Related references
Note: Only part of the references are listed.Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome
John-Paul Berauer et al.
HEPATOLOGY (2019)
Transient elastography is useful in diagnosing biliary atresia and predicting prognosis after hepatoportoenterostomy
Jia-Feng Wu et al.
HEPATOLOGY (2018)
A randomized, placebo-controlled trial of cenicriviroc for treatment of nonalcoholic steatohepatitis with fibrosis
Scott L. Friedman et al.
HEPATOLOGY (2018)
Province-wide Biliary Atresia Home Screening Program in British Columbia: Evaluation of First 2 Years
Jessica P. Woolfson et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2018)
Oral Cholic Acid Is Efficacious and Well Tolerated in Patients With Bile Acid Synthesis and Zellweger Spectrum Disorders
James E. Heubi et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2018)
Inborn Errors of Metabolism with Hepatopathy Metabolism Defects of Galactose, Fructose, and Tyrosine
Didem Demirbas et al.
PEDIATRIC CLINICS OF NORTH AMERICA (2018)
Reducing the Underimmunization of Transplant Recipients
Amy G. Feldman et al.
JAMA PEDIATRICS (2018)
Nuclear Receptors and Liver Disease: Summary of the 2017 Basic Research Symposium
Melanie Tran et al.
HEPATOLOGY COMMUNICATIONS (2018)
Placebo-Controlled Randomized Trial of an Intestinal Bile Salt Transport Inhibitor for Pruritus in Alagille Syndrome
Benjamin L. Shneider et al.
HEPATOLOGY COMMUNICATIONS (2018)
Biliary Atresia: Indications and Timing of Liver Transplantation and Optimization of Pretransplant Care
Shikha S. Sundaram et al.
LIVER TRANSPLANTATION (2017)
Diagnosis and treatment of tyrosinemia type I: a US and Canadian consensus group review and recommendations
Jeffrey M. Chinsky et al.
GENETICS IN MEDICINE (2017)
Analysis of Surgical Interruption of the Enterohepatic Circulation as a Treatment for Pediatric Cholestasis
Kasper S. Wang et al.
HEPATOLOGY (2017)
Hepatic Uptake of Conjugated Bile Acids Is Mediated by Both Sodium Taurocholate Cotransporting Polypeptide and Organic Anion Transporting Polypeptides and Modulated by Intestinal Sensing of Plasma Bile Acid Levels in Mice
Davor Slijepcevic et al.
HEPATOLOGY (2017)
New Therapeutic Concepts in Bile Acid Transport and Signaling for Management of Cholestasis
Michael Trauner et al.
HEPATOLOGY (2017)
EASL Clinical Practice Guidelines: The diagnosis and management of patients with primary biliary cholangitis
Gideon M. Hirschfield et al.
JOURNAL OF HEPATOLOGY (2017)
Guideline for the Evaluation of Cholestatic Jaundice in Infants: Joint Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition and the European Society for Pediatric Gastroenterology, Hepatology, and Nutrition
Rima Fawaz et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2017)
Hospitalizations for Respiratory Syncytial Virus and Vaccine-Preventable Infections in the First 2 Years After Pediatric Liver Transplant
Amy G. Feldman et al.
JOURNAL OF PEDIATRICS (2017)
Incidence of Biliary Atresia and Timing of Hepatoportoenterostomy in the United States
Perri C. Hopkins et al.
JOURNAL OF PEDIATRICS (2017)
Large-scale proteomics identifies MMP-7 as a sentinel of epithelial injury and of biliary atresia
Chatmanee Lertudomphonwanit et al.
SCIENCE TRANSLATIONAL MEDICINE (2017)
Bile acids initiate cholestatic liver injury by triggering a hepatocyte-specific inflammatory response
Shi-Ying Cai et al.
JCI INSIGHT (2017)
Pharmacological Inhibition of Apical Sodium-Dependent Bile Acid Transporter Changes Bile Composition and Blocks Progression of Sclerosing Cholangitis in Multidrug Resistance 2 Knockout Mice
Alexander G. Miethke et al.
HEPATOLOGY (2016)
Increased frequency of double and triple heterozygous gene variants in children with intrahepatic cholestasis
Monique L. Goldschmidt et al.
HEPATOLOGY RESEARCH (2016)
Key Histopathologic Features of Liver Biopsies That Distinguish Biliary Atresia From Other Causes of Infantile Cholestasis and Their Correlation With Outcome A Multicenter Study
Pierre Russo et al.
AMERICAN JOURNAL OF SURGICAL PATHOLOGY (2016)
Cholestasis in Preterm Infants
Katie Satrom et al.
