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Dynamic subcompartmentalization of the mitochondrial inner membrane
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Monolysocardiolipin in cultured fibroblasts is a sensitive and specific marker for Barth Syndrome
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A zebrafish model of human Barth syndrome reveals the essential role of tafazzin in cardiac development and function
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Identification and characterization of human cardiolipin synthase
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FEBS LETTERS (2006)
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Mutation of DNAJC19, a human homologue of yeast inner mitochondrial membrane co-chaperones, causes DCMA syndrome, a novel autosomal recessive Barth syndrome-like condition
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Shotgun lipidomics of cardiolipin molecular species in lipid extracts of biological samples
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Molecular symmetry in mitochondrial cardiolipins
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Taz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: Implications for Barth syndrome
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The import motor of the yeast mitochondrial TIM23 preprotein translocase contains two different J proteins, Tim14 and Mdj2
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Cytochrome c acts as a cardiolipin oxygenase required for release of proapoptotic factors
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Role of Pam16's degenerate J domain in protein import across the mitochondrial inner membrane
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A novel acylglycerol kinase that produces lysophosphatidic acid modulates cross talk with EGFR in prostate cancer cells
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Characterization of lymphoblast mitochondria from patients with Barth syndrome
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Monolysocardiolipins accumulate in Barth syndrome but do not lead to enhanced apoptosis
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Nuclear genes and mitochondrial translation: a new class of genetic disease
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tBid interaction with cardiolipin primarily orchestrates mitochondrial dysfunctions and subsequently activates Bax and Bak
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The mitochondrial inner membrane protein mitofilin controls cristae morphology
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Cloning and characterization of murine 1-acyl-sn-glycerol 3-phosphate acyltransferases and their regulation by PPARα in murine heart
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BIOCHEMICAL JOURNAL (2005)
Mitochondrial DNA and disease
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ANNALS OF MEDICINE (2005)
Formation of membrane-bound ring complexes by prohibitins in mitochondria
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Identification of a new glycerol-3-phosphate acyltransferase isoenzyme, mtGPAT2, in mitochondria*
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The J domain-related cochaperone Tim16 is a constituent of the mitochondrial TIM23 preprotein translocase
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NATURE STRUCTURAL & MOLECULAR BIOLOGY (2004)
Pam16 has an essential role in the mitochondrial protein import motor
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MuLK, a eukaryotic multi-substrate lipid kinase
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RK Naviaux
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Aberrant cardiolipin metabolism in the yeast taz1 mutant: a model for Barth syndrome
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X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): An update
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Cardiolipin stabilizes respiratory chain supercomplexes
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Phospholipid abnormalities in children with Barth syndrome
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A J-protein is an essential subunit of the presequence translocase-associated protein import motor of mitochondria
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Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism
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Tim14, a novel key component of the import motor of the TIM23 protein translocase of mitochondria
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Characterization of the human heart mitochondrial proteome
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CELL (2002)
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