Journal
PEDIATRIC BLOOD & CANCER
Volume 59, Issue 2, Pages 318-319Publisher
WILEY-BLACKWELL
DOI: 10.1002/pbc.23393
Keywords
lymphoma; prognosis; treatment; Wiskott-Aldrich syndrome
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Wiskott-Aldrich syndrome (WAS) is characterized by primary immunodeficiency, thrombocytopenia and eczema. Patients with WAS have an increased risk to develop tumors. Non-Hodgkin lymphoma (NHL) represents the most common malignancy occurring in WAS-affected patients, diffuse-large-B-cell lymphoma is the most frequently encountered variant. We describe a case of a patient with WAS and NHL in the pharynx, an atypical tumor site presentation. The patient was successfully treated with a reduced dose chemotherapy regimen plus anti-CD20 monoclonal antibody. He is in complete remission 3 years from the start of treatment. Pediatr Blood Cancer 2012;59:318319. (c) 2011 Wiley Periodicals, Inc.
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