 and Fdx2, with distinct roles in steroidogenesis, heme, and Fe/S cluster biosynthesis
Alex D. Sheftel et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2010)
Endocytosis of beta-cyclodextrins is responsible for cholesterol reduction in Niemann-Pick type C mutant cells
Anton I. Rosenbaum et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2010)
HDL miR-ed Down by SREBP Introns
Michael S. Brown et al.
SCIENCE (2010)
MicroRNA-33 and the SREBP Host Genes Cooperate to Control Cholesterol Homeostasis
S. Hani Najafi-Shoushtari et al.
SCIENCE (2010)
MiR-33 Contributes to the Regulation of Cholesterol Homeostasis
Katey J. Rayner et al.
SCIENCE (2010)
Cholesterol Oxidation Products Are Sensitive and Specific Blood-Based Biomarkers for Niemann-Pick C1 Disease
Forbes D. Porter et al.
SCIENCE TRANSLATIONAL MEDICINE (2010)
Cell cholesterol homeostasis: Mediation by active cholesterol
Theodore L. Steck et al.
TRENDS IN CELL BIOLOGY (2010)
Hydrophobic Core of the Steroidogenic Acute Regulatory Protein for Cholesterol Transport
Himangshu S. Bose et al.
BIOCHEMISTRY (2009)
Steroidogenic Acute Regulatory Protein Has a More Open Conformation Than the Independently Folded Smaller Subdomains
Himangshu S. Bose et al.
BIOCHEMISTRY (2009)
Targeting and Insertion of the Cholesterol-Binding Translocator Protein into the Outer Mitochondrial Membrane
Malena B. Rone et al.
BIOCHEMISTRY (2009)
Lipid droplet-organelle interactions; sharing the fats
Samantha Murphy et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2009)
Intracellular sterol dynamics
Bruno Mesmin et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2009)
Cholesterol transport in steroid biosynthesis: Role of protein-protein interactions and implications in disease states
Malena B. Rone et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2009)
Long-term metabolic, endocrine, and neuropsychological outcome of hematopoietic cell transplantation for Wolman disease
J. Tolar et al.
BONE MARROW TRANSPLANTATION (2009)
Pathological evidence of Wolman's disease following hematopoietic stem cell transplantation despite correction of lysosomal acid lipase activity
M. M. Gramatges et al.
BONE MARROW TRANSPLANTATION (2009)
Structure of N-Terminal Domain of NPC1 Reveals Distinct Subdomains for Binding and Transfer of Cholesterol
Hyock Joo Kwon et al.
CELL (2009)
Conception and pregnancy outcome in a patient with 11-bp deletion of the steroidogenic acute regulatory protein gene
Amalia Sertedaki et al.
FERTILITY AND STERILITY (2009)
Segregation of sphingolipids and sterols during formation of secretory vesicles at the trans-Golgi network
Robin W. Klemm et al.
JOURNAL OF CELL BIOLOGY (2009)
Oxidative stress in NPC1 deficient cells: protective effect of allopregnanolone
Stefania Zampieri et al.
JOURNAL OF CELLULAR AND MOLECULAR MEDICINE (2009)
Nonclassic Lipoid Congenital Adrenal Hyperplasia Masquerading as Familial Glucocorticoid Deficiency
Louise A. Metherell et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2009)
Gonadal Function, First Cases of Pregnancy, and Child Delivery in a Woman with Lipoid Congenital Adrenal Hyperplasia
Khalil Khoury et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2009)
A Novel Homozygous Mutation in CYP11A1 Gene Is Associated with Late-Onset Adrenal Insufficiency and Hypospadias in a 46, XY Patient
Petr Rubtsov et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2009)
The differential regulation of steroidogenic acute regulatory protein-mediated steroidogenesis by type I and type II PKA in MA-10 cells
Matthew T. Dyson et al.
