Proximal-type epithelioid sarcoma of the perineum: A case report and literature review

Proximal-type epithelioid sarcoma of the perineum is a rare soft-tissue malignancy, and only 55 cases have been reported in the English literature to date. This tumor has an indetectable early symptom and frequent recurrences. Here, we present the case of a 31-year-old man with proximal-type epithelioid sarcoma of the perineum who underwent wide excision. Further, we reviewed the current literature regarding differential diagnosis and management of this disease.

Automated summary

This case report describes a rare case of proximal-type epithelioid sarcoma of the perineum in a 31-year-old male who underwent wide excision. The disease is characterized by an indetectable early symptom and frequent recurrences. A review of the current literature on the differential diagnosis and management of this disease is also presented.