Related references
Note: Only part of the references are listed.Calcium homeostasis is abnormal in cystic fibrosis airway epithelial cells but is normalized after rescue of F508del-CFTR
Fabrice Antigny et al.
CELL CALCIUM (2008)
Parallel improvement of sodium and chloride transport defects by miglustat (n-butyldeoxynojyrimicin) in cystic fibrosis epithelial cells
Sabrina Noel et al.
JOURNAL OF PHARMACOLOGY AND EXPERIMENTAL THERAPEUTICS (2008)
Cystic fibrosis: a disease of vulnerability to airway surface dehydration
Richard C. Boucher
TRENDS IN MOLECULAR MEDICINE (2007)
Modulating the folding of P-glycoprotein and cystic fibrosis transmembrane conductance regulator truncation mutants with pharmacological chaperones
Ying Wang et al.
MOLECULAR PHARMACOLOGY (2007)
The pharmacokinetics and tissue distribution of the glucosylceramide synthase inhibitor miglustat in the rat
A. Treiber et al.
XENOBIOTICA (2007)
Rescue of ΔF508-CFTR trafficking and gating in human cystic fibrosis airway primary cultures by small molecules
F Van Goor et al.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY (2006)
Maintaining low Ca2+ level in the endoplasmic reticulum restores abnormal endogenous F508del-CFTR trafficking in airway epithelial cells
C Norez et al.
TRAFFIC (2006)
Rescue of ΔF508-CFTR (cystic fibrosis transmembrane conductance regulator) by curcumin:: Involvement of the keratin 18 network
J Lipecka et al.
JOURNAL OF PHARMACOLOGY AND EXPERIMENTAL THERAPEUTICS (2006)
Rescue of functional delF508-CFTR channels in cystic fibrosis epithelial cells by the α-glucosidase inhibitor miglustat
C Norez et al.
FEBS LETTERS (2006)
Small-molecule correctors of defective ΔF508-CFTR cellular processing identified by high-throughput screening
N Pedemonte et al.
JOURNAL OF CLINICAL INVESTIGATION (2005)
Correction of the CF defect by curcumin: hypes and disappointments
M Mall et al.
BIOESSAYS (2005)
Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects
ME Egan et al.
SCIENCE (2004)
Thapsigargin selectively rescues the trafficking defective LQT2 channels G601S and F805C
BP Delisle et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Calcium-pump inhibitors induce functional surface expression of ΔF508-CFTR protein in cystic fibrosis epithelial cells
ME Egan et al.
NATURE MEDICINE (2002)
Pharmacotherapy of the ion transport defect in cystic fibrosis
K Kunzelmann et al.
CLINICAL AND EXPERIMENTAL PHARMACOLOGY AND PHYSIOLOGY (2001)
Future pharmacological treatment of cystic fibrosis
PL Zeitlin
RESPIRATION (2000)