MOLECULAR AND CELLULAR ENDOCRINOLOGY (2009)
Cholesteryl Ester Storage Disease (CESD) due to novel mutations in the LIPA gene
Livia Pisciotta et al.
MOLECULAR GENETICS AND METABOLISM (2009)
Reversal of defective lysosomal transport in NPC disease ameliorates liver dysfunction and neurodegeneration in the npc1-/- mouse
Benny Liu et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)
A role for lipid droplets in inter-membrane lipid traffic
John K. Zehmer et al.
PROTEOMICS (2009)
StAR-like activity and molten globule Behavior of StARD6, a male germ-line protein
Himangshu S. Bose et al.
BIOCHEMISTRY (2008)
Mitochondrial A-kinase anchoring protein 121 binds type II protein kinase A and enhances steroidogenic acute regulatory protein-mediated steroidogenesis in MA-10 mouse Leydig tumor cells
Matthew T. Dyson et al.
BIOLOGY OF REPRODUCTION (2008)
Nanoclusters of GPI-Anchored Proteins Are Formed by Cortical Actin-Driven Activity
Debanjan Goswami et al.
CELL (2008)
LBP-1b, LBP-9, and LBP-32/MGR detected in syncytiotrophoblasts from first-trimester human placental tissue and their transcriptional regulation
Ying C. Henderson et al.
DNA AND CELL BIOLOGY (2008)
Identification of Neutral Cholesterol Ester Hydrolase, a Key Enzyme Removing Cholesterol from Macrophages
Hiroaki Okazaki et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Steroidogenic activity of StAR requires contact with mitochondrial VDAC1 and phosphate carrier protein
Mahuya Bose et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
The gregarious lipid droplet
Joel M. Goodman
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Severe combined adrenal and gonadal deficiency caused by novel mutations in the cholesterol side chain cleavage enzyme, P450scc
Chan Jong Kim et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2008)
Intracellular cholesterol transporter StarD4 binds free cholesterol and increases cholesteryl ester formation
Daniel Rodriguez-Agudo et al.
JOURNAL OF LIPID RESEARCH (2008)
Cellular cholesterol trafficking and compartmentalization
Elina Ikonen
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2008)
Membrane lipids: where they are and how they behave
Gerrit van Meer et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2008)
NPC2 facilitates bidirectional transfer of cholesterol between NPC1 and lipid bilayers, a step in cholesterol egress from lysosomes
Rodney E. Infante et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)
Structure of the human voltage-dependent anion channel
Monika Bayrhuber et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)
Cholesterol homeostasis and the escape tendency (activity) of plasma membrane cholesterol
Yvonne Lange et al.
PROGRESS IN LIPID RESEARCH (2008)
Solution structure of the integral human membrane protein VDAC-1 in detergent micelles
Sebastian Hiller et al.
SCIENCE (2008)
Purified NPC1 protein - I. Binding of cholesterol and oxysterols to a 1278-amino acid membrane protein
Rodney E. Infante et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Purified NPC1 protein - II. Localization of sterol binding to a 240-amino acid soluble luminal loop
Rodney E. Infante et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Effect of line tension on the lateral organization of lipid membranes
Ana J. Garcia-Saez et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
SNARE proteins mediate fusion between cytosolic lipid droplets and are implicated in insulin sensitivity
Pontus Bostrom et al.
NATURE CELL BIOLOGY (2007)
Synaptosomal-associated protein 25 gene expression is hormonally regulated during ovulation and is involved in cytokine/chemokine exocytosis from granulosa cells
Masayuki Shimada et al.
MOLECULAR ENDOCRINOLOGY (2007)
Miglustat for treatment of Niemann-Pick C disease: a randomised controlled study
Marc C. Patterson et al.
LANCET NEUROLOGY (2007)
Structural basis of sterol binding by NPC2, a lysosomal protein deficient in Niemann-Pick type C2 disease
Sujuan Xu et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Successful treatment of Wolman disease by unrelated umbilical cord blood transplantation
Jerry Stein et al.
