4.1 Article

The Prion Diseases

Related references

Note: Only part of the references are listed.
Article Biochemistry & Molecular Biology

Live Cell Fluorescence Resonance Energy Transfer Predicts an Altered Molecular Association of Heterologous PrPSc with PrPC

Suparna Mallik et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2010)

Article Neurosciences

Axonal prion protein is required for peripheral myelin maintenance

Juliane Bremer et al.

NATURE NEUROSCIENCE (2010)

Review Clinical Neurology

Genetics and molecular pathogenesis of sporadic and hereditary cerebral amyloid angiopathies

Tamas Revesz et al.

ACTA NEUROPATHOLOGICA (2009)

Article

Cellular Prion Protein Mediates the Toxicity of β-Amyloid Oligomers

Haakon B. Nygaard et al.

ARCHIVES OF NEUROLOGY (2009)

Article Neurosciences

RNAi for the Treatment of Prion Disease: A Window for Intervention in Neurodegeneration?

Melanie D. White et al.

CNS & NEUROLOGICAL DISORDERS-DRUG TARGETS (2009)

Article Biochemistry & Molecular Biology

Human Prion Protein (PrP) 219K Is Converted to PrPSc but Shows Heterozygous Inhibition in Variant Creutzfeldt-Jakob Disease Infection

Masaki Hizume et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2009)

Article Medicine, General & Internal

A Novel Protective Prion Protein Variant that Colocalizes with Kuru Exposure

Simon Mead et al.

NEW ENGLAND JOURNAL OF MEDICINE (2009)

Article Biochemistry & Molecular Biology

Regulation of Embryonic Cell Adhesion by the Prion Protein

Edward Malaga-Trillo et al.

PLOS BIOLOGY (2009)

Article Clinical Neurology

Huntington's disease phenocopies are clinically and genetically heterogeneous

Edward J. Wild et al.

MOVEMENT DISORDERS (2008)

Article Clinical Neurology

Two different clinical phenotypes of Creutzfeldt-Jakob disease with a M232R substitution

Yusei Shiga et al.

JOURNAL OF NEUROLOGY (2007)

Article Multidisciplinary Sciences

Cellular prion protein regulates β-secretase cleavage of the Alzheimer's amyloid precursor protein

Edward T. Parkin et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2007)

Article Geriatrics & Gerontology

Total tau protein in cerebrospinal fluid and diffusion-weighted MRI as an early diagnostic marker for Creutzfeldt-Jakob disease

Katsuya Satoh et al.

DEMENTIA AND GERIATRIC COGNITIVE DISORDERS (2007)

Article Neurosciences

V180I mutation of the prion protein gene associated with atypical PrPSc glycosylation

Stephanie Chasseigneaux et al.

NEUROSCIENCE LETTERS (2006)

Review Immunology

The role of the cellular prion protein in the immune system

J. D. Isaacs et al.

CLINICAL AND EXPERIMENTAL IMMUNOLOGY (2006)

Article Multidisciplinary Sciences

Presymptomatic detection of prions in blood

Paula Saa et al.

SCIENCE (2006)

Article Clinical Neurology

Childhood onset in familial prion disease with a novel mutation in the PRNP gene

Ekaterina Rogaeva et al.

ARCHIVES OF NEUROLOGY (2006)

Article Neurosciences

Clearance and prevention of prion infection in cell culture by anti-PrP antibodies

Joanna Pankiewicz et al.

EUROPEAN JOURNAL OF NEUROSCIENCE (2006)

Article Clinical Neurology

Familial Creutzfeldt-Jakob disease with an R208H-129V haplotype and Kuru plaques

C Basset-Leobon et al.

ARCHIVES OF NEUROLOGY (2006)

Article Geriatrics & Gerontology

Prion protein (PrPc) promotes β-amyloid plaque formation

KA Schwarze-Eicker et al.

NEUROBIOLOGY OF AGING (2005)

Review Genetics & Heredity

Cellular prion protein neuroprotective function: implications in prion diseases

X Roucou et al.

JOURNAL OF MOLECULAR MEDICINE-JMM (2005)

Article Multidisciplinary Sciences

Cross-linking cellular prion protein triggers neuronal apoptosis in vivo

L Solforosi et al.

SCIENCE (2004)

Article Medicine, General & Internal

Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient

AH Peden et al.

LANCET (2004)

Article Multidisciplinary Sciences

Human prion protein with valine 129 prevents expression of variant CJD phenotype

JDF Wadsworth et al.

SCIENCE (2004)

Article Clinical Neurology

Loss of glycosylation associated with the T183A mutation in human prion disease

E Grasbon-Frodl et al.

ACTA NEUROPATHOLOGICA (2004)

Article Multidisciplinary Sciences

Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene

C Korth et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2003)

Article Medical Laboratory Technology

A murine model of a familial prion disease

DA Harris et al.

CLINICS IN LABORATORY MEDICINE (2003)

Article Medical Laboratory Technology

Hereditary prion protein amyloidoses

B Ghetti et al.

CLINICS IN LABORATORY MEDICINE (2003)

Article Genetics & Heredity

Huntington disease phenocopy is a familial prion disease

RC Moore et al.

AMERICAN JOURNAL OF HUMAN GENETICS (2001)

Article Biochemistry & Molecular Biology

PrPC directly interacts with proteins involved in signaling pathways

C Spielhaupter et al.

JOURNAL OF BIOLOGICAL CHEMISTRY (2001)

Article Clinical Neurology

A new PRNP mutation (G131V) associated with Gerstmann-Straussler-Scheinker disease

PK Panegyres et al.

ARCHIVES OF NEUROLOGY (2001)

Article Multidisciplinary Sciences

Acridine and phenothiazine derivatives as pharmacotherapeutics for prion disease

C Korth et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2001)

Article Biochemistry & Molecular Biology

Lack of evidence to support the association of the human prion gene with schizophrenia

MT Tsai et al.

MOLECULAR PSYCHIATRY (2001)

Review Clinical Neurology

Iatrogenic Creutzfeldt-Jakob disease at the millennium

P Brown et al.

NEUROLOGY (2000)

Article Multidisciplinary Sciences

Signal transduction through prion protein

S Mouillet-Richard et al.

SCIENCE (2000)