Journal
JOURNAL OF ARRHYTHMIA
Volume 32, Issue 1, Pages 70-73Publisher
ELSEVIER SCIENCE BV
DOI: 10.1016/j.joa.2015.10.007
Keywords
Brugada syndrome; Arrhythmogenic right ventricular cardiomyopathy/dysplasia; An overlap disease
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Funding
- Grants-in-Aid for Scientific Research [15K21388] Funding Source: KAKEN
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Overlapping characteristics of Brugada syndrome (BrS) and arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) have been reported in recent studies, but little is known about the overlapping disease state of BrS and ARVC/D. A 36-year-old man, hospitalized at our institution for syncope, presented with this overlapping disease state. The electrocardiogram showed spontaneous coved-type ST-segment elevation, and ventricular fibrillation was induced by right ventricular outflow tract stimulation in an electrophysiological study. BrS was subsequently diagnosed; additionally, the presence of epsilon-like waves and right ventricular structural abnormalities met with the 2010 revised task force criteria for ARVC/D. After careful investigation for both BrS and ARVC/D, an implantable cardioverter defibrillator was inserted in the patient. This case revealed 2 important clinical findings: (1) BrS and ARVC/D clinical features can coexist in a single patient, and EPS might be useful for determining the phenotype of overlapping disease (e.g., BrS-like or ARVC/D-like). (2) An overlapping disease state of BrS and ARVC/D can change phenotypically during its clinical course. Therefore, careful examination and attentive follow-up are required for patients with BrS or ARVC/D. (C) 2015 Japanese Heart Rhythm Society. Published by Elsevier B.V.
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