EUROPEAN JOURNAL OF PEDIATRICS (2007)
Steroidogenic acute regulatory protein (StAR), a novel mitochondrial cholesterol transporter
Walter L. Miller
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2007)
GPI-anchored receptor clusters transiently recruit Lyn and Gα for temporary cluster immobilization and Lyn activation:: single-molecule tracking study 1
Kenichi G. N. Suzuki et al.
JOURNAL OF CELL BIOLOGY (2007)
Cholesterol binding does not predict activity of the steroidogenic acute regulatory protein, StAR
Bo Y. Baker et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Insulin signalling to mTOR mediated by the Akt/PKB substrate PRAS40
Emilie Vander Haar et al.
NATURE CELL BIOLOGY (2007)
Human LBP-32/MGR is a repressor of the P450scc in human choriocarcinoma cell line JEG-3
Y. C. Henderson et al.
PLACENTA (2007)
ABCA1: at the nexus of cholesterol, HDL and atherosclerosis
Alan D. Attie
TRENDS IN BIOCHEMICAL SCIENCES (2007)
StAR search - What we know about how the steroidogenic acute regulatory protein mediates mitochondrial cholesterol import
Walter L. Miller
MOLECULAR ENDOCRINOLOGY (2007)
Protein-protein interactions mediate mitochondrial cholesterol transport and steroid biosynthesis
Jun Liu et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2006)
Modeling the structure of the StART domains of MLN64 and StAR proteins in complex with cholesterol
Marta Murcia et al.
JOURNAL OF LIPID RESEARCH (2006)
Nonclassic congenital lipoid adrenal hyperplasia: A new disorder of the steroidogenic acute regulatory protein with very late presentation and normal male genitalia
Bo Y. Baker et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2006)
Mechanism of cholesterol transfer from the Niemann-Pick type C2 protein to model membranes supports a role in lysosomal cholesterol transport
Sunita R. Cheruku et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2006)
Pregnane X receptor (PXR) activation: A mechanism for neuroprotection in a mouse model of Niemann-Pick C disease
S. Joshua Langmade et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)
Translocator protein (18 kDa):: new nomenclature for the peripheral-type benzodiazepine receptor based on its structure and molecular function
Vassilios Papadopoulos et al.
TRENDS IN PHARMACOLOGICAL SCIENCES (2006)
Clinical case seminar - Homozygous mutation of P450 side-chain cleavage enzyme gene (CYP11A1) in 46, XY patient with adrenal insufficiency, complete sex reversal, and agenesis of corpus callosum
Hessa al Kandari et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2006)
MLN64 and MENTHO, two mediators of enclosomal cholesterol transport
F. Alpy et al.
BIOCHEMICAL SOCIETY TRANSACTIONS (2006)
Protein sensors for membrane sterols
JL Goldstein et al.
CELL (2006)
Nonvesicular sterol transport: two protein families and a sterol sensor?
Hongyuan Yang
TRENDS IN CELL BIOLOGY (2006)
A pH-dependent molten globule transition is required for activity of the steroidogenic acute regulatory protein, StAR
BY Baker et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Allopregnanolone treatment, both as a single injection or repetitively, delays demyelination and enhances survival of Niemann-Pick C mice
I Ahmad et al.
JOURNAL OF NEUROSCIENCE RESEARCH (2005)
Role of cholesterol and lipid organization in disease
FR Maxfield et al.
NATURE (2005)
Multiple signaling pathways regulating steroidogenesis and steroidogenic acute regulatory protein expression: More complicated than we thought
DM Stocco et al.
MOLECULAR ENDOCRINOLOGY (2005)
Human StarD5, a cytosolic StAR-related lipid binding protein
D Rodriguez-Agudo et al.
