Related references
Note: Only part of the references are listed.Mitochondrial inner-membrane protease Yme1 degrades outer-membrane proteins Tom22 and Om45
Xi Wu et al.
JOURNAL OF CELL BIOLOGY (2018)
The plant i-AAA protease controls the turnover of an essential mitochondrial protein import component
Magdalena Opalinska et al.
JOURNAL OF CELL SCIENCE (2018)
Effect of Tim23 knockdown in vivo on mitochondrial protein import and retrograde signaling to the UPRmt in muscle
Ashley N. Oliveira et al.
AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY (2018)
Plant mitochondrial protein import: the ins and outs
Abi S. Ghifari et al.
BIOCHEMICAL JOURNAL (2018)
Dissecting Substrate Specificities of the Mitochondrial AFG3L2 Protease
Bojian Ding et al.
BIOCHEMISTRY (2018)
m-AAA proteases, mitochondrial calcium homeostasis and neurodegeneration
Maria Patron et al.
CELL RESEARCH (2018)
Mitophagy and Quality Control Mechanisms in Mitochondrial Maintenance
Sarah Pickles et al.
CURRENT BIOLOGY (2018)
Mitochondrial dynamics: overview of molecular mechanisms
Lisa Tilokani et al.
MITOCHONDRIAL DISEASES (2018)
Mitochondrial medicine in the omics era
Joyeeta Rahman et al.
LANCET (2018)
m-AAA Complexes Are Not Crucial for the Survival of Arabidopsis Under Optimal Growth Conditions Despite Their Importance for Mitochondria! Translation
Marta Kolodziejczak et al.
PLANT AND CELL PHYSIOLOGY (2018)
Mechanisms Orchestrating Mitochondrial Dynamics for Energy Homeostasis
Seungyoon B. Yu et al.
JOURNAL OF MOLECULAR BIOLOGY (2018)
SCA28: Novel Mutation in the AFG3L2 Proteolytic Domain Causes a Mild Cerebellar Syndrome with Selective Type-1 Muscle Fiber Atrophy
Kirsten Svenstrup et al.
CEREBELLUM (2017)
Prion-Like Polymerization in Immunity and Inflammation
Xin Cai et al.
COLD SPRING HARBOR PERSPECTIVES IN BIOLOGY (2017)
Identification of Physiological Substrates and Binding Partners of the Plant Mitochondrial Protease FTSH4 by the Trapping Approach
Magdalena Opalinska et al.
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES (2017)
Identification of a Degradation Signal Sequence within Substrates of the Mitochondrial i-AAA Protease
Anthony J. Rampello et al.
JOURNAL OF MOLECULAR BIOLOGY (2017)
The proteome of baker's yeast mitochondria
Humberto Gonczarowska-Jorge et al.
MITOCHONDRION (2017)
Cytosolic proteostasis through importing of misfolded proteins into mitochondria
Linhao Ruan et al.
NATURE (2017)
Structure of the mitochondrial inner membrane AAA plus protease YME1 gives insight into substrate processing
Cristina Puchades et al.
SCIENCE (2017)
Plasticity of Mitochondrial Translation
Sven Dennerlein et al.
TRENDS IN CELL BIOLOGY (2017)
Effects of lipids on mitochondrial functions
Christoph U. Martensson et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2017)
Biosynthesis, remodeling and turnover of mitochondrial cardiolipin
Michael Schlame et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS (2017)
Metalloproteases of the Inner Mitochondrial Membrane
Roman M. Levytskyy et al.
BIOCHEMISTRY (2017)
When, how and why? Regulated proteolysis by the essential FtsH protease in Escherichia coli
Lisa-Marie Bittner et al.
BIOLOGICAL CHEMISTRY (2017)
Multifunctional Mitochondrial AAA Proteases
Steven E. Glynn
FRONTIERS IN MOLECULAR BIOSCIENCES (2017)
Protein Translocation into the Intermembrane Space and Matrix of Mitochondria: Mechanisms and Driving Forces
Sandra Backes et al.
