Related references
Note: Only part of the references are listed.Monomerized Cu,Zn-superoxide dismutase induces oxidative stress through aberrant Cu binding
Hitoshi Kishigami et al.
FREE RADICAL BIOLOGY AND MEDICINE (2010)
An examination of wild-type SOD1 in modulating the toxicity and aggregation of ALS-associated mutant SOD1
Mercedes Prudencio et al.
HUMAN MOLECULAR GENETICS (2010)
Variation in aggregation propensities among ALS-associated variants of SOD1: Correlation to human disease
Mercedes Prudencio et al.
HUMAN MOLECULAR GENETICS (2009)
Modulation of mutant superoxide dismutase 1 aggregation by co-expression of wild-type enzyme
Mercedes Prudencio et al.
JOURNAL OF NEUROCHEMISTRY (2009)
Molecular dissection of ALS-associated toxicity of SOD1 in transgenic mice using an exon-fusion approach
Deng Han-Xiang et al.
HUMAN MOLECULAR GENETICS (2008)
A limited role for disulfide cross-linking in the aggregation of mutant SOD1 linked to familial amyotrophic lateral sclerosis
Celeste M. Karch et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Complete loss of post-translational modifications triggers fibrillar aggregation of SOD1 in the familial form of amyotrophic lateral sclerosis
Yoshiaki Furukawa et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Neuron-specific expression of mutant superoxide dismutase is sufficient to induce amyotrophic lateral sclerosis in transgenic mice
Dick Jaarsma et al.
JOURNAL OF NEUROSCIENCE (2008)
Initiation and elongation in fibrillation of ALS-linked superoxide dismutase
Madhuri Chattopadhyay et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)
Cysteine 111 affects aggregation and cytotoxicity of mutant Cu,Zn-superoxide dismutase associated with familial amyotrophic lateral sclerosis
Mauro Cozzolino et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2008)
Time course of preferential motor unit loss in the SODIG93A mouse model of amyotrophic lateral sclerosis
J. Hegedus et al.
NEUROBIOLOGY OF DISEASE (2007)
Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD1
Jun-ichi Niwa et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Metal-free superoxide dismutase forms soluble oligomers under physiological conditions: A possible general mechanism for familial ALS
Lucia Banci et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2007)
Increased affinity for copper mediated by cysteine 111 in forms of mutant superoxide dismutase 1 linked to amyotrophic lateral sclerosis
Shohei Watanabe et al.
FREE RADICAL BIOLOGY AND MEDICINE (2007)
Disease-associated mutations at copper ligand histidine residues of superoxide dismutase 1 diminish the binding of copper and compromise dimer stability
Jiou Wang et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2007)
Motor neuron disease in mice expressing the wild type-like D90A mutant superoxide dismutase-1
P. Andreas Jonsson et al.
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY (2006)
Conversion to the amyotrophic lateral sclerosis phenotype is associated with intermolecular linked insoluble aggregates of SOD1 in mitochondria
HX Deng et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)
Mapping superoxide dismutase 1 domains of non-native interaction: roles of intra- and intermolecular disulfide bonding in aggregation
J Wang et al.
JOURNAL OF NEUROCHEMISTRY (2006)
Coincident thresholds of mutant protein for paralytic disease and protein aggregation caused by restrictively expressed superoxide dismutase cDNA
J Wang et al.
NEUROBIOLOGY OF DISEASE (2005)
Aberrantly increased hydrophobicity shared by mutants of Cu,Zn-superoxide dismutase in familial amyotrophic lateral sclerosis
A Tiwari et al.
JOURNAL OF BIOLOGICAL CHEMISTRY (2005)
Somatodendritic accumulation of misfolded SOD1-L126Z in motor neurons mediates degeneration:: αB-crystallin modulates aggregation
J Wang et al.
HUMAN MOLECULAR GENETICS (2005)
Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man
LR Fischer et al.
EXPERIMENTAL NEUROLOGY (2004)
Amyloid-like filaments and water-filled nanotubes formed by SOD1 mutant proteins linked to familial ALS
JS Elam et al.
NATURE STRUCTURAL BIOLOGY (2003)
Misfolded CuZnSOD and amyotrophic lateral sclerosis
JS Valentine et al.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)
Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature
J Wang et al.
HUMAN MOLECULAR GENETICS (2003)
Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site
J Wang et al.
NEUROBIOLOGY OF DISEASE (2002)
Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues
M Watanabe et al.
NEUROBIOLOGY OF DISEASE (2001)
Share Paper
