Journal
INTERACTIVE CARDIOVASCULAR AND THORACIC SURGERY
Volume 34, Issue 6, Pages 1174-1176Publisher
OXFORD UNIV PRESS
DOI: 10.1093/icvts/ivab367
Keywords
Loeys-Dietz syndrome; Valve-sparing aortic root replacement; Aortic valve repair
Ask authors/readers for more resources
A case of a 2-year-old girl with Loeys-Dietz syndrome complicated by aortic root dilatation and aortic regurgitation is reported. Valve-sparing aortic root replacement with reimplantation technique and aortic valve repair were performed to treat the patient. The latest echocardiography after 5 years showed a stable condition with trivial aortic insufficiency.
We report the case of a 2-year-old girl with Loeys-Dietz syndrome complicated by aortic root dilatation and aortic regurgitation. We performed valve-sparing aortic root replacement with reimplantation technique and aortic valve repair using central plication and free-margin reinforcement simultaneously. The postoperative course was uneventful and the latest echocardiography, 5 years after procedure, revealed trivial aortic insufficiency. Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder characterized by arterial tortuosity and aneurysm, hypertelorism and bifid uvula or cleft palate.
Authors
I am an author on this paper
Click your name to claim this paper and add it to your profile.
Reviews
Recommended
No Data Available