FRONTIERS IN MOLECULAR BIOSCIENCES (2017)
Loss of Drosophila i-AAA protease, dYME1L, causes abnormal mitochondria and apoptotic degeneration
Y. Qi et al.
CELL DEATH AND DIFFERENTIATION (2016)
Mic60/Mitofilin determines MICOS assembly essential for mitochondrial dynamics and mtDNA nucleoid organization
H. Li et al.
CELL DEATH AND DIFFERENTIATION (2016)
The membrane scaffold SLP2 anchors a proteolytic hub in mitochondria containing PARL and the i-AAA protease YME1L
Timothy Wai et al.
EMBO REPORTS (2016)
Protein quality control at the mitochondrion
Wolfgang Voos et al.
PROTEOSTASIS (2016)
The m-AAA Protease Associated with Neurodegeneration Limits MCU Activity in Mitochondria
Tim Koenig et al.
MOLECULAR CELL (2016)
Lack of FTSH4 Protease Affects Protein Carbonylation, Mitochondrial Morphology, and Phospholipid Content in Mitochondria of Arabidopsis: New Insights into a Complex Interplay
Elwira Smakowska et al.
PLANT PHYSIOLOGY (2016)
Engineered AAA plus proteases reveal principles of proteolysis at the mitochondrial inner membrane
Hui Shi et al.
NATURE COMMUNICATIONS (2016)
MICU1 Serves as a Molecular Gatekeeper to Prevent In Vivo Mitochondrial Calcium Overload
Julia C. Liu et al.
CELL REPORTS (2016)
The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying
Shuaiyu Wang et al.
PLOS GENETICS (2016)
Homozygous YME1L1 Mutation Causes Mitochondriopathy with Optic Atrophy and Mitochondrial Network Fragmentation
Bianca Hartmann et al.
ELIFE (2016)
Dual functions of a small regulatory subunit in the mitochondrial calcium uniporter complex
Ming-Feng Tsai et al.
ELIFE (2016)
Mitochondrial Protein Quality Control: The Mechanisms Guarding Mitochondrial Health
Iryna Bohovych et al.
ANTIOXIDANTS & REDOX SIGNALING (2015)
Mitochondrial Tim9 protects Tim10 from degradation by the protease Yme1
Michael P. Spiller et al.
BIOSCIENCE REPORTS (2015)
Quality control of mitochondrial protein synthesis is required for membrane integrity and cell fitness
Uwe Richter et al.
JOURNAL OF CELL BIOLOGY (2015)
A novel AFG3L2 mutation in a Somalian patient with spinocerebellar ataxia type 28
Jane Qu et al.
JOURNAL OF THE NEUROLOGICAL SCIENCES (2015)
New roles for mitochondrial proteases in health, ageing and disease
Pedro M. Quiros et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2015)
Imbalanced OPA1 processing and mitochondrial fragmentation cause heart failure in mice
Timothy Wai et al.
SCIENCE (2015)
Unlocking the presequence import pathway
Christian Schulz et al.
TRENDS IN CELL BIOLOGY (2015)
Purkinje neuron Ca2+ influx reduction rescues ataxia in SCA28 model
Francesca Maltecca et al.
JOURNAL OF CLINICAL INVESTIGATION (2015)
Cardiolipin and Mitochondrial Function in Health and Disease
Giuseppe Paradies et al.
ANTIOXIDANTS & REDOX SIGNALING (2014)
Import of ribosomal proteins into yeast mitochondria
Michael W. Woellhaf et al.
BIOCHEMISTRY AND CELL BIOLOGY (2014)
Mutations in the SPG7 gene cause chronic progressive external ophthalmoplegia through disordered mitochondrial DNA maintenance
Gerald Pfeffer et al.
BRAIN (2014)
Mitochondrial protein quality control in health and disease
Michael J. Baker et al.
