Related references
Note: Only part of the references are listed.Effects of elexacaf tor/tezacaf tor/ivacaf tor therapy in children with cystic fibrosis - a comprehensive assessment using lung clearance index, spirometry, and functional and structural lung MRI
Carmen Streibel et al.
JOURNAL OF CYSTIC FIBROSIS (2023)
Reply to migration is not the perfect answer: Optimized methodology to assess LCI agreement between corrected legacy multiple breath nitrogen washout data and that directly collected on updated software
Ediane De Queiroz Andrade et al.
PEDIATRIC PULMONOLOGY (2023)
The clinical impact of Lumacaftor-Ivacaftor on structural lung disease and lung function in children aged 6-11 with cystic fibrosis in a real-world setting
Paul McNally et al.
RESPIRATORY RESEARCH (2023)
Clinical Effectiveness of Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis
David P. Nichols et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2022)
Using chest computed tomography and unsupervised machine learning for predicting and evaluating response to lumacaftor-ivacaftor in people with cystic fibrosis
Alienor Campredon et al.
EUROPEAN RESPIRATORY JOURNAL (2022)
Effects of Elexacaftor/Tezacaftor/Ivacaftor Therapy on Lung Clearance Index and Magnetic Resonance Imaging in Patients with Cystic Fibrosis and One or Two F508del Alleles
Simon Y. Graeber et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2022)
Artificial intelligence in computed tomography for quantifying lung changes in the era of CFTR modulators
Gael Dournes et al.
EUROPEAN RESPIRATORY JOURNAL (2022)
Chest computed tomography improvement in patients with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: Early report
Romain Bec et al.
EUROPEAN JOURNAL OF RADIOLOGY (2022)
Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial
Matthias Griese et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2021)
Rapid Improvement after Starting Elexacaftor-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and Advanced Pulmonary Disease
Pierre-Regis Burgel et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2021)
A Phase 3 Open-Label Study of Elexacaftor/Tezacaftor/lvacaftor in Children 6 through 11 Years of Age with Cystic Fibrosis and at Least One F508del Allele
Edith T. Zemanick et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2021)
Computed Tomographic Changes in Patients with Cystic Fibrosis Treated by Combination Therapy with Lumacaftor and Ivacaftor
Francois Arnaud et al.
JOURNAL OF CLINICAL MEDICINE (2021)
Chest computed tomography outcomes in a randomized clinical trial in cystic fibrosis: Lessons learned from the first ataluren phase 3 study
Harm A. W. M. Tiddens et al.
PLOS ONE (2020)
Guidance for computed tomography (CT) imaging of the lungs for patients with cystic fibrosis (CF) in research studies
Marcel van Straten et al.
Journal of Cystic Fibrosis (2019)
Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial
Harry G. M. Heijerman et al.
LANCET (2019)
Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele
P. G. Middleton et al.
NEW ENGLAND JOURNAL OF MEDICINE (2019)
CORK Study in Cystic Fibrosis Sustained Improvements in Ultra-Low-Dose Chest CT Scores After CFTR Modulation With Ivacaftor
Nicola J. Ronan et al.
CHEST (2018)
Spirometer Guided Chest Imaging in Children: It Is Worth the Effort!
Elizabeth Salamon et al.
PEDIATRIC PULMONOLOGY (2017)
Correlation of sweat chloride and percent predicted FEV1 in cystic fibrosis patients treated with ivacaftor
Meredith C. Fidler et al.
JOURNAL OF CYSTIC FIBROSIS (2017)
Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del
Jennifer L. Taylor-Cousar et al.
NEW ENGLAND JOURNAL OF MEDICINE (2017)
Association between spirometry controlled chest CT scores using computer-animated biofeedback and clinical markers of lung disease in children with cystic fibrosis
Thomas Kongstad et al.
EUROPEAN CLINICAL RESPIRATORY JOURNAL (2017)
Long-term computed tomographic changes in cystic fibrosis patients treated with ivacaftor
Guillaume Chassagnon et al.
EUROPEAN RESPIRATORY JOURNAL (2016)
A Systematic Approach to Multiple Breath Nitrogen Washout Test Quality
Renee Jensen et al.
PLOS ONE (2016)
PRAGMA-CF A Quantitative Structural Lung Disease Computed Tomography Outcome in Young Children with Cystic Fibrosis
Tim Rosenow et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2015)
Computed tomography correlates with improvement with ivacaftor in cystic fibrosis patients with G551D mutation
Shahid I. Sheikh et al.
JOURNAL OF CYSTIC FIBROSIS (2015)
Association of sweat chloride concentration at time of diagnosis and CFTR genotype with mortality and cystic fibrosis phenotype
Edward F. McKone et al.
JOURNAL OF CYSTIC FIBROSIS (2015)
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
C. E. Wainwright et al.
NEW ENGLAND JOURNAL OF MEDICINE (2015)
Ivacaftor Imaging Response in Cystic Fibrosis
Siobhan Hoare et al.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE (2014)
Consensus statement for inert gas washout measurement using multiple- and single-breath tests
Paul D. Robinson et al.
EUROPEAN RESPIRATORY JOURNAL (2013)
Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation
Frank J. Accurso et al.
NEW ENGLAND JOURNAL OF MEDICINE (2010)
Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis
P. M. Gustafsson et al.
THORAX (2008)