Related references
Note: Only part of the references are listed.The distal carboxyl-terminal domains of ADAMTS13 are required for regulation of in vivo thrombus formation
Fumiaki Banno et al.
BLOOD (2009)
Essential role of the disintegrin-like domain in ADAMTS13 function
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BLOOD (2009)
A novel binding site for ADAMTS13 constitutively exposed on the surface of globular VWF
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Storage and regulated secretion of factor VIII in blood outgrowth endothelial cells
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VH1-69 germline encoded antibodies directed towards ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura
W. Pos et al.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS (2009)
Multi-step binding of ADAMTS-13 to von Willebrand factor
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Structural specializations of A2, a force-sensing domain in the ultralarge vascular protein von Willebrand factor
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Crystal structures of the noncatalytic domains of ADAMTS13 reveal multiple discontinuous exosites for von Willebrand factor
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Mechanoenzymatic Cleavage of the Ultralarge Vascular Protein von Willebrand Factor
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SCIENCE (2009)
Pathogenesis of thrombotic microangiopathies
X. Long Zheng et al.
ANNUAL REVIEW OF PATHOLOGY-MECHANISMS OF DISEASE (2008)
Extensive contacts between ADAMTS13 exosites and von Willebrand factor domain A2 contribute to substrate specificity
Weiqiang Gao et al.
BLOOD (2008)
N-linked glycosylation of VWF modulates its interaction with ADAMTS13
Thomas A. J. McKinnon et al.
BLOOD (2008)
Von Willebrand factor, ADAMTS13, and thrombotic thrombocytopenic purpura
J. Evan Sadler
BLOOD (2008)
ADAMTS13 and anti-ADAMTS13 antibodies as markers for recurrence of acquired thrombotic thrombocytopenic purpura during remission
Flora Peyvandi et al.
HAEMATOLOGICA (2008)
Assembly of Weibel-Palade body-like tubules from N-terminal domains of von Willebrand factor
Ren-Huai Huang et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)
Requirements for cellular co-trafficking of factor VIII and von Willebrand factor to Weibel-Palade bodies
M. Van den Biggelaar et al.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS (2007)
The cooperative activity between the carboxyl-terminal TSP1 repeats and the CUB domains of ADAMTS13 is crucial for recognition of von Willebrand factor under flow
Ping Zhang et al.
BLOOD (2007)
Prognostic value of anti-ADAMTS13 antibody features (Ig isotype, titer, and inhibitory effect) in a cohort of 35 adult French patients undergoing a first episode of thrombotic microangiopathy with undetectable ADAMTS13 activity
Silvia Ferrari et al.
BLOOD (2007)
ADAMTS13 and von Willebrand factor and the risk of myocardial infarction in men
Chan K. N. K. Chion et al.
BLOOD (2007)
Exosite interactions contribute to tension-induced cleavage of von Willebrand factor by the antithrombotic ADAMTS13 metalloprotease
Weiqiang Gao et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)
Characterization of a core binding site for ADAMTS-13 in the A2 domain of von Willebrand factor
Jing-Jiang Wu et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)
Multiple B-cell clones producing antibodies directed to the spacer and disintegrin/thrombospondin type-1 repeat 1 (TSP1) of ADAMTS13 in a patient with acquired thrombotic thrombocytopenic purpura
B. M. Luken et al.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS (2006)
Inhibitory autoantibodies against ADAMTS-13 in patients with thrombotic thrombocytopenic purpura bind ADAMTS-13 protease and may accelerate its clearance in vivo
S. G. Shelat et al.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS (2006)
The physiological function of von Willebrand's factor depends on its tubular storage in endothelial Weibel-Palade bodies
G Michaux et al.
DEVELOPMENTAL CELL (2006)
ADAMTS13 substrate recognition of von Willebrand factor A2 domain
S Zanardelli et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2006)
Enzymatically active ADAMTS13 variants are not inhibited by anti-ADAMTS13 autoantibodies - A novel therapeutic strategy?
WH Zhou et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice
DG Motto et al.
JOURNAL OF CLINICAL INVESTIGATION (2005)
The proximal carboxyl-terminal domains of ADAMTS13 determine substrate specificity and are all required for cleavage of von Willebrand factor
JH Ai et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Cleavage of ultralarge multimers of von Willebrand factor by C-terminal-truncated mutants of ADAMTS-13 under flow
ZY Tao et al.
BLOOD (2005)
FRETS-VWF73, a first fluorogenic substrate for ADAMTS13 assay
K Kokame et al.
BRITISH JOURNAL OF HAEMATOLOGY (2005)
Proteolytic inactivation of ADAMTS13 by thrombin and plasmin
JTB Crawley et al.
BLOOD (2005)
Epitope mapping of ADAMTS 13 autoantibodies in acquired thrombotic thrombocytopenic purpura
C Klaus et al.
BLOOD (2004)
Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity, inhibitor level, and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura
XL Zheng et al.
BLOOD (2004)
von Willebrand factor cleaving protease (ADAMTS-13) and ADAMTS-13 neutralizing autoantibodies in 100 patients with thrombotic thrombocytopenic purpura
F Peyvandi et al.
BRITISH JOURNAL OF HAEMATOLOGY (2004)
ADAMTS-13 metalloprotease interacts with the endothelial cell-derived ultra-large von Willebrand factor
JF Dong et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Cleavage of von Willebrand factor requires the spacer domain of the metalloprotease ADAMTS13
XL Zheng et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Von Willebrand factor cleaving protease and ADAMTS13 mutations in childhood TTP
R Schneppenheim et al.
BLOOD (2003)
ADAMTS-13 cysteine-rich/spacer domains are functionally essential for von Willebrand factor cleavage
K Soejima et al.
BLOOD (2003)
ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions
JF Dong et al.
BLOOD (2002)
Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura
XL Zheng et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura
GG Levy et al.
NATURE (2001)
A novel human metalloprotease synthesized in the liver and secreted into the blood: Possibly, the von Willebrand factor-cleaving protease?
K Soejima et al.
JOURNAL OF BIOCHEMISTRY (2001)