BRITISH JOURNAL OF PHARMACOLOGY (2014)
The LYR Factors SDHAF1 and SDHAF3 Mediate Maturation of the Iron-Sulfur Subunit of Succinate Dehydrogenase
Un Na et al.
CELL METABOLISM (2014)
The Protein Import Machinery of Mitochondria-A Regulatory Hub in Metabolism, Stress, and Disease
Angelika B. Harbauer et al.
CELL METABOLISM (2014)
The i-AAA protease YME1L and OMA1 cleave OPA1 to balance mitochondrial fusion and fission
Ruchika Anand et al.
JOURNAL OF CELL BIOLOGY (2014)
A Novel Missense Mutation in AFG3L2 Associated with Late Onset and Slow Progression of Spinocerebellar Ataxia Type 28
Anna Mareike Loebbe et al.
JOURNAL OF MOLECULAR NEUROSCIENCE (2014)
Proteomic Mapping of the Human Mitochondrial Intermembrane Space in Live Cells via Ratiometric APEX Tagging
Victoria Hung et al.
MOLECULAR CELL (2014)
Loss-of-function mutations in MICU1 cause a brain and muscle disorder linked to primary alterations in mitochondrial calcium signaling
Clare V. Logan et al.
NATURE GENETICS (2014)
Mitochondria in Health and Disease
Jose Magalhaes et al.
OXIDATIVE MEDICINE AND CELLULAR LONGEVITY (2014)
Spastic Paraplegia Type 7 Is Associated with Multiple Mitochondrial DNA Deletions
Iselin Marie Wedding et al.
PLOS ONE (2014)
Mitochondrial pathology: stress signals from the energy factory
Nuno Raimundo
TRENDS IN MOLECULAR MEDICINE (2014)
SPG7 Variant Escapes Phosphorylation-Regulated Processing by AFG3L2, Elevates Mitochondrial ROS, and Is Associated with Multiple Clinical Phenotypes
Naif A. M. Almontashiri et al.
CELL REPORTS (2014)
Inaccurately Assembled Cytochrome c Oxidase Can Lead to Oxidative Stress-Induced Growth Arrest
Manuela Bode et al.
ANTIOXIDANTS & REDOX SIGNALING (2013)
Mitochondria as a Source of Reactive Oxygen and Nitrogen Species: From Molecular Mechanisms to Human Health
Tiago R. Figueira et al.
ANTIOXIDANTS & REDOX SIGNALING (2013)
Proteolytic processing of Atg32 by the mitochondrial i-AAA protease Yme1 regulates mitophagy
Ke Wang et al.
AUTOPHAGY (2013)
Stress-Regulated Translational Attenuation Adapts Mitochondrial Protein Import through Tim17A Degradation
T. Kelly Rainbolt et al.
CELL METABOLISM (2013)
TRIAP1/PRELI Complexes Prevent Apoptosis by Mediating Intramitochondrial Transport of Phosphatidic Acid
Christoph Potting et al.
CELL METABOLISM (2013)
The Role of Mitochondria in Cellular Iron-Sulfur Protein Biogenesis: Mechanisms, Connected Processes, and Diseases
Oliver Stehling et al.
COLD SPRING HARBOR PERSPECTIVES IN BIOLOGY (2013)
Mitochondrial AAA proteases - Towards a molecular understanding of membrane-bound proteolytic machines
Florian Gerdes et al.
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH (2012)
Mitochondria: In Sickness and in Health
Jodi Nunnari et al.
CELL (2012)
AFG3L2 supports mitochondrial protein synthesis and Purkinje cell survival
Eva R. Almajan et al.
JOURNAL OF CLINICAL INVESTIGATION (2012)
Impaired Folding of the Mitochondria! Small TIM Chaperones Induces Clearance by the i-AAA Protease
Michael J. Baker et al.
JOURNAL OF MOLECULAR BIOLOGY (2012)
Intermembrane Space Proteome of Yeast Mitochondria
F. -Nora Voegtle et al.
MOLECULAR & CELLULAR PROTEOMICS (2012)
YME1L controls the accumulation of respiratory chain subunits and is required for apoptotic resistance, cristae morphogenesis, and cell proliferation
Lukas Stiburek et al.
