Related references
Note: Only part of the references are listed.Pax7, Pax3 and Mamstr genes are involved in skeletal muscle impaired regeneration of dy2J/dy2J mouse model of Lama2-CMD
Nurit Yanay et al.
HUMAN MOLECULAR GENETICS (2019)
Laminin-deficient muscular dystrophy: Molecular pathogenesis and structural repair strategies
Peter D. Yurchenco et al.
MATRIX BIOLOGY (2018)
ELECTRICAL IMPEDANCE MYOGRAPHY IN INDIVIDUALS WITH COLLAGEN 6 AND LAMININ α-2 CONGENITAL MUSCULAR DYSTROPHY: A CROSS-SECTIONAL AND 2-YEAR ANALYSIS
Carmel Nichols et al.
MUSCLE & NERVE (2018)
At the Crossroads of Clinical and Preclinical Research for Muscular DystrophyAre We Closer to Effective Treatment for Patients?
Kinga I. Gawlik
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES (2018)
Natural disease history of the dy2J mouse model of laminin α2 (merosin)-deficient congenital muscular dystrophy
S. Pasteuning-Vuhman et al.
PLOS ONE (2018)
Effects of metformin on congenital muscular dystrophy type 1A disease progression in mice: a gender impact study
Cibely C. Fontes-Oliveira et al.
SCIENTIFIC REPORTS (2018)
Impaired fetal muscle development and JAK-STAT activation mark disease onset and progression in a mouse model for merosin-deficient congenital muscular dystrophy
Andreia M. Nunes et al.
HUMAN MOLECULAR GENETICS (2017)
The Role of Muscle Imaging in the Diagnosis and Assessment of Children with Genetic Muscle Disease
Jodi Warman Chardon et al.
NEUROPEDIATRICS (2017)
Potent pro-inflammatory and pro-fibrotic molecules, osteopontin and galectin-3, are not major disease modulators of laminin α2 chain-deficient muscular dystrophy
Kinga I. Gawlik et al.
SCIENTIFIC REPORTS (2017)
Bioenergetic Impairment in Congenital Muscular Dystrophy Type 1A and Leigh Syndrome Muscle Cells
Cibely C. Fontes-Oliveira et al.
SCIENTIFIC REPORTS (2017)
Muscle MRI findings in a one-year-old girl with merosin-deficient congenital muscular dystrophy type 1A due to LAMA2 mutation: A case report
Yingyin Liang et al.
BIOMEDICAL REPORTS (2017)
Regulation of muscle growth and regeneration by the immune system
James G. Tidball
NATURE REVIEWS IMMUNOLOGY (2017)
IGF-1/GH axis enhances losartan treatment in Lama2-related muscular dystrophy
Anthony Accorsi et al.
HUMAN MOLECULAR GENETICS (2016)
Autonomous Extracellular Matrix Remodeling Controls a Progressive Adaptation in Muscle Stem Cell Regenerative Capacity during Development
Matthew Timothy Tierney et al.
CELL REPORTS (2016)
A Battery of Motor Tests in a Neonatal Mouse Model of Cerebral Palsy
Danielle N. Feather-Schussler et al.
JOVE-JOURNAL OF VISUALIZED EXPERIMENTS (2016)
Life or death by NFκB, Losartan promotes survival in dy2J/dy2J mouse of MDC1A
M. Elbaz et al.
CELL DEATH & DISEASE (2015)
Magnetic Resonance Imaging Is Sensitive to Pathological Amelioration in a Model for Laminin-Deficient Congenital Muscular Dystrophy (MDC1A)
Ravneet Vohra et al.
PLOS ONE (2015)
Bortezomib Partially Improves Laminin α2 Chain-Deficient Muscular Dystrophy
Zandra Korner et al.
AMERICAN JOURNAL OF PATHOLOGY (2014)
Loss of Dystrophin and β-Sarcoglycan Significantly Exacerbates the Phenotype of Laminin α2 Chain-Deficient Animals
Kinga I. Gawlik et al.
AMERICAN JOURNAL OF PATHOLOGY (2014)
The Extracellular Matrix Protein Laminin α2 Regulates the Maturation and Function of the Blood-Brain Barrier
Michael J. Menezes et al.
JOURNAL OF NEUROSCIENCE (2014)
Quantitative Proteomic Analysis Reveals Metabolic Alterations, Calcium Dysregulation, and Increased Expression of Extracellular Matrix Proteins in Laminin α2 Chain-deficient Muscle
Bruno Menezes de Oliveira et al.
MOLECULAR & CELLULAR PROTEOMICS (2014)
Diagnostic approach to the congenital muscular dystrophies
Carsten G. Boennemann et al.
NEUROMUSCULAR DISORDERS (2014)
Dysregulation of matricellular proteins is an early signature of pathology in laminin-deficient muscular dystrophy
Thomas Mehuron et al.
SKELETAL MUSCLE (2014)
Therapeutic potential of matrix metalloproteinases in Duchenne muscular dystrophy
Yuji Ogura et al.
FRONTIERS IN CELL AND DEVELOPMENTAL BIOLOGY (2014)
Reducing CTGF/CCN2 slows down mdx muscle dystrophy and improves cell therapy
Maria Gabriela Morales et al.
HUMAN MOLECULAR GENETICS (2013)
Macrophage Plasticity and the Role of Inflammation in Skeletal Muscle Repair
Yacine Kharraz et al.