JOURNAL OF LIPID RESEARCH (2005)
Involvement of protein kinase C and cyclic adenosine 3′,5′-monophosphate-dependent kinase in steroidogenic acute regulatory protein expression and steroid biosynthesis in Leydig cells
Y Jo et al.
BIOLOGY OF REPRODUCTION (2005)
Niemann-Pick type C disease and intracellular cholesterol trafficking
TY Chang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Primary adrenal insufficiency in children: Twenty years experience at the Sainte-Justine Hospital, Montreal
R Perry et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2005)
Differential gene regulation of StarD4 and StarD5 cholesterol transfer proteins - Activation of StarD4 by sterol regulatory element-binding protein-2 and StarD5 by endoplasmic reticulum stress
RE Soccio et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
SREBP pathway responds to sterols and functions as an oxygen sensor in fission yeast
AL Hughes et al.
CELL (2005)
cAMP-PKA signaling to the mitochondria: protein scaffolds, mRNA and phosphatases
A Feliciello et al.
CELLULAR SIGNALLING (2005)
LBP proteins modulate SF1-independent expression of P450scc in human placental JEG-3 cells
NW Huang et al.
MOLECULAR ENDOCRINOLOGY (2005)
Peripheral-type benzodiazepine receptor-mediated action of steroidogenic acute regulatory protein on cholesterol entry into Leydig cell mitochondria
T Hauet et al.
MOLECULAR ENDOCRINOLOGY (2005)
A genetic isolate of congenital lipoid adrenal hyperplasia with atypical clinical findings
X Chen et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2005)
pH-dependent interactions of the carboxyl-terminal helix of steroidogenic acute regulatory protein with synthetic membranes
DC Yaworsky et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Why Syndrome X? From Harold Himsworth to the insulin resistance syndrome
GM Reaven
CELL METABOLISM (2005)
Homozygous disruption of P450 side-chain cleavage (CYP11A1) is associated with prematurity, complete 46,XY sex reversal, and severe adrenal failure
O Hiort et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2005)
Targeted mutation of the MLN64 START domain causes only modest alterations in cellular sterol metabolism
T Kishida et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Hormone-sensitive lipase is required for high-density lipoprotein cholesteryl ester-supported adrenal steroidogenesis
FB Kraemer et al.
MOLECULAR ENDOCRINOLOGY (2004)
Oxysterol binding proteins: in more than one place at one time?
VM Olkkonen et al.
BIOCHEMISTRY AND CELL BIOLOGY (2004)
Structural model of MD-2 and functional role of its basic amino acid clusters involved in cellular lipopolysaccharide recognition
A Gruber et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Niemann-Pick type C disease involves disrupted neurosteroidogenesis and responds to allopregnanolone
LD Griffin et al.
NATURE MEDICINE (2004)
A role for yeast oxysterol-binding protein homologs in endocytosis and in the maintenance of intracellular sterol-lipid distribution
CT Beh et al.
JOURNAL OF CELL SCIENCE (2004)
Development and application of a rat ovarian gene expression database
MS Jo et al.
ENDOCRINOLOGY (2004)
Comparison of cytochrome P450 (CYP) genes from the mouse and human genomes, including nomenclature recommendations for genes, pseudogenes and alternative-splice variants
DR Nelson et al.
PHARMACOGENETICS (2004)
SR-BI and cholesterol uptake into steroidogenic cells
MA Connelly et al.
TRENDS IN ENDOCRINOLOGY AND METABOLISM (2003)
Interaction of hormone-sensitive lipase with steroidogeneic acute regulatory protein - Facilitation of cholesterol transfer in adrenal
WJ Shen et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
StAR-related lipid transfer (START) proteins: Mediators of intracellular lipid metabolism
RE Soccio et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Metastatic lymph node 64 (MLN64), a gene overexpressed in breast cancers, is regulated by Sp/KLF transcription factors
F Alpy et al.
ONCOGENE (2003)
The role of the high-density lipoprotein receptor SR-BI in the lipid metabolism of endocrine and other tissues
A Rigotti et al.