MOLECULAR BIOLOGY OF THE CELL (2012)
Role of the AAA protease Yme1 in folding of proteins in the intermembrane space of mitochondria
Bernadette Schreiner et al.
MOLECULAR BIOLOGY OF THE CELL (2012)
Mitochondrial Import Efficiency of ATFS-1 Regulates Mitochondrial UPR Activation
Amrita M. Nargund et al.
SCIENCE (2012)
Intramitochondrial Transport of Phosphatidic Acid in Yeast by a Lipid Transfer Protein
Melanie Connerth et al.
SCIENCE (2012)
Mitochondrial quality control by the ubiquitin-proteasome system
Eric B. Taylor et al.
BIOCHEMICAL SOCIETY TRANSACTIONS (2011)
Regulating mitochondrial outer membrane proteins by ubiquitination and proteasomal degradation
Mariusz Karbowski et al.
CURRENT OPINION IN CELL BIOLOGY (2011)
Presequence-dependent folding ensures MrpL32 processing by the m-AAA protease in mitochondria
Florian Bonn et al.
EMBO JOURNAL (2011)
Electron Cryomicroscopy Structure of a Membrane-anchored Mitochondrial AAA Protease
Sukyeong Lee et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2011)
Making heads or tails of phospholipids in mitochondria
Christof Osman et al.
JOURNAL OF CELL BIOLOGY (2011)
Integrative genomics identifies MCU as an essential component of the mitochondrial calcium uniporter
Joshua M. Baughman et al.
NATURE (2011)
Inventory control: cytochrome c oxidase assembly regulates mitochondrial translation
David U. Mick et al.
NATURE REVIEWS MOLECULAR CELL BIOLOGY (2011)
Mitochondrial protein quality control during biogenesis and aging
Brooke M. Baker et al.
TRENDS IN BIOCHEMICAL SCIENCES (2011)
Whole-Exome Sequencing Identifies Homozygous AFG3L2 Mutations in a Spastic Ataxia-Neuropathy Syndrome Linked to Mitochondrial m-AAA Proteases
Tyler Mark Pierson et al.
PLOS GENETICS (2011)
Regulation of mitochondrial phospholipids by Ups1/PRELI-like proteins depends on proteolysis and Mdm35
Christoph Potting et al.
EMBO JOURNAL (2010)
Missense Mutations in the AFG3L2 Proteolytic Domain Account for ∼1.5% of European Autosomal Dominant Cerebellar Ataxias
Claudia Cagnoli et al.
HUMAN MUTATION (2010)
Identification and Characterization of High Molecular Weight Complexes Formed by Matrix AAA Proteases and Prohibitins in Mitochondria of Arabidopsis thaliana
Janusz Piechota et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2010)
Mutations in the mitochondrial protease gene AFG3L2 cause dominant hereditary ataxia SCA28
Daniela Di Bella et al.
NATURE GENETICS (2010)
Mitochondrial protease AtFtsH4 protects ageing Arabidopsis rosettes against oxidative damage under short-day photoperiod
Marta Kicia et al.
PLANT SIGNALING & BEHAVIOR (2010)
The Role of Mitochondria in Apoptosis
Chunxin Wang et al.
ANNUAL REVIEW OF GENETICS (2009)
Biogenesis of mitochondrial membrane proteins
Thomas Becker et al.
CURRENT OPINION IN CELL BIOLOGY (2009)
Genetic interaction between the m-AAA protease isoenzymes reveals novel roles in cerebellar degeneration
Paola Martinelli et al.
HUMAN MOLECULAR GENETICS (2009)
Prohibitins and the functional compartmentalization of mitochondrial membranes
Christof Osman et al.
JOURNAL OF CELL SCIENCE (2009)
Haploinsufficiency of AFG3L2, the Gene Responsible for Spinocerebellar Ataxia Type 28, Causes Mitochondria-Mediated Purkinje Cell Dark Degeneration
Francesca Maltecca et al.
