Review of diagnosis, differential diagnosis, and management of retroperitoneal lymphangioma

Lymphatic malformation (LM) is the currently preferred term for what was previously known as lymphangioma. Retroperitoneal LMs are extremely rare, benign, cystic masses that arise from lymphatic vessels. They can be challenging to diagnose because they resemble other retroperitoneal cystic tumors. The development of treatment strategies for rare diseases, including retroperitoneal LM, requires the acquisition of new knowledge to enhance our understanding of the disease progression. Therefore, we present an update regarding fundamental and advanced issues associated with retroperitoneal LM. This review describes the epidemiology, histopathology, biomedicine, clinical manifestations, radiological features, differential diagnosis, and management of this lesion.

Automated summary

Lymphatic malformation (LM), previously known as lymphangioma, is a rare, benign, cystic mass that arises from lymphatic vessels. Diagnosing retroperitoneal LMs can be challenging due to their resemblance to other retroperitoneal cystic tumors. This review provides an update on the fundamental and advanced issues associated with retroperitoneal LM, including epidemiology, histopathology, biomedicine, clinical manifestations, radiological features, differential diagnosis, and management.