CLINICS IN PERINATOLOGY (2016)
The toxin biliatresone causes mouse extrahepatic cholangiocyte damage and fibrosis through decreased glutathione and SOX17
Orith Waisbourd-Zinman et al.
HEPATOLOGY (2016)
Inhibition of intestinal bile acid absorption improves cholestatic liver and bile duct injury in a mouse model of sclerosing cholangitis
Anna Baghdasaryan et al.
JOURNAL OF HEPATOLOGY (2016)
Biliary atresia and other cholestatic childhood diseases: Advances and future challenges
Henkjan J. Verkade et al.
JOURNAL OF HEPATOLOGY (2016)
Newborn Direct or Conjugated Bilirubin Measurements As a Potential Screen for Biliary Atresia
Sanjiv Harpavat et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2016)
Molecular Genetic Dissection and Neonatal/Infantile Intrahepatic Cholestasis Using Targeted Next-Generation Sequencing
Takao Togawa et al.
JOURNAL OF PEDIATRICS (2016)
Newborn Bilirubin Screening for Biliary Atresia
Sanjiv Harpavat et al.
NEW ENGLAND JOURNAL OF MEDICINE (2016)
A Specially Designed Multi-Gene Panel Facilitates Genetic Diagnosis in Children with Intrahepatic Cholestasis: Simultaneous Test of Known Large Insertions/Deletions
Neng-Li Wang et al.
PLOS ONE (2016)
Biliatresone, a Reactive Natural Toxin from Dysphania glomulifera and D. littoralis: Discovery of the Toxic Moiety 1,2-Diaryl-2-Propenone
Kyung A. Koo et al.
CHEMICAL RESEARCH IN TOXICOLOGY (2015)
Targeted pharmacotherapy in progressive familial intrahepatic cholestasis type 2: Evidence for improvement of cholestasis with 4-phenylbutyrate
Emmanuel Gonzales et al.
HEPATOLOGY (2015)
New paradigms in the treatment of hepatic cholestasis: From UDCA to FXR, PXR and beyond
Ulrich Beuers et al.
JOURNAL OF HEPATOLOGY (2015)
Cost-Effective Analysis of Screening for Biliary Atresia With the Stool Color Card
Douglas Mogul et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2015)
Intestinal Microbiota, Lipids, and the Pathogenesis of Intestinal Failure-Associated Liver Disease
Way Seah Lee et al.
JOURNAL OF PEDIATRICS (2015)
Taking the next step forward - Diagnosing inherited infantile cholestatic disorders with next generation sequencing
S. M. Herbst et al.
MOLECULAR AND CELLULAR PROBES (2015)
Contribution of acoustic radiation force impulse (ARFI) elastography to the ultrasound diagnosis of biliary atresia
Sylviane Hanquinet et al.
PEDIATRIC RADIOLOGY (2015)
Bile acid nuclear receptor FXR and digestive system diseases
Lili Ding et al.
ACTA PHARMACEUTICA SINICA B (2015)
Shear wave elastography helps differentiate biliary atresia from other neonatal/infantile liver diseases
Jessica R. Leschied et al.
PEDIATRIC RADIOLOGY (2015)
PoopMD, a Mobile Health Application, Accurately Identifies Infant Acholic Stools
Amy Franciscovich et al.
PLOS ONE (2015)
Use of Corticosteroids After Hepatoportoenterostomy for Bile Drainage in Infants With Biliary Atresia The START Randomized Clinical Trial
Jorge A. Bezerra et al.
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION (2014)
Intractable itch relieved by 4-phenylbutyrate therapy in patients with progressive familial intrahepatic cholestasis type 1
Yasuhiro Hasegawa et al.
ORPHANET JOURNAL OF RARE DISEASES (2014)
Three-Dimensional Magnetic Resonance Cholangiopancreatography for the Diagnosis of Biliary Atresia in Infants and Neonates
Bo Liu et al.
PLOS ONE (2014)
The therapeutic potential of chemical chaperones in protein folding diseases
Leonardo Cortez et al.
PRION (2014)
Nuclear Receptors as Drug Targets in Cholestatic Liver Diseases
Emina Halilbasic et al.
CLINICS IN LIVER DISEASE (2013)
Improving outcomes of biliary atresia: French national series 1986-2009
Christophe Chardot et al.
JOURNAL OF HEPATOLOGY (2013)
Mitochondrial Hepatopathies: Advances in Genetics, Therapeutic Approaches, and Outcomes
Way Seah Lee et al.