ENDOCRINE REVIEWS (2003)
Trafficking defects in endogenously synthesized cholesterol in fibroblasts, macrophages, hepatocytes, and glial cells from Niemann-Pick type C1 mice
PC Reid et al.
JOURNAL OF LIPID RESEARCH (2003)
Structure of a cholesterol-binding protein deficient in Niemann-Pick type C2 disease
N Friedland et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)
The integrity of a cholesterol-binding pocket in Niemann-Pick C2 protein is necessary to control lysosome cholesterol levels
DC Ko et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)
MENTHO, a MLN64 homologue devoid of the START domain
F Alpy et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Transfer of cholesterol between phospholipid vesicles mediated by the steroidogenic acute regulatory protein (StAR)
RC Tuckey et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Insights into steroidogenic acute regulatory protein (StAR)-dependent cholesterol transfer in mitochondria: evidence from molecular modeling and structure-based thermodynamics supporting the existence of partially unfolded states of StAR
A. P. Mathieu et al.
JOURNAL OF MOLECULAR ENDOCRINOLOGY (2002)
The transcriptional regulating protein of 132 kDa (TReP-132) enhances P450scc gene transcription through interaction with steroidogenic factor-1 in human adrenal cells
F Gizard et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Altered profile of gene expression in rat hearts induced by chronic nicotine consumption
DH Hu et al.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS (2002)
Intracellular cholesterol transport
FR Maxfield et al.
JOURNAL OF CLINICAL INVESTIGATION (2002)
Hormone-sensitive lipase: control of intracellular tri-(di-)acylglycerol and cholesteryl ester hydrolysis
FB Kraemer et al.
JOURNAL OF LIPID RESEARCH (2002)
MLN64 mediates mobilization of lysosomal cholesterol to steroidogenic mitochondria
M Zhang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Compound heterozygous mutations in the cholesterol side-chain cleavage enzyme gene (CYP11A) cause congenital adrenal insufficiency in humans
N Katsumata et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2002)
Structure of human phosphatidylcholine transfer protein in complex with its ligand
SL Roderick et al.
NATURE STRUCTURAL BIOLOGY (2002)
Crystal structure of the Mus musculus cholesterol-regulated START protein 4 (StarD4) containing a StAR-related lipid transfer domain
MJ Romanowski et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)
The cholesterol-regulated StarD4 gene encodes a StAR-related lipid transfer protein with two closely related homologues, StarD5 and StarD6
RE Soccio et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)
Rapid regulation of steroidogenesis by mitochondrial protein import
HS Bose et al.
NATURE (2002)
SREBPs: activators of the complete program of cholesterol and fatty acid synthesis in the liver
JD Horton et al.
JOURNAL OF CLINICAL INVESTIGATION (2002)
Vesicular and non-vesicular sterol transport in living cells -: The endocytic recycling compartment is a major sterol storage organelle
MM Hao et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Disruption of the sterol carrier protein 2 gene in mice impairs biliary lipid and hepatic cholesterol metabolism
M Fuchs et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Mitochondrial processing of newly synthesized steroidogenic acute regulatory protein (StAR), but not total StAR, mediates cholesterol transfer to cytochrome P450 side chain cleavage enzyme in adrenal cells.
IP Artemenko et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Gene structure, intracellular localization, and functional roles of sterol carrier protein-2
AM Gallegos et al.
PROGRESS IN LIPID RESEARCH (2001)
A novel zinc finger protein TReP-132 interacts with CBP/p300 to regulate human CYP11A1 gene expression
F Gizard et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Heterozygous mutation in the cholesterol side chain cleavage enzyme (P450scc) gene in a patient with 46,XY sex reversal and adrenal insufficiency
T Tajima et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2001)
Binding of steroidogenic acute regulatory protein to synthetic membranes suggests an active molten globule
K Christensen et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Molten-globule structure and membrane binding of the N-terminal protease-resistant domain (63-193) of the steroidogenic acute regulatory protein (StAR)
MS Song et al.
