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Alessandro Prigione et al.
STEM CELLS (2010)
The inheritance of pathogenic mitochondrial DNA mutations
L. M. Cree et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE (2009)
CPEO and KSS differ in the percentage and location of the mtDNA deletion
Ester Lopez-Gallardo et al.
MITOCHONDRION (2009)
The Relationship Between Pluripotency and Mitochondrial DNA Proliferation During Early Embryo Development and Embryonic Stem Cell Differentiation
J. M. Facucho-Oliveira et al.
STEM CELL REVIEWS AND REPORTS (2009)
A mitochondrial protein compendium elucidates complex I disease biology
David J. Pagliarini et al.
CELL (2008)
Development of a single-chain, quasi-dimeric zinc-finger nuclease for the selective degradation of mutated human mitochondrial DNA
Michal Minczuk et al.
NUCLEIC ACIDS RESEARCH (2008)
Strong purifying selection in transmission of mammalian mitochondrial DNA
James Bruce Stewart et al.
PLOS BIOLOGY (2008)
Induction of pluripotent stem cells from adult human fibroblasts by defined factors
Kazutoshi Takahashi et al.
CELL (2007)
Induction of pluripotent stem cells from mouse embryonic and adult fibroblast cultures by defined factors
Kazutoshi Takahashi et al.
CELL (2006)
Generation of trans-mitochondrial mice carrying homoplasmic mtDNAs with a missense mutation in a structural gene using ES cells
A Kasahara et al.
HUMAN MOLECULAR GENETICS (2006)
Mutant mitochondrial helicase Twinkle causes multiple mtDNA deletions and a late-onset mitochondrial disease in mice
H Tyynismaa et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2005)
Genomic alterations in cultured human embryonic stem cells
A Maitra et al.
NATURE GENETICS (2005)
Mitochondrial DNA mutations, oxidative stress, and apoptosis in mammalian aging
GC Kujoth et al.
SCIENCE (2005)
Risk of developing a mitochondrial DNA deletion disorder
PF Chinnery et al.
LANCET (2004)
Premature ageing in mice expressing defective mitochondrial DNA polymerase
A Trifunovic et al.
NATURE (2004)
Replication of mitochondrial DNA occurs throughout the mitochondria of cultured human cells
J Magnusson et al.
EXPERIMENTAL CELL RESEARCH (2003)
A novel mitochondrial DNA tRNAIle (A4267G) mutation in a sporadic. patient with mitochondrial myopathy
RW Taylor et al.
NEUROMUSCULAR DISORDERS (2002)
Leber hereditary optic neuropathy
PYW Man et al.
JOURNAL OF MEDICAL GENETICS (2002)
Gene therapy for mitochondrial disease by delivering restriction endonuclease Smal into mitochondria
M Tanaka et al.
JOURNAL OF BIOMEDICAL SCIENCE (2002)
Manipulating mitochondrial DNA heteroplasmy by a mitochondrially targeted restriction endonuclease
S Srivastava et al.
HUMAN MOLECULAR GENETICS (2001)
Inter-mitochondrial complementation: Mitochondria-specific system preventing mice from expression of disease phenotypes by mutant mtDNA
K Nakada et al.
NATURE MEDICINE (2001)
Generation of mice with mitochondrial dysfunction by introducing mouse mtDNA carrying a deletion into zygotes
K Inoue et al.
NATURE GENETICS (2000)