MEDIATORS OF INFLAMMATION (2013)
Laminin-211 in skeletal muscle function
Johan Holmberg et al.
CELL ADHESION & MIGRATION (2013)
Laminin-111 Protein Therapy Reduces Muscle Pathology and Improves Viability of a Mouse Model of Merosin-Deficient Congenital Muscular Dystrophy
Jachinta E. Rooney et al.
AMERICAN JOURNAL OF PATHOLOGY (2012)
Losartan, a therapeutic candidate in congenital muscular dystrophy: Studies in the dy2J/dy2J Mouse
Moran Elbaz et al.
ANNALS OF NEUROLOGY (2012)
Monocyte-to-Macrophage Differentiation SYNTHESIS AND SECRETION OF A COMPLEX EXTRACELLULAR MATRIX
Mary Y. Chang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2012)
Angiotensin II type 1 receptor antagonists alleviate muscle pathology in the mouse model for laminin-alpha 2-deficient congenital muscular dystrophy (MDC1A)
Sarina Meinen et al.
SKELETAL MUSCLE (2012)
Proteasome inhibition improves the muscle of laminin α2 chain-deficient mice
Virginie Carmignac et al.
HUMAN MOLECULAR GENETICS (2011)
Muscle-specific expression of insulin-like growth factor 1 improves outcome in Lama2Dy-w mice, a model for congenital muscular dystrophy type 1A
Ajay Kumar et al.
HUMAN MOLECULAR GENETICS (2011)
Autophagy is increased in laminin α2 chain-deficient muscle and its inhibition improves muscle morphology in a mouse model of MDC1A
Virginie Carmignac et al.
HUMAN MOLECULAR GENETICS (2011)
Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies
Kinga I. Gawlik et al.
SKELETAL MUSCLE (2011)
Role of TGF-beta signaling in inherited and acquired myopathies
Tyesha N. Burks et al.
SKELETAL MUSCLE (2011)
Regulation and dysregulation of fibrosis in skeletal muscle
Antonio L. Serrano et al.
EXPERIMENTAL CELL RESEARCH (2010)
Effects of 2,4-diaminoquinazoline derivatives on SMN expression and phenotype in a mouse model for spinal muscular atrophy
Matthew E. R. Butchbach et al.
HUMAN MOLECULAR GENETICS (2010)
TRANSGENIC OVEREXPRESSION OF LAMININ α1 CHAIN IN LAMININ α2 CHAIN-DEFICIENT MICE RESCUES THE DISEASE THROUGHOUT THE LIFESPAN
Kinga I. Gawlik et al.
MUSCLE & NERVE (2010)
Distinct Roles for Laminin Globular Domains in Laminin α1 Chain Mediated Rescue of Murine Laminin α2 Chain Deficiency
Kinga I. Gawlik et al.
PLOS ONE (2010)
The impact of the extracellular matrix on inflammation
Lydia Sorokin
NATURE REVIEWS IMMUNOLOGY (2010)
Pathology Is Alleviated by Doxycycline in a Laminin-alpha 2-Null Model of Congenital Muscular Dystrophy
Mahasweta Girgenrath et al.
ANNALS OF NEUROLOGY (2009)
Prenatal chlorpyrifos exposure alters motor behavior and ultrasonic vocalization in cd-1 mouse pups
Aldina Venerosi et al.
ENVIRONMENTAL HEALTH (2009)
Omigapil Ameliorates the Pathology of Muscle Dystrophy Caused by Laminin-α2 Deficiency
Michael Erb et al.
JOURNAL OF PHARMACOLOGY AND EXPERIMENTAL THERAPEUTICS (2009)
Identification of a battery of tests for drug candidate evaluation in the SMNΔ7 neonate model of spinal muscular atrophy
Bassern F. El-Khodor et al.
EXPERIMENTAL NEUROLOGY (2008)
Neural stem cell transplantation can ameliorate the phenotype of a mouse model of spinal muscular atrophy
Stefania Corti et al.
JOURNAL OF CLINICAL INVESTIGATION (2008)
SOCS regulation of the JAK/STAT signalling pathway
Ben A. Croker et al.
SEMINARS IN CELL & DEVELOPMENTAL BIOLOGY (2008)
Regular exercise prolongs survival in a type 2 spinal muscular atrophy model mouse
C Grondard et al.
JOURNAL OF NEUROSCIENCE (2005)
Expression and function of laminins in the embryonic and mature vasculature
R Hallmann et al.
PHYSIOLOGICAL REVIEWS (2005)
Diseased muscles that lack dystrophin or laminin-α2 have altered compositions and proliferation of mononuclear cell populations -: art. no. 7
M Girgenrath et al.
BMC NEUROLOGY (2005)
Laminins α2 and α4 in pancreatic acinar basement membranes are required for basal receptor localization
JH Miner et al.
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY (2004)
Laminin α1 chain reduces muscular dystrophy in laminin α2 chain deficient mice
K Gawlik et al.
HUMAN MOLECULAR GENETICS (2004)
Expression and distribution of laminin α1 and α2 chains in embryonic and adult mouse tissues:: An immunochemical approach
T Sasaki et al.
EXPERIMENTAL CELL RESEARCH (2002)
Endothelial cell laminin isoforms, laminins 8 and 10, play decisive roles in T cell recruitment across the blood-brain barrier in experimental autoimmune encephalomyelitis
M Sixt et al.
JOURNAL OF CELL BIOLOGY (2001)