Launois-Bensaude syndrome involving the orbits

Background: We report the first description of a Launois-Bensaude syndrome involving the orbit. Case report: Launois-Bensaude syndrome was diagnosed in a 70-year-old-man who presented with severe bilateral proptosis (Hertel value 26 mm). We performed a bilateral transpalpebral orbital decompression by resection of intraorbital fat without bone removal. The surgery was uneventful. The volume of resected orbital fat was 16 cc in both sides. Proptosis reduction was 7 mm. Postoperative Hertel values were 19 mm in both eyes. Conclusion: The proptosis was managed successfully. Orbital lipectomy lead to minimal sequelae and, may be repeated if necessary in this case. (C) 2010 European Association for Cranio-Maxillo-Facial Surgery.