Related references
Note: Only part of the references are listed.A Novel, Drug-based, Cellular Assay for the Activity of Neurotoxic Mutants of the Prion Protein
Tania Massignan et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2010)
Mutant Prion Protein Expression Is Associated with an Alteration of the Rab GDP Dissociation Inhibitor α (GDI)/Rab11 Pathway
Tania Massignan et al.
MOLECULAR & CELLULAR PROTEOMICS (2010)
Variety of Antiprion Compounds Discovered through an In Silico Screen Based on Cellular-Form Prion Protein Structure: Correlation between Antiprion Activity and Binding Affinity
Junji Hosokawa-Muto et al.
ANTIMICROBIAL AGENTS AND CHEMOTHERAPY (2009)
Spontaneous Generation of Prion Infectivity in Fatal Familial Insomnia Knockin Mice
Walker S. Jackson et al.
NEURON (2009)
Fishing for Prion Protein Function
Roberto Chiesa et al.
PLOS BIOLOGY (2009)
Identification of an Intracellular Site of Prion Conversion
Zrinka Marijanovic et al.
PLOS PATHOGENS (2009)
Selective Processing and Metabolism of Disease-Causing Mutant Prion Proteins
Aarthi Ashok et al.
PLOS PATHOGENS (2009)
The deletion of amino acids 114-121 in the TM1 domain of mouse prion protein stabilizes its conformation but does not affect the overall structure
Bastian Thaa et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH (2008)
Multiple biochemical similarities between infectious and non-infectious aggregates of a prion protein carrying an octapeptide insertion
Emiliano Biasini et al.
JOURNAL OF NEUROCHEMISTRY (2008)
Non-infectious aggregates of the prion protein react with several PrPSc-directed antibodies
E. Biasini et al.
JOURNAL OF NEUROCHEMISTRY (2008)
Mutant Prion Protein Expression Causes Motor and Memory Deficits and Abnormal Sleep Patterns in a Transgenic Mouse Model
Sara Dossena et al.
NEURON (2008)
Lethal recessive myelin toxicity of prion protein lacking its central domain
Frank Baumann et al.
EMBO JOURNAL (2007)
Mutant prion protein D202N associated with familial prion disease is retained in the endoplasmic reticulum and forms 'Curly' intracellular aggregates
Yaping Gu et al.
JOURNAL OF MOLECULAR NEUROSCIENCE (2007)
Stressing out the EIR: A role of the unfolded protein response in prion-related disorders
CA Hetz et al.
CURRENT MOLECULAR MEDICINE (2006)
The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation
EM Norstrom et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice
KE Nazor et al.
EMBO JOURNAL (2005)
In vitro generation of infectious scrapie prions
J Castilla et al.
CELL (2005)
Cytosolic prion protein (PrP) is not toxic in N2a cells and primary neurons expressing pathogenic PrP mutations
L Fioriti et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Doxycycline and protein folding agents rescue the abnormal phenotype of familial CJD H187R in a cell model
YP Gu et al.
MOLECULAR BRAIN RESEARCH (2004)
Mutant PrPSc conformers induced by a synthetic peptide and several prion strains
P Tremblay et al.
JOURNAL OF VIROLOGY (2004)
NMR structure of the bovine prion protein isolated from healthy calf brains
S Hornemann et al.
EMBO REPORTS (2004)
Preventing misfolding of the prion protein by trimethylamine N-oxide
BJ Bennion et al.
BIOCHEMISTRY (2004)
Structural properties of Gerstmann-Straussler-Scheinker disease amyloid protein
M Salmona et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Molecular distinction between pathogenic and infectious properties of the prion protein
R Chiesa et al.
JOURNAL OF VIROLOGY (2003)
Mutant PrP is delayed in its exit from the endoplasmic reticulum, but neither wild-type nor mutant PrP undergoes retrotranslocation prior to proteasomal degradation
B Drisaldi et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Mutant prion protein-mediated aggregation of normal prion protein in the endoplasmic reticulum: implications for prion propagation and neurotoxicity
YP Gu et al.
JOURNAL OF NEUROCHEMISTRY (2003)
Cellular phenotyping of secretory and nuclear prion proteins associated with inherited prion diseases
H Lorenz et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Mutant prion proteins axe partially retained in the endoplasmic reticulum
L Ivanova et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2001)
Prion diseases: What is the neurotoxic molecule?
R Chiesa et al.
NEUROBIOLOGY OF DISEASE (2001)
The metabolism and imaging in live cells of the bovine prion protein in its native form or carrying single amino acid substitutions
A Negro et al.
MOLECULAR AND CELLULAR NEUROSCIENCE (2001)
Nerve growth factor-induced differentiation does not alter the biochemical properties of a mutant prion protein expressed in PC12 cells
R Chiesa et al.
JOURNAL OF NEUROCHEMISTRY (2000)
Cultured cell sublines highly susceptible to prion infection
PJ Bosque et al.
JOURNAL OF VIROLOGY (2000)
NMR solution structure of the human prion protein
R Zahn et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2000)
Share Paper