BIOCHEMICAL JOURNAL (2001)
Roles of phosphatidylethanolamine and of its several biosynthetic pathways in Saccharomyces cerevisiae
R Birner et al.
MOLECULAR BIOLOGY OF THE CELL (2001)
The steroidogenic acute regulatory protein homolog MLN64, a late endosomal cholesterol-binding protein
F Alpy et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
The cytochrome P450 gene superfamily in Drosophila melanogaster:: Annotation, intron-exon organization and phylogeny
N Tijet et al.
GENE (2001)
Identification of HE1 as the second gene of Niemann-Pick C disease
S Naureckiene et al.
SCIENCE (2000)
Cell biology - How cells handle cholesterol
K Simons et al.
SCIENCE (2000)
Evidence for segregation of sphingomyelin and cholesterol during formation of COPI-coated vesicles
B Brügger et al.
JOURNAL OF CELL BIOLOGY (2000)
Sterol regulatory element-binding proteins (SREBPs): Key regulators of nutritional homeostasis and insulin action
TF Osborne
JOURNAL OF BIOLOGICAL CHEMISTRY (2000)
Mutations in the steroidogenic acute regulatory protein (StAR) in six patients with congenital lipoid adrenal hyperplasia
HS Bose et al.
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM (2000)
N-218 MLN64, a protein with StAR-like steroidogenic activity, is folded and cleaved similarly to StAR
HS Bose et al.
BIOCHEMISTRY (2000)
Effects of high-dose simvastatin on adrenal and gonadal steroidogenesis in men with hypercholesterolemia
AS Dobs et al.
METABOLISM-CLINICAL AND EXPERIMENTAL (2000)
Syntaxin 17 is abundant in steroidogenic cells and implicated in smooth endoplasmic reticulum membrane dynamics
M Steegmaier et al.
MOLECULAR BIOLOGY OF THE CELL (2000)
Synaptosome-associated protein of 25 kilodaltons in oocytes and steroid-producing cells of rat and human ovary: Molecular analysis and regulation by gonadotropins
J Grosse et al.
BIOLOGY OF REPRODUCTION (2000)
Sterol carrier protein-2
U Seedorf et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2000)
Expression of low and high density lipoprotein receptor genes in human adrenals
JQ Liu et al.
EUROPEAN JOURNAL OF ENDOCRINOLOGY (2000)
Structure of sterol carrier protein 2 at 1.8 Å resolution reveals a hydrophobic tunnel suitable for lipid binding
T Choinowski et al.
BIOCHEMISTRY (2000)
Construction and characterization of a catalytic fusion protein system:: P-45011β-adrenodoxin reductase-adrenodoxin
PR Cao et al.
BIOCHIMICA ET BIOPHYSICA ACTA-PROTEIN STRUCTURE AND MOLECULAR ENZYMOLOGY (2000)
Cloning of factors related to HIV-inducible LBP proteins that regulate steroidogenic factor-1-independent human placental transcription of the cholesterol side-chain cleavage enzyme, P450scc
NW Huang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2000)
NMR structure of the sterol carrier protein-2:: Implications for the biological role
FL García et al.
JOURNAL OF MOLECULAR BIOLOGY (2000)
Targeted disruption of hormone-sensitive lipase results in male sterility and adipocyte hypertrophy, but not in obesity
J Osuga et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2000)
Hormonal regulation of steroidogenic enzyme expression in granulosa cells during the peri-ovulatory interval in monkeys
CL Chaffin et al.
MOLECULAR HUMAN REPRODUCTION (2000)
Developmental roles of the steroidogenic acute regulatory protein (StAR) as revealed by StAR knockout mice
T Hasegawa et al.
MOLECULAR ENDOCRINOLOGY (2000)
分享论文
