4.6 Article

Defective CFTR increases synthesis and mass of sphingolipids that modulate membrane composition and lipid signaling

相关参考文献

注意:仅列出部分参考文献,下载原文获取全部文献信息。
Article Biochemistry & Molecular Biology

Fenretinide corrects newly found ceramide deficiency in cystic fibrosis

Claudine Guilbault et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2008)

Article Respiratory System

Fenretinide prevents the development of osteoporosis in Cftr-KO mice

Zienab Saeed et al.

JOURNAL OF CYSTIC FIBROSIS (2008)

Article Biochemistry & Molecular Biology

Ceramide accumulation mediates inflammation, cell death and infection susceptibility in cystic fibrosis

Volker Teichgraeber et al.

NATURE MEDICINE (2008)

Review Cell Biology

Principles of bioactive lipid signalling: lessons from sphingolipids

Yusuf A. Hannun et al.

NATURE REVIEWS MOLECULAR CELL BIOLOGY (2008)

Article Biochemistry & Molecular Biology

Recycling of sphingosine is regulated by the concerted actions of sphingosine-1-phosphate phosphohydrolase 1 and sphingosine kinase 2

Herve Le Stunff et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2007)

Article Biochemistry & Molecular Biology

Is the mammalian serine palmitoyltransferase a high-molecular-mass complex?

Thorsten Hornemann et al.

BIOCHEMICAL JOURNAL (2007)

Article Medicine, Research & Experimental

Direct interaction with filamins modulates the stability and plasma membrane expression of CFTR

William R. Thelin et al.

JOURNAL OF CLINICAL INVESTIGATION (2007)

Article Medicine, General & Internal

Evidence for airway surface dehydration as the initiating event in CF airway disease

R. C. Boucher

JOURNAL OF INTERNAL MEDICINE (2007)

Article Biochemistry & Molecular Biology

Cloning and initial characterization of a new subunit for mammalian serine-palmitoyltransferase

Thorsten Hornemann et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2006)

Article Immunology

Inhibition of IL-8 release from CFTR-deficient lung epithelial cells following pre-treatment with fenretinide

Regina Maria Vilela et al.

INTERNATIONAL IMMUNOPHARMACOLOGY (2006)

Article Biochemistry & Molecular Biology

Respiratory epithelial gene expression in patients with mild and severe cystic fibrosis lung disease

Jerry M. Wright et al.

AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY (2006)

Article Biochemistry & Molecular Biology

Rapid, specific, and sensitive measurements of plasma sphingomyelin and phosphatidylcholine

MR Hojjati et al.

JOURNAL OF LIPID RESEARCH (2006)

Article Biochemical Research Methods

De novo biosynthetic profiling of high abundance proteins in cystic fibrosis lung epithelial cells

Harvey B. Pollard et al.

MOLECULAR & CELLULAR PROTEOMICS (2006)

Review Biochemistry & Molecular Biology

When do lasses (longevity assurance genes) become CerS (ceramide synthases)? Insights into the regulation of ceramide synthesis

Yael Pewzner-Jung et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2006)

Article Physiology

CFTR ΔF508 mutation has minimal effect on the gene expression profile of differentiated human airway epithelia

J Zabner et al.

AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2005)

Article Cell Biology

Characterization of serine palmitoyltransferase in normal human tissues

AD Batheja et al.

JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY (2003)