JOURNAL OF PEDIATRICS (2013)
Accuracy of hepatobiliary scintigraphy for differentiation of neonatal hepatitis from biliary atresia: systematic review and meta-analysis of the literature
Hamid Reza Kianifar et al.
PEDIATRIC RADIOLOGY (2013)
The SPLIT Research Agenda 2013
Estella M. Alonso et al.
PEDIATRIC TRANSPLANTATION (2013)
Association of variants of ABCB11 with transient neonatal cholestasis
Li-Yan Liu et al.
PEDIATRICS INTERNATIONAL (2013)
Phytosterols Promote Liver Injury and Kupffer Cell Activation in Parenteral Nutrition-Associated Liver Disease
Karim C. El Kasmi et al.
SCIENCE TRANSLATIONAL MEDICINE (2013)
Long Term Outcomes after Pediatric Liver Transplantation
Nada A. Yazigi
PEDIATRIC GASTROENTEROLOGY HEPATOLOGY & NUTRITION (2013)
Alterations in Lipid Metabolism Mediate Inflammation, Fibrosis, and Proliferation in a Mouse Model of Chronic Cholestatic Liver Injury
Tarek Moustafa et al.
GASTROENTEROLOGY (2012)
A biliary HCO3- umbrella constitutes a protective mechanism against bile acid-induced injury in human cholangiocytes
Simon Hohenester et al.
HEPATOLOGY (2012)
Portal Hypertension in Children and Young Adults With Biliary Atresia
Benjamin L. Shneider et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2012)
Parenteral nutrition supplementation in biliary atresia patients listed for liver transplantation
Jillian S. Sullivan et al.
LIVER TRANSPLANTATION (2012)
HIDA, percutaneous transhepatic cholecysto-cholangiography and liver biopsy in infants with persistent jaundice: can a combination of PTCC and liver biopsy reduce unnecessary laparotomy?
M. Kyle Jensen et al.
PEDIATRIC RADIOLOGY (2012)
Role of Abdominal Sonography in the Preoperative Diagnosis of Extrahepatic Biliary Atresia in Infants Younger Than 90 Days
Vinayak Mittal et al.
AMERICAN JOURNAL OF ROENTGENOLOGY (2011)
Design and Validation of the Biliary Atresia Research Consortium Histologic Assessment System for Cholestasis in Infancy
Pierre Russo et al.
CLINICAL GASTROENTEROLOGY AND HEPATOLOGY (2011)
Effects of the Infant Stool Color Card Screening Program on 5-Year Outcome of Biliary Atresia in Taiwan
Tien-Hau Lien et al.
HEPATOLOGY (2011)
Stool Color Card Screening for Biliary Atresia
Jui-Ju Tseng et al.
PEDIATRICS (2011)
Patients With Biliary Atresia Have Elevated Direct/Conjugated Bilirubin Levels Shortly After Birth
Sanjiv Harpavat et al.
PEDIATRICS (2011)
Folding Defects in P-Type ATP 8B1 Associated with Hereditary Cholestasis Are Ameliorated by 4-Phenylbutyrate
Lieke M. van der Velden et al.
HEPATOLOGY (2010)
Analysis of Gene Mutations in Children With Cholestasis of Undefined Etiology
Ursula Matte et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2010)
APPLICATIONS OF NEXT-GENERATION SEQUENCING Sequencing technologies - the next generation
Michael L. Metzker
NATURE REVIEWS GENETICS (2010)
Liver fibrosis in biliary atresia
Allah B. Haafiz
EXPERT REVIEW OF GASTROENTEROLOGY & HEPATOLOGY (2010)
Comparison of different diagnostic methods for differentiating biliary atresia from idiopathic neonatal hepatitis
Ji-Gang Yang et al.
CLINICAL IMAGING (2009)
Recent insights into the function and regulation of the bile salt export pump (ABCB11)
Bruno Stieger
CURRENT OPINION IN LIPIDOLOGY (2009)
Side Chain Structure Determines Unique Physiologic and Therapeutic Properties of norUrsodeoxycholic Acid in Mdr2-/- Mice
Emina Halilbasic et al.
HEPATOLOGY (2009)
High-Dose Ursodeoxycholic Acid for the Treatment of Primary Sclerosing Cholangitis
Keith D. Lindor et al.
HEPATOLOGY (2009)
Selective Use of Endoscopic Retrograde Cholangiopancreatography in the Diagnosis of Biliary Atresia in Infants Younger Than 100 Days
Naresh P. Shanmugam et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2009)
Impact of Age at Kasai Operation on Its Results in Late Childhood and Adolescence: A Rational Basis for Biliary Atresia Screening
Marie-Odile Serinet et al.
