Related references
Note: Only part of the references are listed.Understanding the molecular mechanisms of Friedreich's ataxia to develop therapeutic approaches
Stephane Schmucker et al.
HUMAN MOLECULAR GENETICS (2010)
The cell biology of tetrapyrroles: a life and death struggle
Nobuyoshi Mochizuki et al.
TRENDS IN PLANT SCIENCE (2010)
Nitric oxide accumulation is required to protect against iron-mediated oxidative stress in frataxin-deficient Arabidopsis plants
Mariana Martin et al.
FEBS LETTERS (2009)
Multicellular models of Friedreich ataxia
Helene Puccio
JOURNAL OF NEUROLOGY (2009)
GUN4 Is Required for Posttranslational Control of Plant Tetrapyrrole Biosynthesis
Enrico Peter et al.
MOLECULAR PLANT (2009)
Function and biogenesis of iron-sulphur proteins
Roland Lill
NATURE (2009)
Fingerprinting antioxidative activities in plants
Livia Saleh et al.
PLANT METHODS (2009)
Maturation of iron-sulfur proteins in eukaryotes: Mechanisms, connected processes, and diseases
Roland Lill et al.
ANNUAL REVIEW OF BIOCHEMISTRY (2008)
Hemin rescues adrenodoxin, heme a and cytochrome oxidase activity in frataxin-deficient oligodendroglioma cells
Eleonora Napoli et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE (2007)
Induction of isoforms of tetrapyrrole biosynthetic enzymes, AtHEMA2 and AtFC1, under stress conditions and their physiological functions in arabidopsis
Satoshi Nagai et al.
PLANT PHYSIOLOGY (2007)
Knockout of frataxin gene causes embryo lethality in Arabidopsis
Valentina Vazzola et al.
FEBS LETTERS (2007)
Expression and one-step purification of recombinant Arabidopsis thaliana frataxin homolog (AtFH)
Maria V. Maliandi et al.
PROTEIN EXPRESSION AND PURIFICATION (2007)
Deficiency of Arabidopsis thaliana frataxin alters activity of mitochondrial Fe-S proteins and induces oxidative stress
Maria V. Busi et al.
PLANT JOURNAL (2006)
Mrs3p, Mrs4p, and frataxin provide iron for Fe-S cluster synthesis in mitochondria
Yan Zhang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2006)
Characterization of an Arabidopsis thaliana mutant lacking a cytosolic non-phosphorylating glyceraldehyde-3-phosphate dehydrogenase
Sebastian P. Rius et al.
PLANT MOLECULAR BIOLOGY (2006)
Mitochondrial reactive oxygen species. Contribution to oxidative stress and interorganellar signaling
David M. Rhoads et al.
PLANT PHYSIOLOGY (2006)
Frataxin deficiency alters heme pathway transcripts and decreases mitochondrial heme metabolites in mammalian cells
RA Schoenfeld et al.
HUMAN MOLECULAR GENETICS (2005)
Subcellular localization and light-regulated expression of protoporphyrinogen IX oxidase and ferrochelatase in Chlamydomonas reinhardtii
R van Lis et al.
PLANT PHYSIOLOGY (2005)
Recombinant human erythropoietin:: effects on frataxin expression in vitro
B Sturm et al.
EUROPEAN JOURNAL OF CLINICAL INVESTIGATION (2005)
Biogenesis of iron-sulfur proteins in plants
J Balk et al.
TRENDS IN PLANT SCIENCE (2005)
Frataxin and mitochondrial carrier proteins, Mrs3p and Mrs4p, cooperate in providing iron for heme synthesis
Y Zhang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Yeast frataxin solution structure, iron binding, and ferrochelatase interaction
YN He et al.
BIOCHEMISTRY (2004)
The heme synthesis defect of mutants impaired in mitochondrial iron-sulfur protein biogenesis is caused by reversible inhibition of ferrochelatase
H Lange et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Frataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesis
T Yoon et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2004)
Functional and molecular characterization of the frataxin homolog from Arabidopsis thaliana
MV Busi et al.
FEBS LETTERS (2004)
An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1
J Gerber et al.
EMBO REPORTS (2003)
Yeast frataxin sequentially chaperones and stores iron by coupling protein assembly with iron oxidation
S Park et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Subcellular localization of two types of ferrochelatase in cucumber
T Masuda et al.
PLANTA (2003)
Iron use for haeme synthesis is under control of the yeast frataxin homologue (Yfh1)
E Lesuisse et al.
HUMAN MOLECULAR GENETICS (2003)
Double antisense plants lacking ascorbate peroxidase and catalase are less sensitive to oxidative stress than single antisense plants lacking ascorbate peroxidase or catalase
L Rizhsky et al.
PLANT JOURNAL (2002)
Frataxin deficiency and mitochondrial dysfunction
M Pandolfo
MITOCHONDRION (2002)
Inhibition of Fe-S cluster biosynthesis decreases mitochondrial iron export: Evidence that Yfh1p affects Fe-S cluster synthesis
OS Chen et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)
Erythroid differentiation and protoporphyrin IX down-regulate frataxin expression in Friend cells: characterization of frataxin expression compared to molecules involved in iron metabolism and hemoglobinization
EM Becker et al.
BLOOD (2002)
Proteomic approach to identify novel mitochondrial proteins in Arabidopsis
V Kruft et al.
PLANT PHYSIOLOGY (2001)
Arabidopsis thaliana ferrochelatase-I and -II are not imported into Arabidopsis mitochondria
R Lister et al.
FEBS LETTERS (2001)
The phylogenetic distribution of frataxin indicates a role in iron-sulfur cluster protein assembly
MA Huynen et al.
HUMAN MOLECULAR GENETICS (2001)
Regulatory network of tetrapyrrole biosynthesis - studies of intracellular signalling involved in metabolic and developmental control of plastids
J Papenbrock et al.
PLANTA (2001)
Purification and characterization of the preprotein translocase of the outer mitochondrial membrane from Arabidopsis.: Identification of multiple forms of TOM20
W Werhahn et al.
PLANT PHYSIOLOGY (2001)
Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits
H Puccio et al.
NATURE GENETICS (2001)
Frataxin activates mitochondrial energy conversion and oxidative phosphorylation
M Ristow et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2000)
Maturation of cellular Fe-S proteins: an essential function of mitochondria
R Lill et al.
TRENDS IN BIOCHEMICAL SCIENCES (2000)