JOURNAL OF NEUROSCIENCE (2009)
Autocatalytic Processing of m-AAA Protease Subunits in Mitochondria
Mirko Koppen et al.
MOLECULAR BIOLOGY OF THE CELL (2009)
An Intersubunit Signaling Network Coordinates ATP Hydrolysis by m-AAA Proteases
Steffen Augustin et al.
MOLECULAR CELL (2009)
Intra-mitochondrial degradation of Tim23 curtails the survival of cells rescued from apoptosis by caspase inhibitors
C. G. Goemans et al.
CELL DEATH AND DIFFERENTIATION (2008)
Spinocerebellar ataxia type 28: A novel autosomal dominant cerebellar ataxia characterized by slow progression and ophthalmoparesis
Caterina Mariotti et al.
CEREBELLUM (2008)
The mitochondrial protease AFG3L2 is essential for axonal development
Francesca Maltecca et al.
JOURNAL OF NEUROSCIENCE (2008)
Mgr3p and Mgr1p Are Adaptors for the Mitochondrial i-AAA Protease Complex
Cory D. Dunn et al.
MOLECULAR BIOLOGY OF THE CELL (2008)
OPA1 processing controls mitochondrial fusion and is regulated by mRNA splicing, membrane potential, and Yme1L
Zhiyin Song et al.
JOURNAL OF CELL BIOLOGY (2007)
Evidence for a pro-oxidant intermediate in the assembly of cytochrome oxidase
Oleh Khalimonchuk et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
m-AAA protease-driven membrane dislocation allows intramembrane cleavage by rhomboid in mitochondria
Takashi Tatsuta et al.
EMBO JOURNAL (2007)
Variable and tissue-specific subunit composition of mitochondrial m-AAA protease complexes linked to hereditary spastic paraplegia
Mirko Koppen et al.
MOLECULAR AND CELLULAR BIOLOGY (2007)
A new function in translocation for the mitochondrial i-AAA protease Yme1:: Import of polynucleotide phosphorylase into the intermembrane space
Robert N. Rainey et al.
MOLECULAR AND CELLULAR BIOLOGY (2006)
Classification of AAA+ proteins
Moritz Ammelburg et al.
JOURNAL OF STRUCTURAL BIOLOGY (2006)
Mitochondria: More than just a powerhouse
Heidi M. McBride et al.
CURRENT BIOLOGY (2006)
A genomewide screen for petite-negative yeast strains yields a new subunit of the i-AAA protease complex
CD Dunn et al.
MOLECULAR BIOLOGY OF THE CELL (2006)
SCA28, a novel form of autosomal dominant cerebellar ataxia on chromosome 18p11.22-q11.2
C Cagnoli et al.
BRAIN (2006)
The m-AAA protease defective in hereditary spastic paraplegia controls ribosome assembly in mitochondria
M Nolden et al.
CELL (2005)
Plant mitochondria contain at least two i-AAA-like complexes
A Urantowka et al.
PLANT MOLECULAR BIOLOGY (2005)
Evolutionary history and higher order classification of AAA plus ATPases
LM Iyer et al.
JOURNAL OF STRUCTURAL BIOLOGY (2004)
Axonal degeneration in paraplegin-deficient mice is associated with abnormal mitochondria and impairment of axonal transport
F Ferreirinha et al.
JOURNAL OF CLINICAL INVESTIGATION (2004)
Oma1, a novel membrane-bound metallopeptidase in mitochondria with activities overlapping with the m-AAA protease
M Käser et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2003)
Molecular and functional analyses of the human and mouse genes encoding AFG3L1, a mitochondrial metalloprotease homologous to the human spastic paraplegia protein
G Kremmidiotis et al.
GENOMICS (2001)
Membrane protein degradation by AAA proteases in mitochondria: Extraction of substrates from either membrane surface
K Leonhard et al.
MOLECULAR CELL (2000)