PEDIATRICS (2009)
Parenteral Nutrition-associated Cholestasis in Premature Babies: Risk Factors and Predictors
Meng-Han Hsieh et al.
PEDIATRICS AND NEONATOLOGY (2009)
Medical Treatment of Cholestatic Liver Disease
Gustav Paumgartner et al.
CLINICS IN LIVER DISEASE (2008)
Experience of nitisinone for the pharmacological treatment of hereditary tyrosinaemia type 1
Saikat Santra et al.
EXPERT OPINION ON PHARMACOTHERAPY (2008)
Biochemical response to ursodeoxycholic acid and long-term prognosis in primary biliary cirrhosis
Christophe Corpechot et al.
HEPATOLOGY (2008)
Percutaneously inserted central catheter for total parenteral nutrition in neonates: Complications rates related to upper versus lower extremity insertion
Viet Hoang et al.
PEDIATRICS (2008)
Mechanisms of disease: inborn errors of bile acid synthesis
Shikha S. Sundaram et al.
NATURE CLINICAL PRACTICE GASTROENTEROLOGY & HEPATOLOGY (2008)
Universal screening for biliary atresia using an infant stool color card in Taiwan
Cheng-Hui Hsiao et al.
HEPATOLOGY (2008)
Biliary atresia: The Canadian experience
Richard A. Schreiber et al.
JOURNAL OF PEDIATRICS (2007)
Growth failure and outcomes in infants with biliary atresia: A report from the biliary atresia research consortium
Patricia A. DeRusso et al.
HEPATOLOGY (2007)
Expression of bile acid synthesis and detoxification enzymes and the alternative bile acid efflux pump MRP4 in patients with primary biliary cirrhosis
Gernot Zollner et al.
LIVER INTERNATIONAL (2007)
Screening and outcomes in biliary atresia: Summary of a National Institutes of Health workshop
Ronald J. Sokol et al.
HEPATOLOGY (2007)
4-phenylbutyrate enhances the cell surface expression and the transport capacity of wild-type and mutated bile salt export pumps
Hisamitsu Hayashi et al.
HEPATOLOGY (2007)
24-norUrsodeoxycholic acid is superior to ursodeoxycholic acid in the treatment of sclerosing cholangitis in Mdr2 (Abcb4) knockout mice
P Fickert et al.
GASTROENTEROLOGY (2006)
Immunization of pediatric solid-organ transplantation candidates: Immunizations in transplant candidates
AL Campbell et al.
PEDIATRIC TRANSPLANTATION (2005)
Biliary atresia: Clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation
EC Utterson et al.
JOURNAL OF PEDIATRICS (2005)
Intrahepatic cholestasis: Summary of an American Association for the Study of Liver Diseases single-topic conference
WF Balistreri et al.
HEPATOLOGY (2005)
Prolonged follow-up of patients in the US multicenter trial of ursodeoxycholic acid for primary biliary cirrhosis
B Combes et al.
AMERICAN JOURNAL OF GASTROENTEROLOGY (2004)
Prevention of cholesterol gallstone disease by FXR agonists in a mouse model
A Moschetta et al.
NATURE MEDICINE (2004)
Percutaneous cholecysto-cholangiography in the diagnosis of obstructive jaundice in infants
RL Meyers et al.
JOURNAL OF PEDIATRIC SURGERY (2004)
Studies of Pediatric Liver Transplantation 2002: Patient and graft survival and rejection in pediatric recipients of a first liver transplant in the United States and Canada
SR Martin et al.
PEDIATRIC TRANSPLANTATION (2004)
Farnesoid X receptor activates transcription of the phospholipid pump MDR3
L Huang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Transient cholestasis in newborn infants with perinatal asphyxia
D Herzog et al.
CANADIAN JOURNAL OF GASTROENTEROLOGY AND HEPATOLOGY (2003)
Niemann-Pick disease type C in neonatal cholestasis at a North American center
B Yerushalmi et al.
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION (2002)
Regulation of multidrug resistance-associated protein 2 (ABCC2) by nuclear receptors pregnane X receptor, farnesoid X-activated receptor, and constitutive androstane receptor
HR Kast et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2002)
Cholangiocyte biology and cystic fibrosis liver disease
AP Feranchak et al.
SEMINARS IN LIVER DISEASE (2001)
Long-term effects of ursodeoxycholic acid in primary biliary cirrhosis:: results of a double-blind controlled multicentric trial
A Parés et al.
JOURNAL OF HEPATOLOGY (2000)
Share Paper
