Related references
Note: Only part of the references are listed.Gene Therapy Restores Auditory Functions in an Adult Vglut3 Knockout Mouse Model
Xingle Zhao et al.
HUMAN GENE THERAPY (2022)
Unbalanced bidirectional radial stiffness gradients within the organ of Corti promoted by TRIOBP
Hesam Babahosseini et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2022)
AAV8BP2 and AAV8 transduce the mammalian cochlear lateral wall and endolymphatic sac with high efficiency
Kevin Isgrig et al.
MOLECULAR THERAPY-METHODS & CLINICAL DEVELOPMENT (2022)
AAV-S: A versatile capsid variant for transduction of mouse and primate inner ear
Maryna Ivanchenko et al.
MOLECULAR THERAPY-METHODS & CLINICAL DEVELOPMENT (2021)
Adeno-associated virus gene replacement for recessive inner ear dysfunction: Progress and challenges
Charles Askew et al.
HEARING RESEARCH (2020)
AAV2.7m8 is a powerful viral vector for inner ear gene therapy
Kevin Isgrig et al.
NATURE COMMUNICATIONS (2019)
Cochlear outer hair cell horizontal top connectors mediate mature stereocilia bundle mechanics
Alexander X. Cartagena-Rivera et al.
SCIENCE ADVANCES (2019)
Gene Transfer with AAV9-PHP.B Rescues Hearing in a Mouse Model of Usher Syndrome 3A and Transduces Hair Cells in a Non-human Primate
Bence Gyorgy et al.
MOLECULAR THERAPY-METHODS & CLINICAL DEVELOPMENT (2019)
Detailed Clinical Features of Deafness Caused by a Claudin-14 Variant
Tomohiro Kitano et al.
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES (2019)
TRIOBP-5 sculpts stereocilia rootlets and stiffens supporting cells enabling hearing
Tatsuya Katsuno et al.
JCI INSIGHT (2019)
Anatomical basis of drug delivery to the inner ear
R. Glueckert et al.
HEARING RESEARCH (2018)
Why Do Hearing Aids Fail to Restore Normal Auditory Perception?
Nicholas A. Lesica
TRENDS IN NEUROSCIENCES (2018)
Genomic Landscape and Mutational Signatures of Deafness-Associated Genes
Hela Azaiez et al.
AMERICAN JOURNAL OF HUMAN GENETICS (2018)
Evaluation of Dose and Safety of AAV7m8 and AAV8BP2 in the Non-Human Primate Retina
Pavitra S. Ramachandran et al.
HUMAN GENE THERAPY (2017)
Emerging Gene Therapies for Genetic Hearing Loss
Hena Ahmed et al.
JARO-JOURNAL OF THE ASSOCIATION FOR RESEARCH IN OTOLARYNGOLOGY (2017)
What Does Music Sound Like for a Cochlear Implant User?
Nicole T. Jiam et al.
OTOLOGY & NEUROTOLOGY (2017)
Apical surface supracellular mechanical properties in polarized epithelium using noninvasive acoustic force spectroscopy
Alexander X. Cartagena-Rivera et al.
NATURE COMMUNICATIONS (2017)
Tight junctions: from simple barriers to multifunctional molecular gates
Ceniz Zihni et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2016)
Tricellular Tight Junctions in the Inner Ear
Shin-ichiro Kitajiri et al.
BIOMED RESEARCH INTERNATIONAL (2016)
ILDR1 deficiency causes degeneration of cochlear outer hair cells and disrupts the structure of the organ of Corti: a mouse model for human DFNB42
Qing Sang et al.
BIOLOGY OPEN (2015)
ILDR1 null mice, a model of human deafness DFNB42, show structural aberrations of tricellular tight junctions and degeneration of auditory hair cells
Eva L. Morozko et al.
HUMAN MOLECULAR GENETICS (2015)
Virally expressed connexin26 restores gap junction function in the cochlea of conditional Gjb2 knockout mice
Q. Yu et al.
GENE THERAPY (2014)
Analysis of the 'angulin' proteins LSR, ILDR1 and ILDR2 - tricellulin recruitment, epithelial barrier function and implication in deafness pathogenesis (vol 126, pg 966, 2013)
Tomohito Higashi et al.
JOURNAL OF CELL SCIENCE (2013)
Immunoglobulin-like domain containing receptor 1 mediates fat-stimulated cholecystokinin secretion
Rashmi Chandra et al.
JOURNAL OF CLINICAL INVESTIGATION (2013)
Tricellulin deficiency affects tight junction architecture and cochlear hair cells
Gowri Nayak et al.
JOURNAL OF CLINICAL INVESTIGATION (2013)
Cytoskeletal changes in actin and microtubules underlie the developing surface mechanical properties of sensory and supporting cells in the mouse cochlea
Katherine B. Szarama et al.
DEVELOPMENT (2012)
Restoration of Hearing in the VGLUT3 Knockout Mouse Using Virally Mediated Gene Therapy
Omar Akil et al.
NEURON (2012)
Loss-of-Function Mutations of ILDR1 Cause Autosomal-Recessive Hearing Impairment DFNB42
Guntram Borck et al.
AMERICAN JOURNAL OF HUMAN GENETICS (2011)
Noncontact microrheology at acoustic frequencies using frequency-modulated atomic force microscopy
Nuria Gavara et al.
NATURE METHODS (2010)
Hearing Impairment: A Panoply of Genes and Functions
Amiel A. Dror et al.
NEURON (2010)
Dynamics and functions of tight junctions
Emily Steed et al.
TRENDS IN CELL BIOLOGY (2010)
Tricellulin Forms a Barrier to Macromolecules in Tricellular Tight Junctions without Affecting Ion Permeability
Susanne M. Krug et al.
MOLECULAR BIOLOGY OF THE CELL (2009)
Reversal of blindness in animal models of Leber congenital amaurosis using optimized AAV2-mediated gene transfer
Jeannette Bennicelli et al.
MOLECULAR THERAPY (2008)
Tricellulin is a tight-junction protein necessary for hearing
Saima Riazuddin et al.
AMERICAN JOURNAL OF HUMAN GENETICS (2006)
Current concepts: Newborn hearing screening - A silent revolution
CC Morton et al.
NEW ENGLAND JOURNAL OF MEDICINE (2006)
Tricellulin constitutes a novel barrier at tricellular contacts of epithelial cells
J Ikenouchi et al.
JOURNAL OF CELL BIOLOGY (2005)
A mechanism for sensing noise damage in the inner ear
JE Gale et al.
CURRENT BIOLOGY (2004)
Characterization of a novel immunoglobulin-like domain containing receptor
H Hauge et al.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS (2004)
Claudin 14 knockout mice, a model for autosomal recessive deafness DFNB29, are deaf due to cochlear hair cell degeneration
T Ben-Yosef et al.
HUMAN MOLECULAR GENETICS (2003)