Stellate nonheritable idiopathic foveomacular retinoschisis in juveniles: case report

BackgroundStellate nonhereditary idiopathic foveomacular retinoschisis (SNIFR) is a rare type of retinoschisis with a spoke-like splitting that occurs in the outer plexus layer. We present a case of stellate nonhereditary idiopathic foveomacular retinoschisis in a juvenile, in which two eyes show different development trends and macular retinoschisis could be associated with mechanical force in the Henle fibre layer. The removal of mechanical force can partially restore vision.Case presentationA 14-year-old girl with bilateral SNIFR was diagnosed and followed up with spectral-domain optical coherence tomography (SD-OCT). During the two follow-up visits, vitreous adhesion was released in the left eye, and visual acuity improved. Neuroepithelial detachment was aggravated in the right eye, and visual acuity decreased. Therefore, vitrectomy was performed on the right eye. After surgery, the patient's retina was reattached, and her vision was partially restored.ConclusionsWe reported a juvenile with bilateral SNIFR. Each of her eyes showed different development trends, so we adopted different treatment methods for each eye. Vitrectomy was performed on the patient to address progressive vision loss, which improved the patient's vision. It was further confirmed that the Henle layer of SNIFR patients was susceptible to posterior vitreous membrane adhesion.

Automated summary

We present a case of stellate nonhereditary idiopathic foveomacular retinoschisis (SNIFR) in a juvenile, in which each eye showed different development trends. Vitrectomy was performed on the patient to address progressive vision loss and the retina was successfully reattached, partially restoring vision. It was confirmed that the Henle layer of SNIFR patients is susceptible to posterior vitreous membrane adhesion.