Related references
Note: Only part of the references are listed.Overexpression of human wild-type FUS causes progressive motor neuron degeneration in an age- and dose-dependent fashion
Jacqueline C. Mitchell et al.
ACTA NEUROPATHOLOGICA (2013)
Early interneuron dysfunction in ALS: Insights from a mutant sod1 zebrafish model
Alexander McGown et al.
ANNALS OF NEUROLOGY (2013)
RNA-binding ability of FUS regulates neurodegeneration, cytoplasmic mislocalization and incorporation into stress granules associated with FUS carrying ALS-linked mutations
J. Gavin Daigle et al.
HUMAN MOLECULAR GENETICS (2013)
Loss and gain of Drosophila TDP-43 impair synaptic efficacy and motor control leading to age-related neurodegeneration by loss-of-function phenotypes
Danielle C. Diaper et al.
HUMAN MOLECULAR GENETICS (2013)
Calcium Channel Agonists Protect against Neuromuscular Dysfunction in a Genetic Model of TDP-43 Mutation in ALS
Gary A. B. Armstrong et al.
JOURNAL OF NEUROSCIENCE (2013)
ALS mutations in FUS cause neuronal dysfunction and death in Caenorhabditis elegans by a dominant gain-of-function mechanism
Tetsuro Murakami et al.
HUMAN MOLECULAR GENETICS (2012)
A Gradient in Endogenous Rhythmicity and Oscillatory Drive Matches Recruitment Order in an Axial Motor Pool
Evdokia Menelaou et al.
JOURNAL OF NEUROSCIENCE (2012)
Neuromuscular effects of G93A-SOD1 expression in zebrafish
Stacey A. Sakowski et al.
MOLECULAR NEURODEGENERATION (2012)
Defective Neuromuscular Transmission in the SOD1G93A Transgenic Mouse Improves After Administration of Human Umbilical Cord Blood Cells
Nizar Souayah et al.
STEM CELL REVIEWS AND REPORTS (2012)
Links between Electrophysiological and Molecular Pathology of Amyotrophic Lateral Sclerosis
Katharina A. Quinlan
INTEGRATIVE AND COMPARATIVE BIOLOGY (2011)
The Dying-Back Phenomenon of Motor Neurons in ALS
Michal Dadon-Nachum et al.
JOURNAL OF MOLECULAR NEUROSCIENCE (2011)
Altered postnatal maturation of electrical properties in spinal motoneurons in a mouse model of amyotrophic lateral sclerosis
K. A. Quinlan et al.
JOURNAL OF PHYSIOLOGY-LONDON (2011)
Molecular pathways of motor neuron injury in amyotrophic lateral sclerosis
Laura Ferraiuolo et al.
NATURE REVIEWS NEUROLOGY (2011)
Gender-specific mechanism of synaptic impairment and its prevention by GCSF in a mouse model of ALS
Nikolay Naumenko et al.
FRONTIERS IN CELLULAR NEUROSCIENCE (2011)
FUS and TARDBP but Not SOD1 Interact in Genetic Models of Amyotrophic Lateral Sclerosis
Edor Kabashi et al.
PLOS GENETICS (2011)
A genetic model of amyotrophic lateral sclerosis in zebrafish displays phenotypic hallmarks of motoneuron disease
Tennore Ramesh et al.
DISEASE MODELS & MECHANISMS (2010)
Gain and loss of function of ALS-related mutations of TARDBP (TDP-43) cause motor deficits in vivo
Edor Kabashi et al.
HUMAN MOLECULAR GENETICS (2010)
Mutant FUS proteins that cause amyotrophic lateral sclerosis incorporate into stress granules
Daryl A. Bosco et al.
HUMAN MOLECULAR GENETICS (2010)
FUS GENE MUTATIONS IN FAMILIAL AND SPORADIC AMYOTROPHIC LATERAL SCLEROSIS
Rosa Rademakers et al.
MUSCLE & NERVE (2010)
Review: Neuromuscular synaptic vulnerability in motor neurone disease: amyotrophic lateral sclerosis and spinal muscular atrophy
L. M. Murray et al.
NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY (2010)
Zebrafish survival motor neuron mutants exhibit presynaptic neuromuscular junction defects
Kum-Loong Boon et al.
HUMAN MOLECULAR GENETICS (2009)
Mutations in FUS, an RNA Processing Protein, Cause Familial Amyotrophic Lateral Sclerosis Type 6
Caroline Vance et al.
SCIENCE (2009)
Mutations in the FUS/TLS Gene on Chromosome 16 Cause Familial Amyotrophic Lateral Sclerosis
T. J. Kwiatkowski et al.
SCIENCE (2009)
TARDBP mutations in individuals with sporadic and familial amyotrophic lateral sclerosis
Edor Kabashi et al.
NATURE GENETICS (2008)
TDP-43 mutations in familial and sporadic amyotrophic lateral sclerosis
Jemeen Sreedharan et al.
SCIENCE (2008)
Overexpression of mutant superoxide dismutase 1 causes a motor axonopathy in the zebrafish
Robin Lemmens et al.
HUMAN MOLECULAR GENETICS (2007)
Early electrophysiological abnormalities in lumbar motoneurons in a transgenic mouse model of amyotrophic lateral sclerosis
Cyril Bories et al.
EUROPEAN JOURNAL OF NEUROSCIENCE (2007)
Rhythmic motor activity evoked by NMDA in the spinal zebrafish larva
JR McDearmid et al.
JOURNAL OF NEUROPHYSIOLOGY (2006)
Paired motor neuron-muscle recordings in zebrafish test the receptor blockade model for shaping synaptic current
H Wen et al.
JOURNAL OF NEUROSCIENCE (2005)
Increased persistent Na+ current and its effect on excitability in motoneurones cultured from mutant SOD1 mice
JJ Kuo et al.
JOURNAL OF PHYSIOLOGY-LONDON (2005)
Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man
LR Fischer et al.
EXPERIMENTAL NEUROLOGY (2004)