Journal
BRITISH JOURNAL OF HAEMATOLOGY
Volume 199, Issue 2, Pages 171-172Publisher
WILEY
DOI: 10.1111/bjh.18393
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This report provides guidance and management of deferiprone in transfusion-dependent DBA patients, but deferiprone may lead to agranulocytosis in DBA patients.
Transfusion-dependent Diamond-Blackfan anaemia (DBA) patients rapidly develop iron overload and frequently experience cardiac complications. The report by Lecornec and colleagues offers useful details on indications and the management of deferiprone, a highly efficient chelator in removing excess cardiac iron but associated with a high risk of agranulocytosis in DBA patients. Commentary on: Nicolas Lecornec and colleagues: Agranulocytosis in patients with Diamond-Blackfan anaemia treated with deferiprone for post-transfusion iron overload: A retrospective study of the French DBA cohort. British Journal of Haematology 2022.
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